Results 21 to 30 of about 11,099 (227)

Airspace Enlargement with Fibrosis in a Young Heavy Smoker Mimicking Diffuse Cystic Lung Disease

Medicina, 2022
The widespread use of computed tomography (CT) has led to the increased recognition of cystic lung lesions. Multiple pulmonary cysts can be observed in heterogeneous disorders called diffuse cystic lung diseases (DCLDs), which include pulmonary ...
Kyungsoo Bae, Hyo Jung An, Kyung Nyeo Jeon   +2 more
doaj   +1 more source

Refractory chylous effusions in lymphangioleiomyomatosis patient post lung transplant

SAGE Open Medical Case Reports, 2020
Lymphangioleiomyomatosis is a rare systemic disorder of unknown etiology that affects young women almost exclusively. Chylous effusions are known to be associated with lymphangioleiomyomatosis and may be difficult to treat.
Samuel Jacob, Mojahid Ali, Magdy M El-Sayed Ahmed, Maxim Itkin, Tathagat Narula, Si Pham, David Erasmus   +6 more
doaj   +1 more source

Sporadic Lymphangioleiomyomatosis Disease: A Case Report [PDF]

Iranian Journal of Medical Sciences, 2023
Pulmonary Lymphangioleiomyomatosis (LAM) is a rare disease of the lung and lymphatic system that primarily affects women of childbearing age. LAM is a progressive disease with a terrible prognosis, which worsens over time and is extremely difficult to ...
Yousef Nikmanesh, Mansoureh Shokripour, Maral Mokhtari, Mahdi Khazayi, Ahmad Monabati, Ramin Rezayi, Mehrzad Bahtouee   +6 more
doaj   +1 more source

Desaturation-Distance Ratio During Submaximal and Maximal Exercise Tests and Its Association With Lung Function Parameters in Patients With Lymphangioleiomyomatosis

Frontiers in Medicine, 2021
Background: The desaturation–distance ratio (DDR), the ratio of the desaturation area to the distance walked, is a promising, reliable, and simple physiologic tool for functional evaluation in subjects with interstitial lung diseases ...
Douglas Silva Queiroz, Douglas Silva Queiroz, Cibele Cristine Berto Marques da Silva, Alexandre Franco Amaral, Martina Rodrigues Oliveira, Henrique Takachi Moriya, Carlos Roberto Ribeiro Carvalho, Bruno Guedes Baldi, Celso R. F. Carvalho   +8 more
doaj   +1 more source

Pulmonary lymphangioleiomyomatosis with parietal pleural involvement: A case report and discussion of pathogenesis using pulmonary lymphangitic carcinomatosis as a model

Human Pathology: Case Reports, 2019
We report a case of sporadic pulmonary lymphangioleiomyomatosis presenting with chylothorax and with parietal pleural involvement by the disease. The implications for the anatomic distribution of lesions in pulmonary lymphangioleiomyomatosis is discussed.
Shunei Asao, B.A., Charles M. Lombard, M.D., Pei Tsau, M.D.   +2 more
doaj   +1 more source

Differential diagnosis of chylothorax in therapeutic practice

Терапевтический архив, 2021
The article is devoted to the differential diagnosis of chylous pleural effusion. The spectrum of traumatic and non-traumatic causes of chylothorax is discussed in detail.
Marina A. Makarova, Gulsara E. Baimakanova, Stanislav A. Krasovsky   +2 more
doaj   +1 more source

A rare cause of recurrent spontaneous pneumothorax: Birt-hogg-dube syndrome [PDF]

, 2018
Birt-Hogg-Dube (BHD) syndrome is an unusual disorder characterized by the triad of cutaneous lesions, renal tumors and lung cysts. In cases with BHD syndrome, the frequency of recurrent pneumothorax is increased due to presence of multiple lung cysts. It
Demirci, M., Karaman, Engin, Ufuk, F., Yavaş, H.G.   +3 more
core   +1 more source

VATS therapy of chylothorax caused by leiomyomatosis complicated with tuberous sclerosis complex

Journal of Minimal Access Surgery, 2013
Lymphangioleiomyomatosis with tuberous sclerosis complex is a rare disease. One of the most frequent complications of lymphangioleiomyomatosis is pleural effusion (chylothorax) wich can be treated with the use of VATS.
Adrienn Csiszkó, György Herr, Sándor Sz. Kiss, Judit Hallay, Zoltán Gyöngyösi, Zsolt Szentkereszty   +5 more
doaj   +1 more source

Identification of a novel TSC2 c.3610G > A, p.G1204R mutation contribute to aberrant splicing in a patient with classical tuberous sclerosis complex: a case report [PDF]

, 2018
Background: Tuberous sclerosis complex (TSC) is an autosomal dominant disorder characterized by hamartomas in any organ systems. Mutations in the TSC1 or TSC2 gene lead to the dysfunction of hamartin or tuberin proteins, which cause tuberous sclerosis ...
Bottillo, I, Han, Y, Lang, Y, Liu, X, Shao, L., Wang, J, Wang, Q, Zhang, R   +7 more
core   +2 more sources

Possible Novel Therapeutic Targets in Lymphangioleiomyomatosis Treatment

Frontiers in Medicine, 2020
Lymphangioleiomyomatosis (LAM) is a rare systemic neoplastic disease that exclusively happens in women. Studies focusing on LAM and tuberous sclerosis complex (TSC) have made great progress in understanding the pathogenesis and searching for treatment ...
Xixi Song, Hui Cai, Chengyu Yang, Xiaomin Xue, Jian Wang, Yuqing Mo, Mengchan Zhu, Guiping Zhu, Ling Ye, Meiling Jin   +9 more
doaj   +1 more source