Results 11 to 20 of about 6,359 (170)

Cross‐talk between CFTR and sphingolipids in cystic fibrosis

FEBS Open Bio, Volume 13, Issue 9, Page 1601-1614, September 2023., 2023
Several lines of evidence shown that in cystic fibrosis the lack of the cystic fibrosis transmembrane conductance regulator (CFTR) is accompanied by changes in the plasma membrane composition of a bioactive class of lipids known as sphingolipids. Here, we depict a general overview of the literature related to the impact of the modifications of the ...
Dorina Dobi, Nicoletta Loberto, Rosaria Bassi, Anna Pistocchi, Giulia Lunghi, Anna Tamanini, Massimo Aureli   +6 more
wiley   +1 more source

Fibrose cística e a triagem neonatal [PDF]

, 2008
The clinical and diagnostic aspects of cystic fibrosis have been extensively reviewed, with an emphasis on neonatal screening. This systematic literature review involved a search for relevant contributions in the PubMed and SciELO databases.
FERNANDES, Maria I. M., GABETTA, Carmen S., JANUÁRIO, José N., MACIEL, Léa M. Z., MAGALHÃES, Patrícia K. R., PEDRO, Karla P., RODRIGUES, Roberta, VALDETARO, Fabio   +7 more
core   +2 more sources

Comparação da força muscular respiratória, qualidade de vida e capacidade funcional entre adolescentes com fibrose cística com diferentes perfis bacteriológicos

Fisioterapia e Pesquisa, 2018
RESUMO Comparou-se a força muscular respiratória, qualidade de vida e capacidade funcional em adolescentes com fibrose cística com diferentes perfis bacteriológicos.
Rafaela Cerqueira Andrade, Cássio Magalhães da Silva e Silva, Anna Lúcia Lima Diniz da Silva, Sheyla Ramos Haun, Valdivia Alves de Souza, Diego Jorge Souza Ezequiel   +5 more
doaj   +2 more sources

Results of nutritional intervention in children and adolescents with cystic fibrosis [PDF]

, 2002
Objective: few studies have verified longitudinally the evolution of the nutritional status of patients with cystic fibrosis. The objective of this study is to follow the evolution of the nutritional status, body composition and energy consumption ...
Ancona-Lopez, Fabio, Chiba, Sônia M., Gaspar, Maria Cristina A., Gomes, Clovis Eduardo Tadeu, Juliano, Yara, Novo, Neil Ferreira   +5 more
core   +3 more sources

Cell therapy in pulmonary diseases: are there perspectives? [PDF]

, 2009
A terapia celular poderia ser conceituada de forma ampla e genérica como o emprego de células para tratamento de doenças. Apesar de um número não tão expressivo de relatos tendo o pulmão como objeto de estudo na terapia celular em pacientes humanos, há ...
ALVES-DE-MORAES, Luis B. C., BILAQUI, Aldemir, FARIA, Carolina A., GRECO, Oswaldo T., RIBEIRO-PAES, João T., RUIZ, Milton A., STESSUK, Talita   +6 more
core   +1 more source

O impacto de primeiro ano de tratamento com dornase alfa nos parâmetros clínicos de pacientes com fibrose cística: estudo multicêntrico brasileiro [PDF]

, 2013
OBJECTIVE:To describe the clinical impact of the first year treatment with dornase alfa, according to age groups, in a cohort of Brazilian Cystic Fibrosis (CF) patients.METHODS:The data on 152 eligible patients, from 16 CF reference centers, that ...
Adde, Fabíola Villac, Mendes, Rita Heloisa, Rozov, Tatiana, Santana, Maria Angélica, Silva, Fernando Antônio A. E   +4 more
core   +4 more sources

Prevalência de doenças diagnosticadas pela triagem neonatal em uma região de Mato Grosso, Brasil

Journal Health NPEPS, 2021
Objetivo: analisar a prevalência de doenças diagnosticadas pela triagem neonatal em uma região de Mato Grosso, Brasil. Método: estudo descritivo e quantitativo, com análise do rastreamento neonatal de 4057 recém-nascidos em dez municípios de Mato Grosso,
Kaynara Borges Oliveira, Débora Oliveira Jesus, Maria Fernanda Spegiorin Salla Brune, Fernando Riegel, Alessandra Vaccari, Maximilian Wilhelm Brune   +5 more
doaj   +1 more source

The invisible patients: posttraumatic stress disorder in parents of individuals with cystic fibrosis [PDF]

, 2010
BACKGROUND: Besides the growing acknowledgment of the relevance of posttraumatic stress disorder (PTSD) related to medical illness, there is no study in cystic fibrosis yet.
Cabizuca, Mariana, Coutinho, Evandro Silva Freire, Figueira, Ivan, Mari, Jair de Jesus, Marques-Portella, Carla, Mendlowicz, Mauro, Ragoni, Celina, Souza, Wanderson de   +7 more
core   +3 more sources

Towards Targeting the Aryl Hydrocarbon Receptor in Cystic Fibrosis

Mediators of Inflammation, Volume 2018, Issue 1, 2018., 2018
Tryptophan (trp) metabolism is an important regulatory component of gut mucosal homeostasis and the microbiome. Metabolic pathways targeting the trp can lead to a myriad of metabolites, of both host and microbial origins, some of which act as endogenous low‐affinity ligands for the aryl hydrocarbon receptor (AhR), a cytosolic, ligand‐operated ...
Matteo Puccetti, Giuseppe Paolicelli, Vasileios Oikonomou, Antonella De Luca, Giorgia Renga, Monica Borghi, Marilena Pariano, Claudia Stincardini, Lucia Scaringi, Stefano Giovagnoli, Maurizio Ricci, Luigina Romani, Teresa Zelante, Virginia De Rose   +13 more
wiley   +1 more source

The Mast Cell‐Aryl Hydrocarbon Receptor Interplay at the Host‐Microbe Interface

Mediators of Inflammation, Volume 2018, Issue 1, 2018., 2018
Mast cells are increasingly being recognized as crucial cells in the response of the organism to environmental agents. Interestingly, the ability of mast cells to sense and respond to external cues is modulated by the microenvironment that surrounds mast cells and influences their differentiation.
Claudio Costantini, Giorgia Renga, Vasilis Oikonomou, Giuseppe Paolicelli, Monica Borghi, Marilena Pariano, Antonella De Luca, Matteo Puccetti, Claudia Stincardini, Paolo Mosci, Andrea Bartoli, Teresa Zelante, Luigina Romani, Sandra Helena Penha Oliveira   +13 more
wiley   +1 more source