Results 11 to 20 of about 30,033 (220)
Cross‐talk between CFTR and sphingolipids in cystic fibrosis
FEBS Open Bio, Volume 13, Issue 9, Page 1601-1614, September 2023., 2023 Several lines of evidence shown that in cystic fibrosis the lack of the cystic fibrosis transmembrane conductance regulator (CFTR) is accompanied by changes in the plasma membrane composition of a bioactive class of lipids known as sphingolipids. Here, we depict a general overview of the literature related to the impact of the modifications of the ...
Dorina Dobi +6 more
wiley +1 more source
Results of nutritional intervention in children and adolescents with cystic fibrosis [PDF]
, 2002 Objective: few studies have verified longitudinally the evolution of the nutritional status of patients with cystic fibrosis. The objective of this study is to follow the evolution of the nutritional status, body composition and energy consumption ...
Ancona-Lopez, Fabio +5 more
core +3 more sources
Oxigenoterapia domiciliar prolongada em crianças e adolescentes: uma análise do uso clínico e de custos de um programa assistencial [PDF]
, 2010 Objectives: To describe the clinical and laboratory characteristics of patients on long-term home oxygen therapy followed up by the home care program of Hospital das Clinicas, School of Medicine, Universidade de São Paulo, during a period of 8 years, and
Adde, Fabiola V. +5 more
core +2 more sources
Fibrose cística e a triagem neonatal [PDF]
, 2008 The clinical and diagnostic aspects of cystic fibrosis have been extensively reviewed, with an emphasis on neonatal screening. This systematic literature review involved a search for relevant contributions in the PubMed and SciELO databases.
FERNANDES, Maria I. M. +7 more
core +2 more sources
Fisioterapia e Pesquisa, 2018 RESUMO Comparou-se a força muscular respiratória, qualidade de vida e capacidade funcional em adolescentes com fibrose cística com diferentes perfis bacteriológicos.
Rafaela Cerqueira Andrade +5 more
doaj +2 more sources
Cell therapy in pulmonary diseases: are there perspectives? [PDF]
, 2009 A terapia celular poderia ser conceituada de forma ampla e genérica como o emprego de células para tratamento de doenças. Apesar de um número não tão expressivo de relatos tendo o pulmão como objeto de estudo na terapia celular em pacientes humanos, há ...
ALVES-DE-MORAES, Luis B. C. +6 more
core +1 more source
Prevalência de doenças diagnosticadas pela triagem neonatal em uma região de Mato Grosso, Brasil
Journal Health NPEPS, 2021 Objetivo: analisar a prevalência de doenças diagnosticadas pela triagem neonatal em uma região de Mato Grosso, Brasil. Método: estudo descritivo e quantitativo, com análise do rastreamento neonatal de 4057 recém-nascidos em dez municípios de Mato Grosso,
Kaynara Borges Oliveira +5 more
doaj +1 more source
The invisible patients: posttraumatic stress disorder in parents of individuals with cystic fibrosis [PDF]
, 2010 BACKGROUND: Besides the growing acknowledgment of the relevance of posttraumatic stress disorder (PTSD) related to medical illness, there is no study in cystic fibrosis yet.
Cabizuca, Mariana +7 more
core +3 more sources
Renal symptoms in the Joubert syndrome [PDF]
, 2009 OBJECTIVE:To describe the case of a patient with Joubert syndrome associated with renal impairments. CASE DESCRIPTION: A 2 month-old patient was admitted with hypotonia and hyperpneia.
Andrade, Maria Cristina de +2 more
core +4 more sources
Towards Targeting the Aryl Hydrocarbon Receptor in Cystic Fibrosis
Mediators of Inflammation, Volume 2018, Issue 1, 2018., 2018 Tryptophan (trp) metabolism is an important regulatory component of gut mucosal homeostasis and the microbiome. Metabolic pathways targeting the trp can lead to a myriad of metabolites, of both host and microbial origins, some of which act as endogenous low‐affinity ligands for the aryl hydrocarbon receptor (AhR), a cytosolic, ligand‐operated ...
Matteo Puccetti +13 more
wiley +1 more source