Results 11 to 20 of about 59,746 (203)

Acrodermatitis Dysmetabolica as a Cutaneous Manifestation of Isoleucine Deficiency in Maple Syrup Urine Disease: A Systematic Review of Reported Cases. [PDF]

Health Sci Rep
ABSTRACT Background and Aim Maple Syrup Urine Disease (MSUD) is a metabolic disorder affecting branched‐chain amino acid metabolism. While neurological symptoms are well‐characterized, cutaneous manifestations such as acrodermatitis dysmetabolica (AD) caused by isoleucine deficiency remain underrecognized.
Abtahi-Naeini B, Heidari-Beni M, Rostampour N, Davoudi N, Seyedyousefi S.   +4 more
europepmc   +2 more sources

Maple syrup urine disease: mechanisms and management

The Application of Clinical Genetics, 2017
Patrick R Blackburn,1,2,* Jennifer M Gass,1,* Filippo Pinto e Vairo,3,4,* Kristen M Farnham,5 Herjot K Atwal,6 Sarah Macklin,5 Eric W Klee,3,4,7,8 Paldeep S Atwal1,5 1Center for Individualized Medicine, 2Department of Health Sciences Research, Mayo ...
Blackburn PR, Gass JM, Vairo FP, Farnham KM, Atwal HK, Macklin S, Klee EW, Atwal PS   +7 more
doaj   +1 more source

Sap to story : telling the tale of bigleaf maple sugaring through environmental interpretation

Maple sugaring, the process of reducing maple sap into syrup, has traditionally centered around sugar maple (Acer saccharum) in the northeastern United States.
Cameron, Sarah
core   +5 more sources

Mothers' Knowledge and Practices Regarding Care of their children Suffering from Maple Syrup Urine Disease. [PDF]

Helwan International Journal for Nursing Research and Practice
Maple syrup urine disease (MSUD) is a rare inherited autosomal recessive neurometabolic disorder, is brought on by diminished activity of the Branched-chain α-ketoacid dehydrogenase complex (BCKDC), which catalysis the irreversible catabolism of branched-
Aisha Ahmed
doaj   +1 more source

Maple Syrup Urine Disease

Radiology
Hassan SA, Gupta V.
europepmc   +3 more sources

Perceptions of U.S. and Canadian maple syrup producers toward climate change, its impacts, and potential adaptation measures.

PLoS ONE, 2019
The production of maple syrup is an important cultural and economic activity directly related to the climate of northeastern North America. As a result, there are signs that climate change could have negative impacts on maple syrup production in the next
Simon Legault, Daniel Houle, Antoine Plouffe, Aitor Ameztegui, Diane Kuehn, Lisa Chase, Anne Blondlot, Timothy D Perkins   +7 more
doaj   +1 more source

Bioethanol Production as an Alternative End for Maple Syrups with Flavor Defects

Fermentation, 2022
The purpose of this paper is to demonstrate the validity of an alternative route to valorize declassified maple syrups affected by flavor defects such as ropy maple syrup (RMS) and buddy maple syrup (BMS) as feedstocks for ethanol production.
Julia Maria de Medeiros Dantas, André Álvares Monge Neto, Thierry Ghislain, Jean-Michel Lavoie   +3 more
doaj   +1 more source

Pattern Recognition Approach for the Screening of Potential Adulteration of Traditional and Bourbon Barrel-Aged Maple Syrups by Spectral Fingerprinting and Classical Methods

Foods, 2022
This study aims to generate predictive models based on mid-infrared and Raman spectral fingerprints to characterize unique compositional traits of traditional and bourbon barrel (BBL)-aged maple syrups, allowing for fast product authentication and ...
Kuanrong Zhu, Didem P. Aykas, Luis E. Rodriguez-Saona   +2 more
doaj   +1 more source

In Memory of the Maple Syrup Man [PDF]

The Oncologist, 2019
This narrative, written in memory of a cancer patient, considers the emotional aspects of bringing your work home with you as an oncologist.
openaire   +2 more sources

Assessing the Growth Potential and Economic Impact of the U.S. Maple Syrup Industry

Journal of Agriculture, Food Systems, and Community Development, 2016
This paper addresses the growth potential of the U.S. maple syrup industry. It outlines the number of potentially tappable maple trees and the economic impact of utilizing more of these trees for syrup production. U.S. producers currently tap 0.4% of all
Michael L. Farrell, Brian F. Chabot
doaj   +1 more source