Unusual presentation of Rosai-Dorfman disease in a 14-month-old Italian child: a case report and review of the literature [PDF]
Background: Rosai-Dorfman disease (RDD) is a rare form of histiocytosis characterized by histiocyte proliferation within lymph nodes and extranodal tissue. Here we report an unusual presentation of RDD in an Italian toddler.
Bruzzi, Patrizia +5 more
core +2 more sources
A Rare Case of Multiorgan Involvement of Rosai Dorfman Disease in an Elderly Female
Sinus histiocytosis with massive lymphadenopathy (SHML), Rosai-Dorfman Disease, is a rare histiocytic syndrome first described by Rosai and Dorfman, most frequently seen in children and young adults.The disease is more common in males and in individuals ...
Rakesh Digambar Waghmare
doaj +1 more source
Histocytopathological diagnosis of Rosai–Dorfman disease: Case report
Sinus histiocytosis with massive lymphadenopathy (Rosai–Dorfman disease) being a rare benign proliferative self‐limiting disease of the cells of macrophage‐histiocyte family is of unknown etiology and presents with massive lymphadenopathy.
Zephania Saitabau Abraham +4 more
doaj +1 more source
Langerhan’s cell Histiocytosis of Sphenoid Sinus causing Vision Loss: A Case Report
Langerhan's cell histiocytosis is an uncontrolled proliferation of dendritic cells. The involvement of skull base is rare. Variable clinical presentation and multi organ involvement often warrant a multidisciplinary approach for a successful diagnosis ...
Suresh Mani +3 more
doaj +1 more source
A rare case of oral multisystem Langerhans cell histiocytosis [PDF]
Langerhans cell histiocytosis (LCH) is a rare disorder characterized by high proliferation of Langerhans dendritic cells. LCH is a solitary or multifocal disease that primarily involves bone tissue and often affects children and young men. A 29 years-old
Facciolo, Maria Teresa +4 more
core +1 more source
Langerhan’s cell histiocytosis (LCH) results from the proliferation of immunophenotypically and functionally immature, morphologically rounded Langerhan’s cells along with eosinophils, macrophages, lymphocytes, and, commonly, multinucleated giant cells ...
Seema Lale +2 more
doaj +1 more source
A Rare Case of a Systemic Non-Langerhans Histiocytosis Presenting with Diabetes Insipidus and a Tentorial Mass [PDF]
Introduction The histiocytoses are a group of clinically diverse diseases distinguished from one another based on the specific immunophenotype of the lesional cells, implying derivation from the same precursor cell.
Barros, MS, Guilherme +5 more
core +2 more sources
Management and treatment of sinonasal inverted papilloma [PDF]
Aims: The aim of this paper is to describe the surgical experience of 35 patients with Inverted Papilloma (IP) of paranasal sinuses and its recurrence rate after a year of follow-up.
Agrillo, Alessandro +6 more
core +1 more source
Discrepancy of target sites between clinician and cytopathological reports in head neck fine needle aspiration: Did I miss the target or did the clinician mistake the organ site? [PDF]
The diagnostic accuracy of fine needle aspiration cytology (FNAC) of head and neck lesions is relatively high, but cytologic interpretation might be confusing if the sample is lacking typical cytologic features according to labeled site by physician ...
Aledavood, A +9 more
core +2 more sources
Solitary extranodal Rosai-Dorfman disease of the mandible: an exceedingly rare presentation
Sinus histiocytosis with massive lymphadenopathy, generally known by the name of Rosai-Dorfman disease is a rare benign condition principally affecting cervical lymph nodes.
Ameer Hamza +2 more
doaj +1 more source

