Results 31 to 40 of about 18,484 (199)

Intermediate-dose cytarabine is an effective therapy for adults with non-Langerhans cell histiocytosis

Orphanet Journal of Rare Diseases, 2022
Background Non-Langerhans cell histiocytosis, including Erdheim–Chester disease (ECD), Rosai–Dorfman disease (RDD), indeterminate cell histiocytosis (ICH), and unclassified histiocytosis, is a rare disorder lacking a standard treatment strategy.
Ting Liu, Hua-cong Cai, Hao Cai, Miao Chen, Wei Zhang, Jian Li, Dao-bin Zhou, Xin-xin Cao   +7 more
doaj   +1 more source

A Diagnostic Mimic of Lung Cancer: Nodular Pulmonary Amyloidosis Presenting With Cystic Changes. [PDF]

Respirol Case Rep
A 62‐year‐old man with coal workers' pneumoconiosis and a heavy smoking history presented with progressive respiratory symptoms and cystic lung lesions. Surgical biopsy revealed localised AL (kappa) nodular pulmonary amyloidosis, highlighting the need to consider amyloidosis in the differential diagnosis of cystic lung disease with indeterminate ...
Peshin S, Kulkarni V, Bashir F, Iftekhar R, Kapadia J, Donovan M, Nader E.   +6 more
europepmc   +2 more sources

Rare variants of histiocytic tumors: peculiarities of diagnosis and choice of treatment (literature review)

Онкогематология, 2022
Histiocytic tumors are a highly heterogeneous group of diseases, with Langerhans cell histiocytosis occupying the main place among it. Despite the rare frequency of occurrence, long-term analysis of clinical, morpho-immunological and molecular-biological
T. T. Valiev, O. D. Gurieva, A. I. Pavlovskaya   +2 more
doaj   +1 more source

CD1a-positive dendritic cell-enriched pigmented purpuric dermatosis in association with dyslipidemia

Journal of Dermatology and Dermatologic Surgery, 2022
Indeterminate cells (ICs) are dendritic cells (DCs) that share the histologic features of Langerhans cells and macrophages but lack Birbeck granules. It remains unclear whether IC histiocytosis is a separate disease entity or a reactive process.
Tiffany Hinojosa, Daniel J Lewis, Madeleine Duvic, Carlos A Torres-Cabala   +3 more
doaj   +1 more source

LANGERHANS CELLS HISTIOCYTOSIS [PDF]

, 2023
Langerhans cell histiocytosis (LCH) merupakan salah satu penyakit terbanyak dari histiositosis dengan 2,0–5,4 kasus/100 juta populasi diseluruh dunia ...
Murti, Krisna, Ulfa, Maria
core   +2 more sources

CURRENT THERAPIES PRIMARY LANGERHANS CELL HYSTIOCYTOSIS

Hematology, Transfusion and Cell Therapy, 2023
Langerhans cell histiocytosis (LCH) is a neoplastic histiocytic disorder that most commonly affects bones and skin, but it can also involve the bone marrow, liver, spleen, lungs, pituitary gland/central nervous system, and other organs.
Deniz Tuğcu
doaj   +1 more source

Lymphoid Interstitial Pneumonia Without Known Cause: Diagnostic Work Up and Differential Considerations. [PDF]

Respirol Case Rep
We present a case of diffuse cystic lung disease without any known underlying systemic disorder, biopsy confirmed as lymphoid interstitial pneumonia (LIP). This case highlights the benefit of histological confirmation where there is diagnostic uncertainty and the clinical situation permits, particularly in the setting of symptomatic deterioration ...
Lau HX, Krebs L, Sim S, Reddy T.
europepmc   +2 more sources

Central nervous system crystal-storing histiocytosis: A case report and literature review. [PDF]

Eur J Neurol
Abstract Background Crystal‐storing histiocytosis (CSH) is a rare form of histiocytosis with intralysosomal accumulations of immunoglobulins or paraproteins that aggregate as crystals. Central nervous system (CNS) involvement of CSH is uncommon but should be considered in cases of persistent parenchymal enhancement on neuroimaging.
Nathoo N, Larson DP, Guo Y, Giannini C, Lucchinetti CF, Micallef IN, Rech KL, Jevremovic D, Lachance DH, Abeykoon JP, Go RS, Tobin WO.   +11 more
europepmc   +2 more sources

BRAF V600E mutations in urine and plasma cell-free DNA from patients with Erdheim-Chester disease. [PDF]

, 2014
Erdheim-Chester disease (ECD) is a rare histiocytosis with a high prevalence of BRAF V600E mutation (>50% of patients). Patients with BRAF-mutant ECD can respond to BRAF inhibitors.
Cabrilo, Goran, Erlander, Mark G, Hassaine, Latifa, Holley, Veronica R, Janku, Filip, Kosco, Karena, Kurzrock, Razelle, Leppin, Lorieta, Lin, Patrick P, Meric-Bernstam, Funda, Poole, Jason C, Stepanek, Vanda M, Vibat, Cecile Rose T   +12 more
core   +3 more sources

BRAF V600E-Positive Multisite Langerhans Cell Histiocytosis in a Preterm Neonate [PDF]

, 2013
Hemorrhagic pustules with a “blueberry muffin” appearance accompanied by respiratory failure in a neonate present a challenging differential diagnosis that includes infections and neoplasms.
Aslam, Muhammad, Badalian-Very, Gayane, Bates, Sara V., Degar, Barbara A., Fleck, Patricia, Green, Adam L., Lakshmanan, Ashwini, Rollins, Barrett J., Terry, Jefferson   +8 more
core   +3 more sources