Results 21 to 30 of about 9,884 (233)

A rare cause of recurrent spontaneous pneumothorax: Birt-hogg-dube syndrome [PDF]

, 2018
Birt-Hogg-Dube (BHD) syndrome is an unusual disorder characterized by the triad of cutaneous lesions, renal tumors and lung cysts. In cases with BHD syndrome, the frequency of recurrent pneumothorax is increased due to presence of multiple lung cysts. It
Demirci, M., Karaman, Engin, Ufuk, F., Yavaş, H.G.   +3 more
core   +1 more source

PAPULAR HISTIOCYTOSIS OF HEAD : TYPE OF NON - LANGERHANS CELLS HISTIOCYTOSIS

Journal of Evolution of Medical and Dental Sciences, 2014
Papular histiocytosis of the head also known as benign cephalic histiocytosis is a rare, self-limiting histiocytosis that typically starts in early childhood. 1 Erythematous macules, papules and nodules develop on cheeks and spread to the forehead, earlobes and neck. Lesions are asymptomatic, gradually become reddish brown and may spread to involve the
Anil Kumar Gupta, Gaurav Murti
openaire   +1 more source

Clinicopathological Features, Treatment Response, and Outcome of Rosai‐Dorfman Disease in Two Children [PDF]

Clin Case Rep
ABSTRACT Rosai‐Dorfman disease is a rare non‐Langerhans cell histiocytic disorder. It is common in male children and young adults of African descent. It is classified into sporadic and familial types. The most common clinical presentation is massive bilateral cervical lymphadenopathy associated with constitutional symptoms. Histiocytic emperipolesis is
Evele G, Francine K.
europepmc   +2 more sources

ADULT ONSET XANTHOGRANULOMA – CASE REPORT AND REVIEW OF LITERATURE [PDF]

Romanian Medical Journal, 2019
Juvenile xanthogranuloma represents the most common form of non-Langerhans cell histiocytosis. It is tipically a childhood disorder, over 80% of cases developing in the first year of life.
Liliana Gabriela Popa, Mara Madalina Mihai, Olguta Anca Orzan, Cristina Beiu, Tiberiu Tebeica, Calin Giurcaneanu   +5 more
doaj   +1 more source

Indeterminate Cell Histiocytosis: A Case Report

Kaohsiung Journal of Medical Sciences, 2004
Indeterminate cell histiocytosis is a rare neoplasm composed of cells with mixed characteristics of Langerhans cells and non-Langerhans cells. An otherwise healthy, 36-year-old woman presented with asymptomatic generalized papules and nodules that had ...
Chun-Hua Wang, Gwo-Shing Chen
doaj   +1 more source

Efficacy of vinblastine in central nervous system Langerhans cell histiocytosis: a nationwide retrospective study [PDF]

, 2011
Background Vinblastine (VBL) is the standard treatment for systemic Langerhans cell histiocytosis (LCH), but little is known about its efficacy in central nervous system (CNS) mass lesions. Methods
Sophie Ng Wing Tin, Nadine Martin-Duverneuil, Ahmed Idbaih, Catherine Garel, Maria Ribeiro, Judith Parker, Anne-Sophie Defachelles, Anne Lambilliotte, Mohamed Barkaoui, Martine Munzer, Martine Gardembas, Jean Sibilia, Patrick Lutz, Renato Fior, Michel Polak, Alain Robert, Olivier Aumaitre, Dominique Plantaz, Corinne Armari-Alla, Thierry Genereau, Perrine Berard, Ghislain Talom, Jean-Loup Pennaforte, Hubert Le Pointe, Marie-Anne Barthez, Gérard Couillault, Julien Haroche, Karima Mokhtari, Jean Donadieu, Khê Hoang-Xuan, null null   +30 more
core   +2 more sources

Non-Langerhans cell histiocytosis in a child with Kawasaki disease

BMJ Case Reports, 2009
Polymorphous skin rashes are one of the major presentations in children with Kawasaki disease. This report describes an unusual presentation of a skin rash (non-Langerhans cell histiocytosis) in a 4-month-old baby with resistance to intravenous immunoglobulin (IVIG) treatment and coronary artery dilatation.
Ho-Chang, Kuo, Chih-Chiang, Wu, Tsung-Hsien, Yang, Hong-Ren, Yu, Chi-Di, Liang, Yi-Ju, Chen, Kuender D, Yang   +6 more
openaire   +3 more sources

Unusual facial lesions in H syndrome

Clinical Case Reports, 2022
H Syndrome is a rare genodermatosis. It may include facial involvement such as: facial telangiectasia, both hypo‐ and hyperpigmented lesions, hirsutism, swollen cheeks due to subcutaneous infiltration and eczematous lesions.
Mariem Rekik, Emna Bahloul, Mohamed Ben Rejeb, Khadija Sellami, Slim Charfi, Hamza Chouk, Tahya Boudaouara, Hamida Turki   +7 more
doaj   +1 more source

Efficacy, safety, and relapse outcomes of MAPK inhibitors in pediatric Langerhans cell histiocytosis: A real-world study. [PDF]

Int J Cancer
What's new? Mitogen‐activated protein kinase (MAPK) inhibitors are promising treatments for pediatric Langerhans cell histiocytosis (LCH), a rare heterogeneous neoplasm that often affects multiple organ systems. Which MAPK inhibitors are most effective against LCH remains uncertain.
Tang X, Sun JJ, Wan Z, Jing XY, Guo X, Gao J.   +5 more
europepmc   +2 more sources

Langerhans cell histiocytosis [PDF]

, 1998
The authors present a rare case of Langerhans cell histiocytosis in a 31 year old female patient with vulvar, peri-anal and oral lesions, diabetes insipidus, pulmonary skin and bone infiltrations.
Atallah, Álvaro Nagib, Chauffaille, Maria de Lourdes Lopes Ferrari, Diniz, Cybelle Maria Costa, Enokihara, Silva, Ferreira, Karin Ventura, Hassun, Karine Marques, Kerbauy, José, Martinez, José Antônio Baddini, Michalany, Nylceo, Simões, Milvia Maria, Valério, Rosana M.   +10 more
core   +2 more sources