Indeterminate Cell Histiocytosis: A Case Report [PDF]
Kaohsiung Journal of Medical Sciences, 2004 Indeterminate cell histiocytosis is a rare neoplasm composed of cells with mixed characteristics of Langerhans cells and non-Langerhans cells. An otherwise healthy, 36-year-old woman presented with asymptomatic generalized papules and nodules that had ...
Chun-Hua Wang, Gwo-Shing Chen
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Intermediate-dose cytarabine is an effective therapy for adults with non-Langerhans cell histiocytosis [PDF]
Orphanet Journal of Rare Diseases, 2022 Background Non-Langerhans cell histiocytosis, including Erdheim–Chester disease (ECD), Rosai–Dorfman disease (RDD), indeterminate cell histiocytosis (ICH), and unclassified histiocytosis, is a rare disorder lacking a standard treatment strategy.
Ting Liu +7 more
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Journal of the International Association of Providers of AIDS Care, 2022 Non-Langerhans cell histiocytosis is a rare disease which seldom affects adults. We report a case of a 32-year-old Bulgarian woman living with HIV. She developed severe anemia, extreme splenomegaly, requiring splenectomy and vertebral tumor formations ...
Nina Yancheva +4 more
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Erdheim–Chester Disease Manifesting Without Long Bone Involvement [PDF]
Respirology Case ReportsErdheim–Chester Disease (ECD) is an extremely rare, non‐Langerhans cell histiocytosis characterised by the proliferation of foamy histiocytes infiltrating various organs.
Dhiran Sivasubramanian +6 more
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Baby with neonatal systemic juvenile xanthogranuloma born within a cross-cousin marriage [PDF]
Dermatologica Sinica, 2015 Juvenile xanthogranuloma is a non-Langerhans cell histiocytosis seen most commonly in childhood and adolescence. Extracutaneous involvement is rare. We report an interesting and extremely rare case of systemic (skin, lung, spleen, and colon) “juvenile ...
Hikmet Tekin Nacaroglu +6 more
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Renovascular Hypertension: Unraveling a Case of Mixed Histiocytosis
Annals of Internal Medicine: Clinical Cases, 2023 Renovascular hypertension is a cause of secondary hypertension. Atherosclerotic renal artery stenosis and fibromuscular dysplasia are the main causes, but other rare entities can involve the renal arteries.
Pedro Marques +8 more
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Adult-onset of Langerhans cell histiocytosis: a clinical case
Alʹmanah Kliničeskoj Mediciny, 2021 Langerhans cell histiocytosis is mainly diagnosed in children, and its manifestation in adult age is quite uncommon. Skin rashes may be non-specific and mimic a number of dermatoses.
Olga V. Chernysheva +3 more
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Radiotherapy in langerhans cell histiocytosis : a rare indication in a rare disease [PDF]
, 2013 Introduction: Langerhans Cell Histiocytosis (LCH) represents a rare benign disorder, previously designated as "Histiocytosis X", "Type II Histiocytosis" or "Langerhans Cell Granulomatosis".
Bruns, Frank +8 more
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BRAF V600E mutations in urine and plasma cell-free DNA from patients with Erdheim-Chester disease. [PDF]
, 2014 Erdheim-Chester disease (ECD) is a rare histiocytosis with a high prevalence of BRAF V600E mutation (>50% of patients). Patients with BRAF-mutant ECD can respond to BRAF inhibitors.
Cabrilo, Goran +12 more
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BRAFV600E mutation in cutaneous lesions of patients with adult Langerhans cell histiocytosis. [PDF]
, 2015 BACKGROUND: Langerhans cell histiocytosis (LCH) is characterized by the proliferation of pathologic Langerhans cells. The disease can develop in any age and can affect almost any organ. Cutaneous involvement is frequent in LCH.
Badalian-Very +18 more
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