Results 41 to 50 of about 1,002,705 (170)
The phosphoglucomutase (pgm) gene codes for a key enzyme required for the formation of UDP-glucose and ADP-glucose, the sugar donors for the biosynthesis of glucose containing polysaccharides.
Viviana C. Lepek +5 more
doaj +1 more source
Origin and evolution of the main starch biosynthetic enzymes
Starch, a semi-crystalline energy storage form primarily found in plant plastids plays a crucial role in various food or no-food applications. Despite the starch biosynthetic pathway's main enzymes have been characterized, their origin and evolution ...
Hong Chang +8 more
doaj +1 more source
Phylogenomic analysis of glycogen branching and debranching enzymatic duo [PDF]
BackgroundBranched polymers of glucose are universally used for energy storage in cells, taking the form of glycogen in animals, fungi, Bacteria, and Archaea, and of amylopectin in plants.
Zmasek, Christian M +3 more
core +2 more sources
Cardiac Involvement in Glycogen Storage Disease Type IV: Two Cases and the Two Ends of a Spectrum
Glycogen storage disease type IV (GSD IV) is an autosomal recessive disorder due to the deficiency of α 1,4-glucan branching enzyme, resulting in an accumulation of amylopectin-like polysaccharide in various systems.
Tolga Aksu, Ayse Colak, Omac Tufekcioglu
doaj +1 more source
Glycogen storage disease type IV (GSD IV) is an ultra-rare autosomal recessive disease caused by variants in the GBE1 gene, which encodes the glycogen branching enzyme (GBE). GSD IV accounts for approximately 3% of all GSD. The phenotype of GSD IV ranges
Matheus Vernet Machado Bressan Wilke +13 more
doaj +1 more source
Improving bread quality using Deinococcus geothermalis glycogen branching enzyme [PDF]
Glycogen branching enzyme(GBE) catalyzes transglycosylation reaction producing α-1,6-glucosidic linkages by cleaving an α-1,4-glucosidic linkage. Deinococcus geothermalis GBE (DgGBE) has the unique activity to form a large number of short oligosaccharide
Park, Jong-Tae +3 more
core +1 more source
Compartmentation of glycogen metabolism revealed from 13C isotopologue distributions [PDF]
Background: Stable isotope tracers are used to assess metabolic flux profiles in living cells. The existing methods of measurement average out the isotopic isomer distribution in metabolites throughout the cell, whereas the knowledge of compartmental ...
Marin, Silvia +18 more
core +1 more source
AbstractBranching enzymes (BE) are responsible for the formation of branching points at the 1,6 position in glycogen and starch, by catalyzing the cleavage of α-1,4-linkages and the subsequent transfer by introducing α-1,6-linked glucose branched points.
Léa Conchou +7 more
openaire +3 more sources
Fibroblasts have been developed from skin biopsies obtained from 3 children with type IV glycogen storage disease (amylopectinosis) and have been shown to be profoundly deficient in branching enzyme activity.
Brown, Barbara I +2 more
core +1 more source
Microalgae can effectively accumulate starch by using nutritional limitation methods in the context of bioalcohol fuel production. However, relatively few studies have focused on starch accumulation in microalgae and its molecular basis, especially under
Haiqing Xu +16 more
doaj +1 more source

