Evidence of Iron Accumulation in Cerebral Adrenoleukodystrophy: A Potential Novel Disease Mechanism
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT In this first application of Quantitative Susceptibility Mapping Source Separation to cerebral adrenoleukodystrophy, we uncovered alterations in iron and myelin within lesions and normal appearing white matter. As validation, we demonstrate abnormal iron accumulation in those same compartments within primary brain tissue.
Christina L. Nemeth +8 more
wiley +1 more source
Bee Venom Melittin Disintegrates the Respiration of Mitochondria in Healthy Cells and Lymphoblasts, and Induces the Formation of Non-Bilayer Structures in Model Inner Mitochondrial Membranes. [PDF]
Int J Mol Sci, 2021 Gasanoff E +4 more
europepmc +1 more source
Mitochondrial Membrane-Associated Protein Mba1 Confers Antifungal Resistance by Affecting the Production of Reactive Oxygen Species in Aspergillus fumigatus [PDF]
, 2023 Guoxing Zhu +3 more
openalex +1 more source
SPG4 and Dementia: Expanding the Clinical Spectrum
Annals of Clinical and Translational Neurology, EarlyView.ABSTRACT Objective Hereditary spastic paraplegia (HSP) is a group of disorders characterized by progressive spasticity and lower limb weakness, with mutations in SPG4/SPAST being the most common cause. Detailed studies and clinical and molecular comparisons across different populations are missing.
Emanuele Panza +19 more
wiley +1 more source
Interface mobility between monomers in dimeric bovine ATP synthase participates in the ultrastructure of inner mitochondrial membranes. [PDF]
Proc Natl Acad Sci U S A, 2021 Spikes TE, Montgomery MG, Walker JE.
europepmc +1 more source
Conserved function, divergent evolution: mitochondrial outer membrane insertases across eukaryotes [PDF]
Anna Roza Dimogkioka, Doron Rapaport
openalex +1 more source
The mitochondrial membrane system
Progress in Biophysics and Molecular Biology, 1972 J M, Palmer, D O, Hall
openaire +2 more sources