Results 11 to 20 of about 1,153,947 (162)

Seronegative Morvan Syndrome Presenting With Agrypnia Excitata and Peripheral Nerve Hyperexcitability: A Phenotype‐Supported Diagnostic and Therapeutic Approach in a Resource‐Limited Setting [PDF]

Clinical Case Reports
We report a 63‐year‐old Palestinian man with seronegative Morvan syndrome presenting with the complete clinical triad: continuous neuromyotonia with visible myokymia, severe insomnia consistent with agrypnia excitata phenotype (2–3 h/night; Insomnia ...
Hatem Mousa Taha, Khaled Hatem Taha
doaj   +3 more sources

Morvan syndrome: a rare cause of syndrome of inappropriate antidiuretic hormone secretion. [PDF]

Clujul Med, 2017
The syndrome of inappropriate antidiuretic hormone secretion (SIADH) accounts for an important part of hyponatremia cases. The causes of SIADH can be detected almost always. As a rare disorder, Morvan Syndrome can be defined by the sum of peripheral nerve hyperexcitability, autonomic instability and neuropsychiatric features.
Demirbas S, Aykan MB, Zengin H, Mazman S, Saglam K.   +4 more
europepmc   +5 more sources

Morvan Syndrome Secondary to Thymic Carcinoma in a Patient with Systemic Lupus Erythematosus [PDF]

Case Reports in Neurological Medicine, 2016
Morvan syndrome (MoS) is a rare paraneoplastic autoimmune disorder characterized by peripheral nerve hyperexcitability, autonomic dysfunction, and sleep disorders. Systemic lupus erythmatosus (SLE) cooccurs in 6–10% of patients with thymoma. It may occur
Gabrielle Macaron, Elie El Rassy, Salam Koussa   +2 more
doaj   +3 more sources

CASPR2-Related Morvan Syndrome: Autonomic, Polysomnographic, and Neuropsychological Observations. [PDF]

Neurol Clin Pract, 2021
Morvan syndrome is characterized by central, autonomic, and peripheral hyperexcitability due to contactin-associated protein 2 (CASPR2) antibody. Our objective was to study the clinical spectrum, electrophysiologic, autonomic, polysomnographic, and neuropsychological profile in patients with CASPR2-related Morvan syndrome.Serum and CSF samples that ...
Swayang PS, Nalini A, Preethish-Kumar V, Udupa K, Yadav R, Vengalil S, Reshma SS, Polavarapu K, Nashi S, Sathyaprabha TN, Treesa Thomas P, Maya B, Jamuna R, Mahadevan A, Netravathi M.   +14 more
europepmc   +3 more sources

Insomnia and Dysautonomia with Contactin-Associated Protein 2 and Leucine-Rich Glioma Inactivated Protein 1 Antibodies: A “Forme Fruste” of Morvan Syndrome? [PDF]

Case Reports in Neurology, 2019
Morvan syndrome (MoS) is typically characterized by neuromyotonia, sleep dysfunction, dysautonomia, and cognitive dysfunction. However, MoS patients with mild peripheral nerve hyperexcitability (PNH) or encephalopathy features have been described.
Ezgi Bakırcıoğlu-Duman, Zeynep Acar, Gülçin Benbir, Hande Yüceer, Hürtan Acar, Birgül Baştan, Belgin Petek-Balcı, Derya Karadeniz, Özlem Çokar, Erdem Tüzün   +9 more
doaj   +2 more sources

A Case Report of an Atypical Presentation of Morvan Syndrome. [PDF]

Cureus
Morvan syndrome, also known as Morvan's fibrillary chorea, is a rare paraneoplastic neurological syndrome presenting with central nervous system (CNS) symptoms, peripheral nerve hyperexcitability, and autonomic nervous system (ANS) manifestations. The etiology and severity of the disease are not well understood.
Haroutunian SG, Hoseen R, Farmand D, Camilon M, Hashemi S.   +4 more
europepmc   +3 more sources

CASPR2 antibody-related neurological syndromes in children: three cases report and literature review [PDF]

BMC Pediatrics
Background Contactin-associated protein-like 2 (CASPR2) antibody-related neurological syndrome is well defined in adults, while data in children is rare.
Long-Ying Peng, Shu-Jing Pan, Ren-Ke Li, Juan Li, Jing Chen, Xiao-Hua Yu, Chang-Jian Yang, Xiao-Mei Shu, Mao-Qiang Tian   +8 more
doaj   +2 more sources

Successful therapeutic plasma exchange in a patient with Morvan syndrome. [PDF]

Asian J Transfus Sci, 2019
Morvan syndrome is a rare autoimmune disorder, characterized by hyperexcitability of both central and peripheral nervous systems, accompanied by autonomic dysfunction and hallucinations.[1] Therapeutic plasma exchange (TPE) has been found to be an effective mode of treatment for this disease, but there is limited literature supporting the same.[2] A 26-
Dubey R, Mallhi RS, Asthana B, Kushwaha N, Yadav A.   +4 more
europepmc   +3 more sources

Dual diagnosis at the neuro-immune interface: a case report of neuronal intranuclear inclusion disease with acute anti-CASPR2 encephalitis [PDF]

Frontiers in Immunology
Neuronal intranuclear inclusion disease (NIID) is a rare autosomal-dominant, progressive neurodegenerative condition characterized by complex and variable clinical manifestations that can affect multiple neurological domains.
Wan Zhu, Tiansi Liu, Tiansi Liu, Xinran Yu, Min Peng, Min Peng, Jinghan Hu, Jinghan Hu   +7 more
doaj   +2 more sources

Extrapleural pneumonectomy for recurrent thymoma diagnosed after return of paraneoplastic Morvan syndrome. [PDF]

J Surg Case Rep, 2022
A 50-year-old male with history of HIV, syphilis, paraneoplastic Morvan syndrome secondary to thymoma resected in 2013 presented recently with tachycardia, tremors, diarrhea, hyperhidrosis and bilateral lower extremity pain leading to the discovery of ...
Banks KC, Hsu DS, Velotta JB.
europepmc   +2 more sources