Prevalence of constipation in cystic fibrosis patients: a systematic review of observational studies [PDF]
Jornal de Pediatria, 2020 Objective: To systematically revise the literature in search of data about the prevalence of constipation in patients with cystic fibrosis according to the publications in this field, which partly refer to guidelines defined in 2010 by the European ...
Marina A. Stefano +5 more
doaj +4 more sources
EXAMES PARA AVALIAR A SENSIBILIZAÇÃO AO ASPERGILLUS FUMIGATUS EM FIBROSE CÍSTICA [PDF]
Revista Paulista de Pediatria, 2017 RESUMO Objetivo: Avaliar os resultados dos exames utilizados para identificar a sensibilização IgE-mediada ao Aspergillus fumigatus em pacientes com fibrose cística.
Simone Santana Aguiar +2 more
doaj +2 more sources
Brazilian guidelines for the diagnosis and treatment of cystic fibrosis [PDF]
Jornal Brasileiro de Pneumologia, 2017 Cystic fibrosis (CF) is an autosomal recessive genetic disorder characterized by dysfunction of the CFTR gene. It is a multisystem disease that most often affects White individuals. In recent decades, various advances in the diagnosis and treatment of CF
Rodrigo Abensur Athanazio +17 more
doaj +2 more sources
Jornal de Pediatria, 2023 Objective: To assess the prevalence of GERD exclusively by means of multichannel intraluminal impedanciometry associated with pH monitoring (MIIpH) and compare it with respiratory symptoms in children with CF.
Emília da Silva Gonçalves +10 more
doaj +1 more source
Doenças raras na agenda da inovação em saúde: avanços e desafios na fibrose cística [PDF]
Cadernos de Saúde Pública, 2020 Resumo: O presente artigo se propõe a discutir as muitas complexidades envolvidas na incorporação de novas tecnologias em saúde para doenças raras, tomando como foco central da discussão o caso da fibrose cística.
Marise Basso Amaral, Sergio Rego
doaj +1 more source
Problemas Internalizantes e Externalizantes de Crianças e Adolescentes com Fibrose Cística
Psicologia: Ciência e Profissão, 2022 Resumo A fibrose cística é uma doença genética, ainda sem cura, provocada por mutações cromossômicas, que pode afetar vários sistemas, dentre os quais o respiratório e o digestivo são os mais comumente atingidos.
Carla Cristina Borges +1 more
doaj +1 more source
Linguistic validation of cystic fibrosis quality of life questionnaires [PDF]
, 2006 OBJECTIVE: The purpose of this study was to validate the Portuguese translations of four cystic fibrosis quality of life questionnaires (CFQ). The first three were developed for patients with cystic fibrosis aged from 6 to 11 years, from 12 to 13 years ...
Cunha, Maristela T. +4 more
core +2 more sources
Jornal de Pediatria (Versão em Português), 2019 Objectives: Volumetric capnography provides the standard CO2 elimination by the volume expired per respiratory cycle and is a measure to assess pulmonary involvement.
Paloma L.F. Parazzi +4 more
doaj +3 more sources
Results of nutritional intervention in children and adolescents with cystic fibrosis [PDF]
, 2002 Objective: few studies have verified longitudinally the evolution of the nutritional status of patients with cystic fibrosis. The objective of this study is to follow the evolution of the nutritional status, body composition and energy consumption ...
Ancona-Lopez, Fabio +5 more
core +3 more sources
Oxigenoterapia domiciliar prolongada em crianças e adolescentes: uma análise do uso clínico e de custos de um programa assistencial [PDF]
, 2010 Objectives: To describe the clinical and laboratory characteristics of patients on long-term home oxygen therapy followed up by the home care program of Hospital das Clinicas, School of Medicine, Universidade de São Paulo, during a period of 8 years, and
Adde, Fabiola V. +5 more
core +2 more sources