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Amyloid: the International Journal of Experimental and Clinical Investigation: the Official Journal of the International Society of Amyloidosis, 2005 Item does not contain fulltextBACKGROUND: Hyper-IgD and periodic fever syndrome (HIDS) is an autosomal recessively inherited disorder characterized by recurrent episodes of fever and inflammation. Unlike other chronic inflammatory conditions, amyloidosis
J C H Van Der Hilst +2 more
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Das Hyper-IgD-Syndrom (The hyper-IgD-syndrome)
Zeitschrift f�r Rheumatologie, 1997We report on a 6-year-old Romanian girl with recently diagnosed hyper-IgD-syndrome. The leading symptom of this rare disease are periodic pyrexia, joint involvements (arthralgias/arthritis) and swollen lymph nodes. A permanent increase of alpha 1-acid glycoprotein fucosylation indicates persisting inflammation.
J. Suschke, J.-U. Walther
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Crescentic glomerulonephritis in hyper IgD syndrome
Pediatric Nephrology, 1999The hyperimmunoglobulinemia D syndrome (HIDS) is a well-defined entity resembling familial Mediterranean fever. HIDS is a systemic inflammatory disease associated with stimulation of T-cell-mediated immunity. These patients are at low risk for amyloidosis and are not known to develop nephropathy.
M, Tsimaratos +5 more
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Syndrome des hyper-IgD et grossesse
La Revue de Médecine Interne, 1998 F Sarrot-Reynauld, C Massot
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Treatment of adult hyper-IgD syndrome with canakinumab
The Journal of Allergy and Clinical Immunology: In Practice, 2015Hyper-IgD and periodic fever syndrome (HIDS) is a rare, autosomal-recessive autoinflammatory disease characterized by lifelong recurrent episodes of systemic inflammation. HIDS frequently presents in infancy with intermittent fevers lasting from 4 to 7 days, recurring every 4 to 6 weeks.
Casey D, Curtis, Charity C, Fox
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Syndrome hyper-IgD: à propos d'une observation
La Revue de Médecine Interne, 1998 J Fach +7 more
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Hyper-IgD syndrome with novel mutation in a Japanese girl
Modern Rheumatology, 2008Hyperimmunoglobulin D and periodic fever syndrome (HIDS) is an autosomal recessive auto-inflammatory disorder characterized by recurrent febrile attacks with lymphadenopathy, abdominal distress, skin eruptions and joint involvement. We discuss the case of a 15-year-old Japanese girl who had presented with periodic fever, hepatosplenomegaly and ...
Takuya, Naruto +5 more
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A patient with hyper-IgD syndrome responding to simvastatin treatment
European Journal of Internal Medicine, 2008The hyper-IgD syndrome (HIDS) is an autosomal recessively inherited auto-inflammatory syndrome, caused by deficient enzyme activity of mevalonate kinase (MVK), an enzyme in the isoprenoid pathway. Patients present with a long history of recurrent fever attacks, accompanied by abdominal pain, skin lesions, lymphadenopathy and arthralgia.
H, Attout +4 more
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