Results 21 to 30 of about 228 (152)

Mastocitosis. Presentación de un caso

open access: yesRevista de Ciencias Médicas de Pinar del Río, 2013
La mastocitosis o mastocitoma es una genodermatosis poco frecuente, de etiología desconocida, incluida en el grupo de "enfermedades raras", que aparece en la infancia generalmente.
Carlos Alberto Blanco Córdova
doaj   +1 more source

Histiocitosis cefálica benigna simulando una mastocitosis

open access: yesActas Dermo-Sifiliográficas, 2022
E. Silva Díaz   +3 more
doaj   +2 more sources

Mastocitosis sistémica con afectación de piel versus mastocitosis indolente [PDF]

open access: yesAnales de Medicina Interna, 2001
El objetivo de trabajo es la presentación de los datos clínicos, analíticos, radiológicos, terapéuticos y de evolución de un caso de matocitosis sistémica (MS) con afectación de piel. Revisando la literatura ya que la mastocitosis sigue siendo una enfermedad de difídicl diagnóstico, sobre todo en los casos que no existen alteraciones cutáneas.
Tiberio,G.   +5 more
openaire   +4 more sources

A case of high‐risk AML in a patient with advanced systemic mastocytosis

open access: yesClinical Case Reports, Volume 11, Issue 7, July 2023., 2023
Abstract Aggressive SM + AML has limited therapeutic options. Even a strong combination of decitabine–venetoclax–midostaurin has a transient effect on AML and a mitigated effect on SM. Larger series are required to identify the best therapeutic strategy.
Manlio Fazio   +15 more
wiley   +1 more source

KITD816V mutation in blood for the diagnostic screening of systemic mastocytosis and mast cell activation syndromes

open access: yesAllergy, Volume 78, Issue 5, Page 1347-1359, May 2023., 2023
This study evaluates the utility of KITD816V mutational status in blood (vs. bone marrow) for the diagnostic screening of SM and MCAS patients, having a high specificity but a limited sensitivity in patients presenting with clonal MCAS without skin lesions.
Paula Navarro‐Navarro   +11 more
wiley   +1 more source

Artificial intelligence processing electronic health records to identify commonalities and comorbidities cluster at Immuno Center Humanitas

open access: yesClinical and Translational Allergy, Volume 12, Issue 6, June 2022., 2022
Abstract Background Comorbidities are common in chronic inflammatory conditions, requiring multidisciplinary treatment approach. Understanding the link between a single disease and its comorbidities is important for appropriate treatment and management.
Pierandrea Morandini   +10 more
wiley   +1 more source

CUTANEOUS MASTOCYTOSIS IN THE ADULT: WHAT LIES BENEATH

open access: yesGalicia Clínica, 2020
Mastocytosis is a disorder characterized by clonal mast cell proliferation and accumulation within various organs, most commonly, the skin. Adult-onset mastocytosis is highly suggestive of a systemic involvement and the cases limited to the skin are ...
Liliana Torres   +3 more
doaj   +1 more source

Urticaria pigmentosa de presentación atípica en la infancia: Reporte de un caso clínico

open access: yesARS Medica, 2016
La Urticaria Pigmentosa es el tipo más frecuente de mastocitosis cutáneas de inicio en la edad pediátrica, representando el 75% de los casos. Se presenta con máculas y/o pápulas de color amarillo a café-rojizo, usualmente con signo de Darier positivo y ...
Catherina Moll-Manzur   +2 more
doaj   +1 more source

Mast cell activation syndrome. About a clinical case

open access: yesRevista Alergia México, 2019
Background: Monoclonal mast cell activation syndrome is included in mast cell activation disorders in which, after a diagnostic process, it is not possible to meet the required criteria for a diagnosis of systemic mastocytosis.
Ricardo Cardona   +4 more
doaj   +1 more source

Mastocitoma solitario. Comunicación de un caso

open access: yesRevista Alergia México, 2023
Antecedentes: El mastocitoma solitario es una variante de mastocitosis cutánea de buen pronóstico, congénita, que aparece durante las primeras semanas de vida.
Camila Delgadillo Jordán
doaj   +1 more source

Home - About - Disclaimer - Privacy