Results 21 to 30 of about 13,250 (289)

Effectiveness of pulmonary rehabilitation in lymphangioleiomyomatosis

Indian Journal of Respiratory Care, 2021
Lymphangioleiomyomatosis (LAM) is a cystic lung disease frequently associated with reduced exercise capacity, mostly affecting young women. The disease is characterized by progressive pulmonary cystic change, recurrent pneumothorax, chylous pleural ...
Manivel Arumugam, Senthil Dhanasekaran, Kancherla Roopa, Pitchaimani Govindharaj   +3 more
doaj   +1 more source

Sirolimus reduces the risk of pneumothorax recurrence in patients with lymphangioleiomyomatosis: a historical prospective self-controlled study

Orphanet Journal of Rare Diseases, 2022
Background Spontaneous pneumothorax has a high incidence and high rate of recurrence in patients with lymphangioleiomyomatosis (LAM). The risk factors for pneumothorax and the effects of sirolimus on pneumothorax in patients with LAM are unknown.
Chongsheng Cheng, Wenshuai Xu, Yani Wang, Tengyue Zhang, Lu Yang, Wangji Zhou, Danjing Hu, Yanli Yang, X. Tian, Kaifeng Xu   +9 more
semanticscholar   +1 more source

Airspace Enlargement with Fibrosis in a Young Heavy Smoker Mimicking Diffuse Cystic Lung Disease

Medicina, 2022
The widespread use of computed tomography (CT) has led to the increased recognition of cystic lung lesions. Multiple pulmonary cysts can be observed in heterogeneous disorders called diffuse cystic lung diseases (DCLDs), which include pulmonary ...
Kyungsoo Bae, Hyo Jung An, Kyung Nyeo Jeon   +2 more
doaj   +1 more source

YouTube-videos for patient education in lymphangioleiomyomatosis?

Respiratory Research, 2022
Background The Internet is commonly used by patients to acquire health information. To date, no studies have evaluated the quality of information available on YouTube regarding lymphangioleiomyomatosis (LAM).
F. Wilkens, C. Ganter, Katharina Kriegsmann, H. Wilkens, N. Kahn, G. Goobie, C. Ryerson, M. Kreuter   +7 more
semanticscholar   +1 more source

A Clinical Case of Pulmonary Lymphangioleiomyomatosis

Туберкулез и болезни лёгких, 2022
The article describes a clinical case of pulmonary lymphangioleiomyomatosis (LAM) in a 44-year-old female Patient N., who has been suffering from this disease for a long time.
S. S. Kazakova, E. V. Аftaeva, Z. V. Zinovieva   +2 more
doaj   +1 more source

Tissue‐Engineered Disease Modeling of Lymphangioleiomyomatosis Exposes a Therapeutic Vulnerability to HDAC Inhibition

Advanced Science, 2023
Lymphangioleiomyomatosis (LAM) is a rare disease involving cystic lung destruction by invasive LAM cells. These cells harbor loss‐of‐function mutations in TSC2, conferring hyperactive mTORC1 signaling. Here, tissue engineering tools are employed to model
Adam Pietrobon, Julien Yockell‐Lelièvre, Nicole Melong, Laura J. Smith, Sean P. Delaney, Nadine Azzam, Chang Xue, Nishanth Merwin, Eric Lian, Alberto Camacho‐Magallanes, Carole Doré, Gabriel Musso, Lisa M. Julian, Arnold S. Kristof, Roger Y. Tam, Jason N. Berman, Molly S. Shoichet, William L. Stanford   +17 more
doaj   +1 more source

Refractory chylous effusions in lymphangioleiomyomatosis patient post lung transplant

SAGE Open Medical Case Reports, 2020
Lymphangioleiomyomatosis is a rare systemic disorder of unknown etiology that affects young women almost exclusively. Chylous effusions are known to be associated with lymphangioleiomyomatosis and may be difficult to treat.
Samuel Jacob, Mojahid Ali, Magdy M El-Sayed Ahmed, Maxim Itkin, Tathagat Narula, Si Pham, David Erasmus   +6 more
doaj   +1 more source

Lymphangioleiomyomatosis of the lungs: features of the clinical picture, diagnosis and treatment. Case report

Consilium Medicum, 2022
The article highlights the main issues of etiology, pathogenesis, clinical picture, diagnosis and treatment of patients with lymphangioleiomyomatosis. The clinical observation presents the features of the condition, the rate of progression, diagnostic ...
Galina L. Ignatova, Elena V. Blinova, Mariia S. Bel'sner   +2 more
doaj   +1 more source

Possible Novel Therapeutic Targets in Lymphangioleiomyomatosis Treatment

Frontiers in Medicine, 2020
Lymphangioleiomyomatosis (LAM) is a rare systemic neoplastic disease that exclusively happens in women. Studies focusing on LAM and tuberous sclerosis complex (TSC) have made great progress in understanding the pathogenesis and searching for treatment ...
Xixi Song, Hui Cai, Chengyu Yang, Xiaomin Xue, Jian Wang, Yuqing Mo, Mengchan Zhu, Guiping Zhu, Ling Ye, Meiling Jin   +9 more
doaj   +1 more source

Diagnostic performance of VEGF-D for lymphangioleiomyomatosis: a meta-analysis

Jornal Brasileiro de Pneumologia, 2022
Objective: VEGF-D is a potential biomarker for lymphangioleiomyomatosis (LAM); however, its diagnostic performance has yet to be systematically studied. Methods: We searched PubMed, EMBASE, Scopus, Web of Science, and Cochrane Library to identify primary
Min Li, Wenye Zhu, Ji Wang, Xiao-Dong Yang, Wei-Min Li, G. Wang   +5 more
semanticscholar   +1 more source