Background and Objective Paroxysmal nocturnal hemoglobinuria is a rare blood disorder characterized by life-threatening hemolysis and thrombosis. Complement C5 inhibitor therapy improves symptoms and life prognosis; however, it can result in insufficient
Ryan L. Crass +4 more
doaj +1 more source
Se presenta el caso de un paciente de sexo masculino, de 65 años de edad, portador de una cardiopatía isquémica y severo prolapso de la válvula mitral, que fue sometido a cirugía de revascularización con un puente aorto coronario utilizando la vena ...
Régulo Agusti +2 more
doaj
How Severe is Severe Enough? Organ Failure Rather Than Anemia Severity as a Potential Threshold for Complement Inhibition in Pediatric Paroxysmal Cold Hemoglobinuria: A Case Report. [PDF]
Yu C, Rane Z, Nedelcu E, Matsunaga A.
europepmc +1 more source
Cognitive Biases in Early Trauma Transfusions: Lessons From Three Rare Cases of Acute Hemolytic Reaction. [PDF]
Entezari Meybodi MJ +3 more
europepmc +1 more source
Deficiencia de proteínas de superficie en el diagnóstico de hemoglobinuria paroxística nocturna [PDF]
Paroxysmal Nocturnal Hemoglobinuria is a disorder that occurs when there is a mutation, in the PIG-A gene, which\u27s responsible for encoding the glycosylphosphatidylinositol anchored protein class A.
Mena-Zapata, Susana
core
A real-world, multi-center, prospective, observational study for paroxysmal nocturnal haemoglobinuria (PNH) in China: Baseline characteristics, disease burden and treatment patterns. [PDF]
Han B +11 more
europepmc +1 more source
Anemia and Patient-Reported Outcomes in Patients With Paroxysmal Nocturnal Hemoglobinuria: A Real-World Observational Study. [PDF]
Oliva EN +22 more
europepmc +1 more source
A case report of CD4<sup>-</sup> CD8<sup>+</sup> CD56<sup>-</sup> TCRγδ<sup>+</sup> T-large granular lymphocytic leukaemia with severe aplastic anemia and a PNH clone. [PDF]
Du Y, Zhang J, Jin S.
europepmc +1 more source
Direct Switch From Iptacopan to Pegcetacoplan in a Patient With Paroxysmal Nocturnal Hemoglobinuria. [PDF]
Latyshev V +3 more
europepmc +1 more source
Hemoglobinuria associated with Candidatus Mycoplasma Haemobos in a primiparous Holstein cow in Turkey: a case report. [PDF]
Emlik F +6 more
europepmc +1 more source

