Results 51 to 60 of about 11,099 (227)

Management of everolimus-associated adverse events in patients with tuberous sclerosis complex: a practical guide [PDF]

, 2017
Tuberous sclerosis complex (TSC) is a genetic disorder characterised by highly variable comorbid dysfunction and subsequent morbidity. The mTOR inhibitor everolimus is indicated for the treatment of adult TSC patients with renal angiomyolipomas (AMLs ...
Davies, Mark, Kingswood, John C., Saxena, Anurag   +2 more
core   +3 more sources

Lymphangioleiomyomatosis biomarkers linked to lung metastatic potential and cell stemness [PDF]

, 2016
Lymphangioleiomyomatosis (LAM) is a rare lung-metastasizing neoplasm caused by the proliferation of smooth muscle-like cells that commonly carry loss-of-function mutations in either the tuberous sclerosis complex 1 or 2 (TSC1 or TSC2) genes.
Aguilar, Helena, Ancochea Bermúdez, Julio, Boni, Jacopo, Campos, Miriam, Casanova, Álvaro, Climent, Fina, Cordero, Alex, Esteller, Manel, Extremera, Ana I., Falo, Catalina, Fernández, Adela, García, Nadia, Gil, Miguel, González Suárez, Eva, Gumà i Garcia, Anna Maria, Gómez Baldó, Laia, Hernández-Losa, Javier, Herranz, Carmen, Laporta, Rosalía, Llatjós, Roger, Llorente, Alicia, López, José Ignacio, Mateo González, Francesca, Molina Molina, María, Morilla, Idoia, Ortega, Raúl, Pernas, Sònia, Petit, Anna, Pla Farnós, María Jesús, Pujana Genestar, M. Ángel, Román, Antonio, Ruiz de Garibay, Gorka, Sanchez-Mut, Jose Vicente, Serra-Musach, Jordi, Ussetti, Piedad, Valenzuela, Claudio, Varela Rodríguez, Mar, Vidal-Bel, August, Xaubet Mir, Antonio   +38 more
core   +1 more source

Comparison of Signal‐ and Volume‐Based Ventilation‐Weighted Assessment Using 3D FLORET UTE MRI in Patients With Various Pulmonary Disease

Magnetic Resonance in Medicine, EarlyView.
ABSTRACT Purpose 3D free‐breathing, proton, contrast‐agent‐free MR methods are increasingly used for pulmonary ventilation‐weighted measurements. The methods are split between: (1) signal‐based, which rely on lung parenchyma signal changes during respiration, and (2) volume‐based that utilize the Jacobian determinant of deformation fields from the ...
Filip Klimeš, Joseph W. Plummer, Andreas Voskrebenzev, Marcel Gutberlet, Marius M. Klein, Matthew M. Willmering, Alexander M. Matheson, Abdullah S. Bdaiwi, Frank Wacker, Jason C. Woods, Zackary I. Cleveland, Laura L. Walkup, Jens Vogel‐Claussen   +12 more
wiley   +1 more source

Complications of lymphangioleiomyomatosis in pregnancy: a case report and review of the literature

AJOG Global Reports
Lymphangioleiomyomatosis is a rare cystic lung disease primarily affecting premenopausal females and may be exacerbated by pregnancy. We conducted a literature review of lymphangioleiomyomatosis during pregnancy with a specific focus on related maternal ...
Eileen Wang-Koehler, MD, Adina R. Kern-Goldberger, MD, MPH, MSCE, Sindhu K. Srinivas, MD, MSCE   +2 more
doaj   +1 more source

A rare lung disease diagnosed by CT in a young pregnant woman

Clinical Case Reports, 2021
Lymphangioleiomyomatosis (LAM) is an unusual lung disease which can be diagnosed by its characteristic appearance on a high‐resolution CT, and may not always require a biopsy.
Sunil Persad, Nadiya Dowlath, Michael Prasad, Vanessa Harry   +3 more
doaj   +1 more source

Epitheloid Variant of Angiomyolipoma in a Patient with Tuberous Sclerosis. [PDF]

, 2013
Epitheloid angiomyolipoma of kidney is a type of Perivascular endothelial cell derived tumor with an aggressive behaviour with specific pathological, immunohistochemistrical and genetic characteristics.
Amirtham, U, Challa, VR, Goud, BYG, Rangappa, P, Swamyvelu, K   +4 more
core   +1 more source

Improvement of lung preservation - From experiment to clinical practice [PDF]

, 2002
Background. Reperfusion injury represents a severe early complication following lung transplantation. Among the pathogenetic factors, the high potassium content of Euro-Collins(R) solution is discussed.
Bittmann, I., Fürst, H., Hatz, Rudolf A., Kellner, B., Müller, Ch., Reichart, B., Schelling, G., Schildberg, Friedrich Wilhelm   +7 more
core   +1 more source

Coil Sketching for Fast and Efficient 4D Lung MRI Reconstruction

Magnetic Resonance in Medicine, Volume 95, Issue 4, Page 2241-2253, April 2026.
ABSTRACT Purpose To develop and evaluate a memory‐efficient and accelerated reconstruction framework for respiratory‐resolved 4D lung MRI using coil sketching and Toeplitz approximation, enabling high‐quality motion‐compensated low‐rank (MoCo‐LR) reconstructions on clinically accessible GPU hardware.
Joseph W. Plummer, Pierre Daudé, Anastasia Tsakirellis, Jordan Taylor, Joel Moss, Rajiv Ramasawmy, Ahsan Javed, Adrienne E. Campbell‐Washburn   +7 more
wiley   +1 more source

Recurrent pneumothoraces with diffuse small ground‐glass and solid nodules

Respirology Case Reports, 2021
Multifocal micronodular pneumocyte hyperplasia (MMPH) is the lesser known pulmonary manifestation of tuberous sclerosis. It manifests radiologically as diffuse small ground‐glass and solid nodules.
Li Yan Sandra Hui, Xin Min Cheng, Ing Xiang Soo, Su Ying Low   +3 more
doaj   +1 more source

Lymphangioleiomyomatosis (LAM) [PDF]

Breathe, 2017
LAM is characterised by lung cysts (air-filled sacs which gradually destroy the lung), changes to the lymphatic system and tumours in the kidneys.
openaire   +2 more sources