High prevalence of myeloid neoplasms in adults with non–Langerhans cell histiocytosis [PDF]
Blood, 2017 Key Points Some 10.1% of adults with non–Langerhans cell histiocytosis have a concomitant myeloid neoplasm with each often harboring distinct mutations. The presence of distinct kinase mutations in histiocytosis and myeloid neoplasms resulted in discordant responses to targeted therapy.
Papo, Matthias +22 more
openaire +3 more sources
Erdheim-Chester Disease: a comprehensive review of the literature [PDF]
, 2013 Erdheim-Chester Disease (ECD) is a rare form of non Langerhans' cell histiocytosis. Individuals affected by this disease are typically adults between their 5th and 7th decades of life. Males and females are almost equally affected.
Mirra Manevich-Mazor +2 more
core +1 more source
Clinical experience in an infant with Langerhans cell histiocytosis
Universidad Médica Pinareña, 2021 Introduction: Langerhans cell histiocytosis (LCH) or Histiocytosis X is a benign proliferative disease affecting dendritic cells. It presents a wide clinical spectrum, from isolated eosinophilic bone granuloma to multisystem involvement with multiple ...
Yamilka Pita Barrios +2 more
doaj
Smoking-related interstitial lung disease [PDF]
, 2011 Cigarette smoking has a clear epidemiological association with lung diseases, characterised by chronic inflammation of both the bronchiolar and the interstitial lung compartments.
CERRI, Stefania +3 more
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Indeterminate cell histocytosis with naïve cells
Rare Tumors, 2013 Histiocytoses are a heterogeneous group of disorders characterized by proliferation and accumulation of cells of mononuclearmacrophage system and dendritic cells.
Sheren F Younes +3 more
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Common Acute Lymphoblastic Leukemia Ph＋ Following Langerhans Cell Histiocytosis in a Multi-Malformed Child with INV (9) (p12;q13) (mat):Case Report [PDF]
, 2010 The occurrence of Langerhans cell histiocytosis (LCH) and another malignancy in the same patient is infrequent but has been recognized. The genetic changes that could be responsible for LCH and/or concomitant leukemia development are obscure. To the best
Pavelić, Jasminka +2 more
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Erdheim-Chester disease detected with 99MTC MDP bone SPECT/CT
Journal of the Belgian Society of Radiology, 2012 Erdheim-Chester disease (ECD) is a rare non-Langerhans’ cell histiocytosis. Mild but permanent juxta-articular bone pain in mainly knees and ankles is the most frequent associated symptom.
G Ceulemans +8 more
doaj +1 more source
Rare Presentation of a Rare Orthopedic Pathology: Erdheim Chester Disease [PDF]
, 2017 In 1930, William Chester and pathologist Jakob Erdheim discovered the pathology currently known as Erdheim Chester disease. There are only approximately 249 histologically confirmed patients to have been diagnosed with this disease as noted in the ...
Samona J, Owen J, Martin S
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Growth of children with Langerhans cell histiocytosis [PDF]
, 1995 Conclusion: GH deficiency is not a common manifestation of LCH in childhood and GH provocation tests are only indicated when there is a poor or decelerating growth rate.
Egeler, R.M. (Maarten) +3 more
core +1 more source
An unusual case of intertrigo in an adult caused by purely cutaneous Langerhans cell histiocytosis [PDF]
, 2016 We report a case of persistent intertrigo in an adult, eventually diagnosed as cutaneous Langerhans cell histiocytosis (LCH). It is known that LCH has a predilection for intertriginous areas, however purely cutaneous disease as in our case, is uncommon ...
Baldacchino, Godfrey +3 more
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