Recent advances in interstitial lung disease research [PDF]
The interstitial lung diseases are a diverse collection of disorders characterized by impaired gas exchange, restricted physiology on lung function testing, and diffuse parenchymal lung infiltrates on radiography.
Vassallo, Robert
core
Erdheim-Chester Disease: a comprehensive review of the literature [PDF]
Erdheim-Chester Disease (ECD) is a rare form of non Langerhans' cell histiocytosis. Individuals affected by this disease are typically adults between their 5th and 7th decades of life. Males and females are almost equally affected.
Mirra Manevich-Mazor+2 more
core +1 more source
Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia
Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis. We report a fatal case of ECD with extensive cardiac involvement associated with a marginal zone lymphoma and monoclonal proteinemia in a young man.
Peter G. Pavlidakey+3 more
doaj +1 more source
Multisystem Langerhans' cell histiocytosis (Hand-Schüller-Christian disease) in an adult: a case report and review of the literature [PDF]
Langerhans' cell histiocytosis (LCH) is a rare and enigmatic clonal disorder that affects mainly children. It is characterized by single or multiple granulomatous mass lesions composed of cells with the Langerhans' cell phenotype.
Jaques, B.+3 more
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Somatic mutations in solid tumors: a spectrum at the service of diagnostic armamentarium or an indecipherable puzzle? The morphological eyes looking for BRAF and somatic molecular detections on cyto-histological samples [PDF]
This review article deals with the analysis and the detection of the morphological features associated with somatic mutations, mostly BRAF(V600E) mutation, on both cytological and histological samples of carcinomas.
Abildgaard+112 more
core +1 more source
Flat Topped Brown Papules on a Four-Year-Old Male
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Francisca Alves+3 more
doaj +1 more source
Cerebral tumor or pseudotumor? [PDF]
Pseudotumoral lesions are uncommon but important to identity lesions. They can occur during inflammatory diseases (systemic diseases, vasculitis, demyelinating diseases), infectious, and vascular diseases.
Bertrand, A.+6 more
core +3 more sources
Xanthoma Disseminatum with Tumor-Like Lesion on Face
Xanthoma disseminatum (XD) is a rare benign mucocutaneous xanthomatosis that is classified as a benign non-Langerhans cell histiocytosis. We report a 62-year-old man who presented with widespread yellow-brown papulonodular and tumoral lesions on face ...
Habib Ansarin+3 more
doaj +1 more source
Rare Presentation of a Rare Orthopedic Pathology: Erdheim Chester Disease [PDF]
In 1930, William Chester and pathologist Jakob Erdheim discovered the pathology currently known as Erdheim Chester disease. There are only approximately 249 histologically confirmed patients to have been diagnosed with this disease as noted in the ...
Samona J, Owen J, Martin S
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Caso para diagnóstico Case for diagnosis
Relatamos um caso de histiocitose cefálica benigna em uma criança do sexo masculino, de um ano e três meses de idade que desenvolveu múltiplas pápulas na região malar bilateralmente, sem outros comemorativos associados.
Maria de Fátima Guimarães Scotelaro Alves+4 more
doaj +1 more source