Infantile spams without hypsarrhythmia: A study of 16 cases [PDF]
In this study, we present the electroclinical features and evolution of patients with epileptic spasms (ES) in clusters without hypsarrhythmia and with or without focal or generalized paroxysmal discharges on the interictal EEG. We also discuss how to nosologically define these cases.Between February 1, 1990, and December, 2009, sixteen patients met ...
Caraballo, Roberto Horacio+7 more
core +7 more sources
ACTH Therapy in Epileptic Spasms without Hypsarrhythmia
The short and long-term effects of adrenocorticotrophic hormone (ACTH) in 30 children ages 11 to 86 months (median 29 months) with epileptic spasms (ES) without hypsarrhythmia were analyzed at Tokyo Women’s Medical University, Japan.
J Gordon Millichap
doaj +5 more sources
Hypsarrhythmia in epileptic spasms: Synchrony in chaos [PDF]
Hypsarrhythmia is an electroencephalographic pattern associated with epileptic spasms and West syndrome. West syndrome is a devastating epileptic encephalopathy, originating in infancy. Hypsarrhythmia has been deemed to be the interictal brain activity, while the electrodecremental event associated with the spasms is denoted as the ictal event.
Vera Nenadovic+3 more
semanticscholar +5 more sources
The impact of hypsarrhythmia on infantile spasms treatment response: Observational cohort study from the National Infantile Spasms Consortium [PDF]
Peer Reviewedhttps://deepblue.lib.umich.edu/bitstream/2027.42/141801/1/epi13937_am.pdfhttps://deepblue.lib.umich.edu/bitstream/2027.42/141801/2/epi13937 ...
Anup D. Patel+22 more
core +5 more sources
Hypsarrhythmia is associated with widespread, asymmetric cerebral hypermetabolism [PDF]
Hypsarrhythmia is the interictal EEG pattern most often associated with infantile spasms. We set out to evaluate the metabolic impact of hypsarrhythmia among patients with infantile spasms by contrasting regional cerebral metabolic activity among children with and without hypsarrhythmia.Patients with video-EEG confirmed infantile spasms who underwent ...
Shaun A. Hussain+2 more
semanticscholar +5 more sources
Infantile Spasms, Hypsarrhythmia, and Adrenoleukodystrophy (ALD)
An 8 1/2 month-old girl with seizures beginning at 5 days, hypsarrhythmia in the EEG, severe retardation, and a clinical diagnosis of infantile spasms was discovered to have biochemical and pathological features of adrenoleukodystrophy, as reported from ...
J Gordon Millichap
doaj +5 more sources
Pseudo hypsarrhythmia: An early marker of angelman syndrome
Annals of Indian Academy of Neurology ¦ Volume 22 ¦ Issue 3 ¦ July-September 2019 359 disorders. Ann Endocrinol 2007;68:173-6. 4. Patnaik SK, Upreti V, Dhull P. Steroid responsive encephalopathy associated with autoimmune thyroiditis (SREAT) in childhood.
Sumeet R Dhawan+3 more
semanticscholar +6 more sources
Congenital rubella associated with hypsarrhythmia. [PDF]
A child with acute lymphoblastic leukaemia complicated by prolonged gastrointestinal and skin haemorrhages due to profound thrombocytopenia finally died of thrombotic occlusions of major cerebral arteries due to mucormycosis. Biopsy of any suspect lesion is needed urgently before prolonged therapy with amphotericin B is started.
D Harvey, R K Oates
openaire +4 more sources
Involvement of the Thalamus, Hippocampus, and Brainstem in Hypsarrhythmia of West Syndrome: Simultaneous Recordings of Electroencephalography and fMRI Study [PDF]
BACKGROUND AND PURPOSE: West syndrome is a developmental and epileptic encephalopathy characterized by epileptic spasms, neurodevelopmental regression, and a specific EEG pattern called hypsarrhythmia.
Y. Maki+14 more
semanticscholar +2 more sources