Results 91 to 100 of about 6,740 (215)

Evidence-based diagnosis and treatment of macrophage activation syndrome in systemic juvenile idiopathic arthritis. [PDF]

, 2017
Background Macrophage activation syndrome (MAS) is a severe and potentially lethal complication of several inflammatory diseases but seems particularly linked to systemic juvenile idiopathic arthritis (sJIA).
Antón López, Jordi, Boom, V., Lahdenne, P., Quartier, Pierre, Ravelli, Angelo, Vastert, Sebastiaan J., Wulffraat, Nico   +6 more
core   +1 more source

Recent acquisitions in the pathophysiology, diagnosis and treatment of disseminated intravascular coagulation [PDF]

, 2006
Disseminated intravascular coagulation (DIC) is a disorder characterized by both acute generalized, widespread activation of coagulation, which results in thrombotic complications due to the intravascular formation of fibrin, and diffuse hemorrhages, due
Lippi Giuseppe, Franchini Massimo, Manzato Franco   +2 more
core   +2 more sources

Congenital hypofibrinogenemia.

Indian pediatrics, 2004
Congenital afibrinogenemia/hypofibrinogenemia is an extremely rare coagulation disorder. We describe a case of congenital hypofibrinogenemia in a 6-year female child, who presented with recurrent ecchymotic spots with no frank bleeding.
Neeraj, Awasthy, K C, Aggarwal, H, Gupta, S, Saluja   +3 more
openaire   +1 more source

Acute Promyelocytic Leukemia Associated with Hypofibrinogenemia [PDF]

Blood, 1963
Abstract This study of 17 cases further establishes acute promyelocytic leukemia with hypofibrinogenemia as a distinct entity. This disease has a rapid course characterized by severe hemorrhagic manifestations and a poor response to therapy.
openaire   +2 more sources

Diagnostic and management practices for inherited fibrinogen disorders: a nationwide survey of Italian Hemophilia Treatment Centers

Bleeding, Thrombosis and Vascular Biology
Background: inherited fibrinogen disorders are characterized by a spectrum of quantitative or qualitative fibrinogen deficiency associated with both a hemorrhagic and thrombotic risk.
Renato Marino, Silvia Linari, Marzia Leotta, Antonio Coppola, Chiara Biasoli, Maria Elisa Mancuso, Flora Peyvandi, Cristina Santoro, Ezio Zanon, Rita Carlotta Santoro   +9 more
doaj   +1 more source

Chiari I Malformation and Intramedullary Hemorrhage in a Female Patient with Klippel Trenaunay Syndrome: A Rare Case Report Study [PDF]

International Journal of Caring Sciences
Chiari I Malformation and Intramedullary Hemorrhage in a Female Patient with Klippel Trenaunay Syndrome: A Rare Case Report ...
Kalliopi Magounaki, Emmanouil Kalafatis, Dimitris Stergiou, Maria Tzaki, Dionysios Vekios, Aggelos Papakalos and Ioannis Kyriazis   +5 more
doaj  

Pancreatite Hipertrigliceridémica: Tratamento Convencional Versus Troca Plasmática Terapêutica [PDF]

, 2017
Introduction: Acute pancreatitis (AP) induced by hypertriglyceridemia (HTG) can be treated with therapeutic plasma exchange (TPE), resulting in rapid reduction of triglyceride level. However, there are no definitive comparative studies that prove the
Aragão, A, Carvalho, A, Ferreira, DM, Ferreira, M, Ferreira, M, Fonseca, JP, Lobo, F, Mendes, PA, Tomáz, J   +8 more
core  

Increasing hematocrit above 28% during early resuscitative phase is not associated with decreased mortality following severe traumatic brain injury [PDF]

, 2018
Background: To prevent iatrogenic damage, transfusions of red blood cells should be avoided. For this, specific and reliable transfusion triggers must be defined.
Brenni, Mirko, Béchir, Markus, Cottini, Silvia, Flückiger, Carole, Keel, Marius, Ludwig, Silke, Sommerfeld, Jutta, Stocker, Reto, Stover, John   +8 more
core  

A novel mutation in the FGG gene causes hypofibrinogenemia in a Chinese family

Hereditas
Congenital fibrinogen disorders are a group of coagulation deficiencies caused by fibrinogen defects and are divided into four types, including afibrinogenemia, hypofibrinogenemia, dysfibrinogenemia, and hypodysfibrinogenemia. In this study, we collected
Xiaoying Xie, Juan Du, Shunkang Geng, Baoqin Yi, Qingpu Li, Jiangcheng Zuo   +5 more
doaj   +1 more source

A Case Report of Crotalidae Immune F(ab’)2-associated Coagulopathy Recurrence in a Preschool-age Child

Clinical Practice and Cases in Emergency Medicine
Introduction: Pit viper envenomation may cause coagulopathy. The coagulopathy has been treated with crotalidae polyvalent immune fragment antigen-binding (Fab) ovine antivenom for the last few decades in the United States and usually corrects the acute ...
Jean C.Y. Lo, E. Lea Walters, Brian Wolk
doaj   +1 more source