Results 71 to 80 of about 1,120 (144)

US, CT and MRI findings in a case of diffuse lymphangiomatosis and cystic hygroma

, 2008
Lymphangiomatosis is a rare disease with multifocal lymphatic proliferation that typically occurs during childhood and involves multiple parenchymal organs including the lung, liver, spleen, bone, and skin.
Erturk, S. M., Basak, M., Ozel, A, Uysal, E., CANTISANI, VITO, Dokucu, A. I.   +5 more
core   +1 more source

Upfront radiotherapy for diffuse lymphangiomatosis in a child

, 2016
Lymphangiomatosis is an extremely rare multisystem disorder resulting from congenital malformations of lymphatic development mainly affecting the pulmonary and skeletal systems without a preset therapeutic approach.
Abhishek Purkayastha, Neelam Sharma, Shuvendu Roy, Chetan Agarwal   +3 more
core   +1 more source

Unusual clinical manifestation of lymphangiomatosis [PDF]

, 2011
A 6-year- old boy presented with disseminated intravascular coagulation and was diagnosed with lymphangiomatosis. Disseminated intravascular coagulation develops in a minority of cases. Bone lesions were present on his left shoulder.
C Heijmans, O Prieur, N Damry, C Christophe   +3 more
core   +1 more source

Systemic generalised lymphangiomatosis: unknown aetiology and a challenge to treat

, 2021
We describe a case of a woman diagnosed at the age of 35 years with a generalised mediastinal and abdominal lymphangiomatosis associated with a protein losing enteropathy, who successfully improved when treatment with sirolimus was initiated.SCOPUS: ar ...
Velkeniers, Brigitte, Van Meerhaeghe, Tess, Vandenbroucke, Frederik, Tess Van Meerhaeghe, Brigitte Velkeniers, Frederik Vandenbroucke   +5 more
core   +1 more source

Thoracic lymphangiomatosis in a child

, 2004
An 8-year-old boy who presented with a mediastinal mass, pulmonary infiltrates, and disseminated intravascular coagulation was diagnosed with lymphangiomatosis. Despite medical management, he developed multiple organ failure and died. The authors discuss
Alvarez, Ofelia A, Kjellin, Ingrid, Zuppan, Craig W   +2 more
core   +1 more source

Splenic lymphangiomatosis showing rapid growth during lactation: a case report. [PDF]

, 2010
Splenic lymphangiomatosis is a very rare condition that, from 1990 to date, has been described only nine times. In the present report, we describe the first case of splenic lymphangiomatosis with rapid growth during lactation in a 35-year-old woman.
PATTI, Rosalia, DI VITA, Gaetano Giuseppe, Iannitto, E   +2 more
core   +1 more source

Mosaicism of Vascular Origin

JEADV Clinical Practice, Volume 4, Issue 3, Page 697-699, August 2025.
Olivia Boccara
wiley   +1 more source

Kaposiform Lymphangiomatosis: Update on Outcomes and Use of Sirolimus As a Therapeutic Intervention

Blood, 2018
Abstract Background: Kaposiform lymphangiomatosis (KLA) is a rare, aggressive lymphatic malformation that can lead to significant morbidity and mortality (Croteau et al 2014). First described as a distinct entity from generalized lymphatic anomaly (GLA) in 2014, KLA is histologically defined by spindled "kaposiform ...
Whitney Eng, Hasan Al-Sayegh, Clement Ma, Denise Adams   +3 more
openaire   +1 more source

Surgical treatment of a huge kaposiform hemangioendothelioma in the chest wall: A case study

, 2016
Kaposiform hemangioendothelioma, a rare vascular pediatric tumor often associated with Kasabach–Merritt phenomenon, is characterized by severe thrombocytopenia and consumptive coagulopathy.
Xiaonan Guo, Changxian Dong, Yubin Gong
core   +1 more source

Laparoscopic management in a rare case of bilateral perirenal lymphangiomatosis

, 2013
Lymphangiomas are lymphatic malformations commonly seen around the neck, axillary region and the mediastinum. Perirenal lymphangiomatosis is very rare with only a few cases being reported in literature.
RM Meyyappan, R M Meyyappan, S Ravikumar, M Gopinath   +3 more
core   +1 more source