Results 91 to 100 of about 1,410,782 (208)

Contribution of multiple inert gas elimination technique to pulmonary medicine. 2. Chronic pulmonary diseases: chronic obstructive pulmonary disease and idiopathic pulmonary fibrosis. [PDF]

, 1994
Àlvar Agustí, Joan Albert Barberà
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Glucose tolerance in Canadian and French cystic fibrosis adult patients [PDF]

, 2019
Quitterie Reynaud, Valérie Boudreau, Sandrine Touzet, Katherine Desjardins, Stéphanie Bourdy, Emilie Blond, Yves Berthiaume, Rémi Rabasa‐Lhoret, I. Durieu   +8 more
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CFTR modulators response of S737F and T465N CFTR variants on patient-derived rectal organoids

Orphanet Journal of Rare Diseases
Background Predictions based on patient-derived materials of CFTR modulators efficacy have been performed lately in patient-derived cells, extending FDA-approved drugs for CF patients harboring rare variants.
Karina Kleinfelder, Paola Melotti, Anca Manuela Hristodor, Cristina Fevola, Giovanni Taccetti, Vito Terlizzi, Claudio Sorio   +6 more
doaj   +1 more source

Lung clearance index short-term variability in cystic fibrosis: a pre-post pulmonary exacerbation study

Italian Journal of Pediatrics
Background Multiple Breath washout (MBW) represents an important tool to detect early a possible pulmonary exacerbation especially in Cystic Fibrosis (CF) disease.
Matteo De Marchis, Enza Montemitro, Alessandra Boni, Alessandra Federici, Daniele Di Giovanni, Luca Cristiani, Renato Cutrera, Alessandro G. Fiocchi   +7 more
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ECM formation and degradation during fibrosis, repair, and regeneration

npj Metabolic Health and Disease
Imperfect attempts at organ repair after repeated injury result in aberrant formation of extracellular matrix (ECM) and loss of tissue structure. This abnormal ECM goes from being a consequence of cellular dysregulation to become the backbone of a ...
Alejandro E. Mayorca-Guiliani, Diana Julie Leeming, Kim Henriksen, Joachim Høg Mortensen, Signe Holm Nielsen, Quentin M. Anstee, Arun J. Sanyal, Morten A. Karsdal, Detlef Schuppan   +8 more
doaj   +1 more source

Exploring the utilisation and effectiveness of implementation science strategies by cystic fibrosis registries for healthcare improvement: a systematic review

European Respiratory Review
Background Cystic fibrosis (CF) registries capture important information in high-burden health domains to support improvement in health outcomes, although a number of unanswered questions persist, as follows.
Rob G. Stirling, Bhumika Sood, Macken J.L. Stirling, Tom Kotsimbos, Dominic T. Keating, Catherine E. Rang, James M. Trauer, Alan C. Young, Christiaan Yu, Julianna Bailey, Peter Wark, Angela Melder, Paul Dawkins   +12 more
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Antifibrotic drugs for idiopathic pulmonary fibrosis

, 2020
Vijay Hadda, Randeep Guleria
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Evolving Up‐regulation of Biliary Fibrosis–Related Extracellular Matrix Molecules After Successful Portoenterostomy [PDF]

, 2021
Antti Kyrönlahti, Nimish Godbole, Oyediran Akinrinade, Tea Soini, Iiris Nyholm, Noora Andersson, Maria Hukkinen, Jouko Lohi, David B. Wilson, Marjut Pihlajoki, Mikko P. Pakarinen, Markku Heikinheimo   +11 more
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Detection of cytokines in nasal lavage samples of patients with cystic fibrosis: comparison of two different cytokine detection assays

BMC Pulmonary Medicine
Background Cystic fibrosis (CF) is a genetic multisystem disorder. Inflammatory processes, which presumably begin early in infancy, play a crucial role in the progression of the disease. The detection of inflammatory biomarkers, especially in the airways,
Teresa Fuchs, Manuela Zlamy, Thomas Zöggeler, Dorothea Appelt, Katharina Niedermayr, Anja Siedl, Verena Gasser, Johannes Eder, Helmut Ellemunter   +8 more
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Retinoic acid receptor α activity in proximal tubules prevents kidney injury and fibrosis [PDF]

Krysta M. DiKun, Xiao‐Han Tang, Leiping Fu, Mary E. Choi, Changyuan Lu, Lorraine J. Gudas   +5 more
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