Results 51 to 60 of about 4,997 (156)

Prospective studies of swallowing in Mucopolysaccharidosis II (Hunter syndrome) before and after enzyme treatment [PDF]

open access: yes, 2011
Case study with the aim to evaluate swallowing pre- and post-enzyme treatment of an individual with Mucopolysaccharidosis, and to analyze whether this treatment caused swallowing improvement.
Ferreira, Ana Carolina Rocha Gomes   +1 more
core   +4 more sources

Los glicosaminoglicanos se encuentran implicados en la adherencia de Candida albicans y Malassezia spp. a queratinocitos, pero no a fibroblastos dérmicos

open access: yesActas Dermo-Sifiliográficas, 2021
Financiado por el premio 2019 «AEDV investiga», de la Fundación Piel Sana de la Academia Española de Dermatología y Venereología (AEDV).
Ordiales Trabanco, Helena   +6 more
openaire   +2 more sources

Achados anatomo-patológicos e ultraestruturais na mucopoussacaridose: relato de caso Anatomo-pathological and ultrastructural features in mucopolysaccharidosis: case report

open access: yesArquivos de Neuro-Psiquiatria, 1997
As mucopolissacaridoses (MPS) são doenças de acúmulo lisossomal em que ocorre defeito enzimático específico com consequente acúmulo de glicosaminoglicanos nos tecidos.
Luiz Fernando Bleggi Torres   +3 more
doaj   +1 more source

FIND: a importância de um diagnóstico [PDF]

open access: yes, 2017
O Projeto FIND é um estudo de colaboração entre a SDHM da SPP e o INSA e permite disponibilizar uma ferramenta de diagnóstico aos médicos que sigam um doente com suspeita clínica de mucopolissacaridose (MPS).N/
Alves, Sandra   +3 more
core   +1 more source

Daño oxidativo y capacidad de defensa antioxidante en pacientes cubanos con mucopolisacaridosis

open access: yesMedisan, 2019
Introducción: Las mucopolisacaridosis son causadas por la deficiencia de las actividades de las enzimas lisosomales necesarias para degradar los glicosaminoglicanos.
Tatiana Acosta Sánchez   +4 more
doaj  

Modificaciones fisarias en el conejo inducidas por campos electromagnéticos [PDF]

open access: yes, 1994
Se efectúa un estudio experimental para valorar los efectos de campos electromagnéticos de dos intensidades diferentes (2,4 y 10 Gauss) sobre la fisis de huesos largos.
Castro Moraleja, R. de, Garces, G. L.
core  

Purification and characterization of hyaluronic acid from chicken combs Purificação e caracterização do ácido hialurônico obtido da crista de frango

open access: yesCiência Rural, 2012
Hyaluronic acid (HA) is an important macromolecule in medical and pharmaceutical fields. The umbilical cord and the chicken comb are some of the tissues richest in this polysaccharide. The profit from obtaining HA from the combs of slaughtered animals is
Claudia Severo da Rosa   +5 more
doaj  

Interference of oropharyngeal dysphagia in food consumption in patients with mucopolysaccharidosis II [PDF]

open access: yes, 2012
PURPOSE: this study aimed to relate the degree of dysphagia and food consumption of individuals with mucopolysaccharidosis II (MPS II). METHOD: it was included individuals with MPS II of the genetics department at the State University of Alagoas and ...
Barbosa, Pauliana Buarque   +5 more
core   +2 more sources

Heparina no fraccionada en el manejo del síndrome coronario agudo.

open access: yesRevista de la Facultad de Medicina, 2007
La formación de trombos es un proceso normal que tiene como objetivo prevenir sangrados importantes ante la presencia de una noxa que altere la integridad vascular.
Nelson Moreno Ruíz   +1 more
doaj  

A useful routine for biochemical detection and diagnosis of mucopolysaccharidoses

open access: yesGenetics and Molecular Biology, 1998
Mucopolysaccharidoses (MPS) constitute, owing to their biochemical, genetical and clinical characteristics, a large and heterogeneous subgroup among the lysosomal storage diseases (LSD).
Sandra Leistner, Roberto Giugliani
doaj   +1 more source

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