Recommendations on clinical trial design for treatment of Mucopolysaccharidosis Type III [PDF]
Background Mucopolysaccharidosis type III is a progressive, neurodegenerative lysosomal storage disorder for which there is currently no effective therapy. Though numerous potential therapies are in development, there are several challenges to conducting
Bigger, Brian +12 more
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Some side effects of heparin, heparinoids, and their antagonists [PDF]
Peer Reviewedhttp://deepblue.lib.umich.edu/bitstream/2027.42/117045/1/cpt196673379 ...
Coon, William W., Willis, Park W.
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A Minireview Of Cellulose Nanocrystals And Its Potential Integration As Co-product In Bioethanol Production [PDF]
Cellulose nanocrystals appeared as important bio-based products and the collected information in term of production, characterization and application suggest that this nanomaterial could be easily extrapolated to bioethanol production.
Baeza J. +4 more
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An investigation of total and 35S-labeled mucopolysaccharides in intestinal wall kidney of cattle, sheep and swine [PDF]
Mucopolysaccharides (MPS) occur in the ground substance of connective tissue and have been isolated and identified from many diverse types of tissue.
Berry, Robert Kerns
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Heparinases: cloning, expression and structural requirements for activity [PDF]
Structural characteristics of heparin (Hep) and heparan sulfate (HS) have been determined using enzymes from Flavobacterium heparinum, a non-pathogenic soil bacterium.
Córdula, Carolina Ribeiro
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小児における尿中酸性ムコ多糖類の排泄パターンに関する研究 第II編 遺伝性酸性ムコ多糖代謝異常症*5例の尿中酸性ムコ多糖類の排泄パターン [PDF]
Since Brante suggested that Hurler syndrome was mucopolysaccharidosis, urinary acid mucopolysaccharides (AMPS) have been of interest to investigators.
南 良二
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Characterization of a Mucopolysaccharidosis Type I and GalNAc Transferase deficiency double knockout mouse [PDF]
The mucopolysaccharidoses (MPSs) are a group of lysosomal storage diseases (LSDs) which are characterized by the aberrant primary storage of glycosaminoglycans (GAGs) in lysosomes of multiple organ and tissue systems.
Gera, Karan
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新鮮血漿静注による遺伝性ムコ多糖代謝異常症の尿中酸性ムコ多糖の変化について 第II編 尿中酸性ムコ多糖の組成変化 [PDF]
In our previous paper, the decrease of acid mucopolysaccharides and increase of non-cetylpyridinium chloride-precipitates in five patients with mucopolysaccharidosis after normal fresh plasma infusions were reported.
山口 衛
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Studies on the Urinary Cetylpyridinium Chloride-Precipitates and Non-Cetylpyridinium Chloride-Precipitates in Normal Children and the Patients with Mucopolys-accharidoses, Mucolipidoses and Lipidoses. ―Hyperglyeopeptiduria in Mucolipidoses― [PDF]
Urinary cetylPyridinium chloride(CPC)-precipitates and non-CPC-precipitates in normal male children and seven patients with a new type of mucolipidosis, GM1-gangliosidosis type 1, I-cell disease, MPS I (Hurler type), MPS IV (Morquio type), Gauche's ...
千葉, 学道
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Wound healing effect of acanthaster planci sulfated glycosaminoglycans extracted from diabetic induced rats [PDF]
The Crown-of-Thorns starfish is an echidonermata that inhabits tropical and subtropical marine ecosystem within the Indo-Pacific. The starfish: A. Planci causes endemic devegetation of coral reef ecosystem.
Zainudin, Nur Hanim
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