Results 71 to 80 of about 5,300 (203)

Peste des Petits Ruminants: Aetiology, Pathology, Immunology, Disease Status in Africa, Diagnosis, Control, Prevention and Treatment: A Review

Notulae Scientia Biologicae, 2019
Peste des petits ruminants (PPR) is a disease of economic and veterinary importance leading to considerable economic losses. PPR affects small domestic and wild ruminants.
Iniobong C. I. UGOCHUKWU, Chukwunonso K. EZEASOR, Onyinyechukwu A. AGINA, Davinson C. ANYOGU, Ijeoma C. CHUKWUDI, Sunday I. IDOKO, Emmanuel I. UGOCHUKWU   +6 more
doaj   +1 more source

GIANT HEMANGIOENDOTHELIOMA WITH THROMBOCYTOPENIA AND HYPOFIBRINOGENEMIA [PDF]

American Journal of Roentgenology, 1969
A 17 month old child with a large subcutaneous hemangioendothelioma with platelet trapping and hypofibrinogenemia is reported.Despite multiple transfusions, splenectomy and corticosteroid therapy there was no improvement.Administration of roentgen therapy with a cumulative dose of 1,825 r during a time interval of 7 months resulted in complete ...
O K, Williams, F W, Van Buskirk, S, Burns, R W, Mellish   +3 more
openaire   +2 more sources

Immune Dysregulation in Branched Chain Organic Acidemias

Journal of Inherited Metabolic Disease, Volume 49, Issue 4, July 2026.
ABSTRACT Organic acidemias (OAs) are a group of inherited disorders, most commonly caused by defects in mitochondrial enzymes involved in amino acid and fatty acid metabolism. While they characteristically present with metabolic and neurological crises, growing evidence reveals a significant burden of chronic immune dysregulation in some disorders and ...
Abdul L. Shakerdi, Jack Drda, Justin A. Dutta, Jerry Vockley   +3 more
wiley   +1 more source

EBV‐associated hemophagocytic lymphohistiocytosis complicated by severe coagulation disorders and opportunistic infections: case report of a survivor

Clinical Case Reports, 2018
Key Clinical Message The possibility of hemophagocytic lymphohistiocytosis should always be kept in mind when examining/treating a patient with fever of unknown origin and sepsis‐like symptoms.
Kirsten Saevels, Dominique Robert, Sylvie Van den Broeck, Ronald Malfait, Alain Gadisseur, Philippe Jorens, Anke Verlinden   +6 more
doaj   +1 more source

Massive hemopericranium following trivial trauma in a child with hypofibrinogenemia: A case report and review of the literature

Indian Journal of Neurosurgery, 2014
Subgaleal hematoma is a potentially life-threatening extracranial bleed that occurs most commonly in neonates after difficult instrumental deliveries. Its occurrence beyond the neonatal period is rare and is often associated with head trauma involving ...
Rajeev Sharma, Laxmi Naraian Gupta
doaj   +1 more source

Maternal Severity and Diagnostic Validity of the Revised Japanese Criteria for Obstetric Disseminated Intravascular Coagulation: A Retrospective Observational Study

Journal of Obstetrics and Gynaecology Research, Volume 52, Issue 7, July 2026.
ABSTRACT Aim In Japan, the diagnostic criteria for obstetric disseminated intravascular coagulation (DIC) were revised in 2024. This study aimed to evaluate the clinical utility of the revised obstetric DIC criteria, defined as the ability to identify patients at higher risk of severe maternal outcomes at presentation.
Yutaro Takahashi, Soichiro Obata, Sayuri Nakanishi, Ryosuke Shindo, Shigeru Aoki, Etsuko Miyagi   +5 more
wiley   +1 more source

Genetic Analysis of Afibrinogenemia and Hypofibrinogenemia: Novel Mutations in the FGB Gene in the Turkish Population

, 2020
Introduction: Congenital afibrinogenemia is a rare autosomal recessive disorder characterized by bleeding that varies from mild to severe and by complete absence or extremely low levels of plasma and platelet fibrinogen.
Ozkan, Didem Torun, Sarper, Nazan, Akar, Nejat   +2 more
core   +1 more source

Extranodal natural killer/T‐cell lymphoma: From fatal to curable

CA: A Cancer Journal for Clinicians, Volume 76, Issue 4, July/August 2026.
Abstract Extranodal natural killer (NK)/T‐cell lymphoma (ENKTCL) is one of the most aggressive non‐Hodgkin lymphomas characterized by NK‐cell or T‐cell origins, a geographic prevalence in Asian and South American populations, and Epstein–Barr virus (EBV) infection.
Jie Xiong, Yok‐Lam Kwong, Laurence de Leval, Shu‐Nan Qi, Choon Kiat Ong, Philippe Gaulard, Arnaud Jaccard, Steven M. Horwitz, Ye‐Xiong Li, Sai‐Juan Chen, Ritsuro Suzuki, Won Seog Kim, Wei‐Li Zhao   +12 more
wiley   +1 more source

ERDHEIM‐Chester Disease: Two Fatal Cases With Unusual Presentations

Clinical Case Reports, Volume 14, Issue 6, June 2026.
Fluorodeoxyglucose positron emission tomography‐computed tomography (FDG PET‐CT) demonstrated markedly increased metabolic activity in serosal surfaces including pericardium, pleura, and renal fascia, as well as diffuse uptake along vascular walls, particularly the entire aorta.
Ribero‐Vargas Daniel Andres, C. Álvarez Payares José, Murillo‐Pérez Juliana   +2 more
wiley   +1 more source

Dysfibrinogenemia and hypofibrinogenemia - Spectrum of pathogenic variants in Slovak patients

Biomedical Papers
Introduction. Congenital hypofibrinogenemia (CH) and congenital dysfibrinogenemia (CD) are rare coagulation disorders caused by quantitative or qualitative defects in the fibrinogen gene.
Dominika Jaraskova, Jan Chandoga, Angelika Batorova, Tatiana Prigancova, Miriama Juhosova, Pavol Durina, Alzbeta Vavrova, Silvia Dallemule, Robert Petrovic, Anna Kyselova, Denisa Jankovicova, Daniel Bohmer   +11 more
doaj   +1 more source