Results 51 to 60 of about 1,120 (144)
Congenital cutaneous multifocal kaposiform hemangioendothelioma
, 1999 Kaposiform hemangioendothelioma is a rare vascular neoplasm in children often associated with Kasabach-Merritt syndrome. The tumor usually presents in retroperitoneal location and is rarely present at birth.
R. Gianotti, C. Gelmetti, E. Alessi
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Case report: Perinephric lymphangiomatosis
, 2010 Perirenal lymphangiomatosis is a rare benign malformation of the lymphatic system. We report here a case of bilateral perirenal and parapelvic involvement with a normal excretory collecting ...
Bhawna Dev +3 more
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Sigmoid colon obstruction due to Kaposiform Haemangioendothelioma
, 2021 Background: Kaposiform Haemangioendothelioma (KHE) is a very rare, benign but locally aggressive vascular tumour. Its incidence is 1/100000, and it is most commonly found in the cutaneous tissues of the extremities.
Bourke, C +5 more
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Frontiers in OncologyComplex lymphatic anomalies (CLAs) are rare vascular anomalies characterized by abnormal proliferation of lymphatic and blood vessels, often resulting in multisystem involvement with heterogeneous clinical manifestations.
Yujia Zhang +8 more
doaj +1 more source
An Examination of Sirolimus's Role in Endothelial Cells of Kaposiform Haemangioendothelioma
Journal of Cellular and Molecular Medicine, Volume 29, Issue 20, October 2025.ABSTRACT Kaposiform haemangioendothelioma (KHE) research faces challenges due to the lack of established cell lines and suitable animal models. Our study aimed to establish KHE cell lines, spheroids and refine murine models to mimic disease characteristics, advancing our understanding of KHE pathogenesis and exploring novel therapies. Primary KHE cells
Yanan Li +4 more
wiley +1 more source
Generalized Lymphangiomatosis Presenting as Cardiomegaly
, 2007 Lymphangioma refers to the local proliferation of well-differentiated lymphatic tissue. Generalized lymphangiomatosis is rare. We report a previously healthy 8-month-old infant who suffered from tachypnea with mild fever for 2 weeks.
Yi-Ling Chen +4 more
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Targeted Medical Therapies for Vascular Anomalies: A Clinical Review
American Journal of Medical Genetics Part C: Seminars in Medical Genetics, Volume 199, Issue 3, Page 161-175, September 2025.ABSTRACT Vascular anomalies represent a broad spectrum of disorders characterized by aberrant blood or lymphatic vessel development, which can lead to complex clinical phenotypes. Historically, vascular anomalies were classified solely on the basis of their clinical and histopathologic features.
Whitney Eng
wiley +1 more source
Case report - An acute presentation of lymphangiomatosis.
, 2012 IntroductionLymphangioma is an uncommon malformation of lymphatic system. Multiple colonic lymphangioma named as lymphangiomatosis is considered an extremely rare disease.Presentation of caseWe report a case of colonic lymphangiomatosis presenting as ...
Nason, G J +3 more
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Lymphangiomatosis of the arm with massive osteolysis. A case report. [PDF]
, 1987 A case of massive osteolysis of the arm is described where the typical bony lesions were associated with soft tissue ...
Mora R, Ceciliani L., PAZZAGLIA, Ugo
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RAS Pathway Mutations and Therapeutics in Vascular Anomalies
Pediatric Blood &Cancer, Volume 72, Issue 5, May 2025.ABSTRACT Vascular anomalies (VAs) are a diverse group of vascular tumors and vascular malformations (VMs). VMs are characterized by abnormal vessel development, overgrowth, and dysfunction. Coagulopathy, edema, and effusions can cause severe morbidity and mortality in children and adults with these diseases. Germline or somatic mutations in the RAS/RAF/
Sara Alharbi +4 more
wiley +1 more source