Results 11 to 20 of about 345,366 (342)
Glycogen Metabolism in Glycogen-rich Erythrocytes [PDF]
Abstract High concentrations of red blood cell glycogen were visualized by electron microscopy and demonstrated biochemically in amylo-1,6-glucosidase- and phosphorylase-deficient red blood cells. Glycogen concentration decreased as a function of cell age.
Moses Sw+3 more
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Incorporation of phosphate into glycogen by glycogen synthase [PDF]
The storage polymer glycogen normally contains small amounts of covalently attached phosphate as phosphomonoesters at C2, C3 and C6 atoms of glucose residues. In the absence of the laforin phosphatase, as in the rare childhood epilepsy Lafora disease, the phosphorylation level is elevated and is associated with abnormal glycogen structure that ...
Christopher J. Contreras+7 more
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Glycogen metabolism and glycogen storage disorders [PDF]
Glucose is the main energy fuel for the human brain. Maintenance of glucose homeostasis is therefore, crucial to meet cellular energy demands in both - normal physiological states and during stress or increased demands. Glucose is stored as glycogen primarily in the liver and skeletal muscle with a small amount stored in the brain.
Taylor Tribett+3 more
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Liver Glycogen Synthase in Rats with a Glycogen‐Storage Disorder [PDF]
1. A strain of rats with a genetically‐determined liver glycogen‐storage disorder (gsd/gsd) caused by a deficiency of liver phosphorylase kinase has a very high concentration of glycogen in the liver with a total glycogen synthase activity higher than in liver of fed normal animals, but only a small amount of the enzyme in the active form.
Colin Watts, Rex S. Malthus
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Action Patterns of Phosphorylase and Glycogen Synthetase on Glycogen [PDF]
The action patterns of liver and muscle glycogen synthetases and of muscle phosphorylase b on glycogen samples of different molecular weight and on β‐amylase limit dextrins were studied. For this purpose a method for measuring the number of newly added glucose residues that are at non‐reducing ends was developed.It was found that glucose transfer to ...
Parodi, Armando José A.+3 more
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Changes of gangliosides and other lipids in skeletal muscle from rabbits with experimental dystrophy
Comparison of the skeletal muscles from vitamin E-deficient and control rabbits showed that the muscles from the deficient animals had lower contents of protein and glycogen but more water and lipid.
I. Albarracín, F.E. Lassaga, R. Caputto
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Lafora disease offers a unique window into neuronal glycogen metabolism [PDF]
Lafora disease (LD) is a fatal, autosomal recessive, glycogen-storage disorder that manifests as severe epilepsy. LD results from mutations in the gene encoding either the glycogen phosphatase laforin or the E3 ubiquitin ligase malin. Individuals with LD
Gentry, Matthew S.+4 more
core +2 more sources
A forage-only diet alters the metabolic response of horses in training [PDF]
Most athletic horses are fed a high-starch diet despite the risk of health problems. Replacing starch concentrate with high-energy forage would alleviate these health problems, but could result in a shift in major substrates for muscle energy supply from
A. Jansson+45 more
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Background: Diabetic mellitus is a multifactorial disorder associated with its devastating consequences has assumed epidemic proportion. Diabetes mellitus (DM) is a global health problem and the incidence of DM is increasing at alarming rate all over the
Mamata Laxmikant Pochhi
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