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Intermediate-dose cytarabine is an effective therapy for adults with non-Langerhans cell histiocytosis [PDF]
Orphanet Journal of Rare Diseases, 2022 Background Non-Langerhans cell histiocytosis, including Erdheim–Chester disease (ECD), Rosai–Dorfman disease (RDD), indeterminate cell histiocytosis (ICH), and unclassified histiocytosis, is a rare disorder lacking a standard treatment strategy.
Ting Liu +7 more
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Journal of the International Association of Providers of AIDS Care, 2022 Non-Langerhans cell histiocytosis is a rare disease which seldom affects adults. We report a case of a 32-year-old Bulgarian woman living with HIV. She developed severe anemia, extreme splenomegaly, requiring splenectomy and vertebral tumor formations ...
Nina Yancheva +4 more
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Progress in the diagnosis and treatment of ocular histiocytosis [PDF]
Guoji Yanke Zazhi, 2023 Ocular histiocytosis is a rare and heterogeneous group of disorders which can occur in children and adults. There is a great challenge in the diagnosis and treatment because of the atypical clinical and imaging manifestations.
Jun-Yi Qiao, Wei-Min He
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Adult-onset of Langerhans cell histiocytosis: a clinical case
Alʹmanah Kliničeskoj Mediciny, 2021 Langerhans cell histiocytosis is mainly diagnosed in children, and its manifestation in adult age is quite uncommon. Skin rashes may be non-specific and mimic a number of dermatoses.
Olga V. Chernysheva +3 more
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A case of disseminated extranodal Rosai–Dorfman disease diagnosed by skin manifestations
Journal of Cutaneous Immunology and Allergy, 2023 Rosai–Dorfman disease (RDD) is a rare non‐Langerhans cell histiocytosis that was first described as sinus histiocytosis with massive lymphadenopathy by Rosai and Dorfman in 1969.
Shintaro Saito +3 more
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Adult Langerhans cell histiocytosis with pulmonary and colorectoanal involvement: a case report
Journal of Medical Case Reports, 2017 Background Langerhans cell histiocytosis is a rare systemic disease characterized by the abnormal overproduction of histiocytes that tend to infiltrate single or multiple organ systems leading to significant tissue damage. It mainly affects – by order of
Mohamad Jihad Mansour +4 more
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Orbital mass and hairy kidney as characteristics of Erdheim‐Chester disease
Clinical Case Reports, 2021 Erdheim‐Chester disease (ECD) is a rare non‐Langerhans cell histiocytosis, involving multiple organs. We report a case of ECD with typical features of an orbital mass and "hairy kidneys," whose recognition can lead to early diagnosis and treatment.
Koichiro Yamamoto +3 more
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Dermatopathology, 2019 A case of congenital self-healing Langerhans cell histiocytosis (CSHLCH), also known as Hashimoto-Pritzker disease, is reported. The newborn presented as blueberry muffin baby at birth, showing numerous non-blanching blue-purplish and dark-red papular ...
Katharina Hansel +7 more
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ADULT ONSET XANTHOGRANULOMA – CASE REPORT AND REVIEW OF LITERATURE [PDF]
Romanian Medical Journal, 2019 Juvenile xanthogranuloma represents the most common form of non-Langerhans cell histiocytosis. It is tipically a childhood disorder, over 80% of cases developing in the first year of life.
Liliana Gabriela Popa +5 more
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Unusual facial lesions in H syndrome
Clinical Case Reports, 2022 H Syndrome is a rare genodermatosis. It may include facial involvement such as: facial telangiectasia, both hypo‐ and hyperpigmented lesions, hirsutism, swollen cheeks due to subcutaneous infiltration and eczematous lesions.
Mariem Rekik +7 more
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