Results 141 to 150 of about 37,394 (238)

Hyperimmunoglobulinemia D and periodic fever : A new syndrome [PDF]

open access: yes, 1984
Contains fulltext : 4434.pdf (publisher's version ) (Open ...
Furth, R. van   +6 more
core   +1 more source

野生型转甲状腺素蛋白心脏淀粉样变性病例1例

open access: yesZhongguo shiyan zhenduanxue, 2023
转甲状腺素蛋白心脏淀粉样变(transthyretin cardiac amyloidosis, ATTR-CA)是除外免疫球蛋白轻链心脏淀粉样变(immunoglobulin light chain amyloidosis, AL-CA)最常见的心脏淀粉样变(cardiac amyloidosis, CA)[1]。ATTR-CA患者生活质量差、生存率低[2]。
翟书慧, 王丹, 赵绮旎, 刘龙
doaj  

Cardiac amyloidosis

open access: yesAnnales Academiae Medicae Silesiensis
Amyloidosis is a rare disease characterized by an abnormal accumulation of the amyloid protein in tissues. Amyloidosis can be divided into two main subtypes: transthyretin amyloidosis (ATTR-CA) and immunoglobulin light chain amyloidosis (AL-CA ...
Magdalena Balwierz   +2 more
doaj   +1 more source

Stronger inflammatory/cytotoxic T cell response in women identified by microarray analysis [PDF]

open access: yes, 2008
Women develop chronic inflammatory autoimmune diseases like lupus more often than men. The mechanisms causing the increased susceptibility are incompletely understood, although estrogen is believed to contribute.
Anura Hewagama   +4 more
core   +1 more source

Syndrome in question. Immunoglobulin light chain amyloidosis.

open access: yesAnais brasileiros de dermatologia, 2015
Immunoglobulin light chain amyloidosis is the most common acquired systemic amyloidosis. Its presentation is often insidious and progressive, which may delay diagnosis. The authors describe a rare case of immunoglobulin light chain amyloidosis in a 34-year-old man with scleroderma-like manifestation substantiated by multifarious laboratory ...
Han, Ma   +4 more
openaire   +1 more source

Refractory IgM AL amyloidosis with massive soft tissue tumors: Rescue with zanubrutinib. A case report

open access: yesCurrent Problems in Cancer: Case Reports
Waldenström macroglobulinemia (WM) is a rare indolent B-cell non-Hodgkin lymphoma with lymphoplasmacytic morphology, associated with immunoglobulin M (IgM) monoclonal gammopathy. The coexistence of WM and immunoglobulin light chain (AL) amyloidosis is an
Piotr Jachimowski   +5 more
doaj   +1 more source

Immunoglobulin light chain amyloidosis involved multiple organs [PDF]

open access: yesQJM: An International Journal of Medicine, 2019
J, Bai, J, Qiao, H, Fang
openaire   +2 more sources

Amyloid Neuropathy: From Pathophysiology to Treatment in Light‐Chain Amyloidosis and Hereditary Transthyretin Amyloidosis

open access: yesAnnals of Neurology
Amyloid neuropathy is caused by deposition of insoluble β‐pleated amyloid sheets in the peripheral nervous system. It is most common in: (1) light‐chain amyloidosis, a clonal non‐proliferative plasma cell disorder in which fragments of immunoglobulin ...
Pitcha Chompoopong   +3 more
semanticscholar   +1 more source

A case of pulmonary transthyretin amyloidosis with concurrent mycobacterial tuberculosis infection

open access: yesRespirology Case Reports
Amyloidosis is a pathological deposition disease that causes a spectrum of organ dysfunction. Pulmonary involvement is generally associated with immunoglobulin light chain type (AL) amyloid. Transthyretin (ATTR) amyloid build up in the lung is thought to
Hanson Siu   +5 more
doaj   +1 more source

Definition of organ involvement and treatment response in immunoglobulin light chain amyloidosis (AL): A consensus opinion from the 10th International Symposium on Amyloid and Amyloidosis

open access: yesAmerican journal of hematology/oncology, 2005
M. Gertz   +12 more
semanticscholar   +1 more source

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