Results 21 to 30 of about 7,288 (241)

A conceptual framework to develop a patient-reported experience questionnaire on the cystic fibrosis journey in France: the ExPaParM collaborative study

Orphanet Journal of Rare Diseases, 2023
Background The objective of the study was to elaborate a conceptual framework related to the domains of patient experience along the cystic fibrosis (CF) journey from the patients and parents of children with CF to inform the design of a patient-reported
D. Pougheon Bertrand, A. Fanchini, P. Lombrail, G. Rault, A. Chansard, N. Le Breton, C. Frenod, F. Milon, C. Heymes Royer, D. Segretain, M. Silber, S. Therouanne, J. Haesebaert, C. Llerena, P. Michel, Q. Reynaud   +15 more
doaj   +1 more source

Modulation of the immune response by the Pseudomonas aeruginosa type-III secretion system

Frontiers in Cellular and Infection Microbiology, 2022
Pseudomonas aeruginosa is an opportunistic pathogen that can cause critical cellular damage and subvert the immune response to promote its survival. Among the numerous virulence factors of P.
Albane Jouault, Albane Jouault, Alessandra Mattos Saliba, Lhousseine Touqui, Lhousseine Touqui   +4 more
doaj   +1 more source

Beneficial short-term effect of autogenic drainage on peripheral resistance in childhood cystic fibrosis disease

BMC Pulmonary Medicine, 2022
Background Airway clearance techniques are supposed to be a necessary adjunct for the enhancement of impaired peripheral clearance in cystic fibrosis (CF).
Plamen Bokov, Michèle Gerardin, Géraldine Brialix, Emmanuelle Da Costa Noble, Romain Juif, Antonia Vital Foucher, Laurence Le Clainche, Véronique Houdouin, Benjamin Mauroy, Christophe Delclaux   +9 more
doaj   +1 more source

Registre Français de la Mucoviscidose. Bilan des données 2017 [PDF]

, 2019
Objectifs L’association Vaincre la Mucoviscidose a mis en place en 1992 un Observatoire National de la Mucoviscidose (ONM) ayant les objectifs suivants : – améliorer la connaissance des caractéristiques médicales et sociales, – mieux appréhender le coût
Lemonnier, Lydie, Dehillotte, Clémence, Bellis, Gil   +2 more
core   +4 more sources

Corrigendum: Long term NIV in an infant with Hallermann-Streiff syndrome: a case report and overview of respiratory morbidity [PDF]

Frontiers in Pediatrics
S. Guerin, S. Blanchon, Q. de Halleux, V. Bayon, T. Ferry   +4 more
doaj   +2 more sources

Estudo da freqüência de diabetes mellitus e intolerância à glicose em pacientes com fibrose cística Study of the frequency of diabetes mellitus and glucose intolerance in patients with cystic fibrosis

Jornal de Pediatria, 2001
OBJETIVO: avaliar a freqüência de diabetes mellitus (DM) e de intolerância à glicose nos pacientes com fibrose cística seguidos no Serviço de Gastropediatria do HC-FMRP-USP.
Flávia A.A. de Castro, Maria I.M. Fernandes, Renan M. Montenegro Júnior, Milton C. Foss   +3 more
doaj   +1 more source

Correction to: In vitro prediction of stop-codon suppression by intravenous gentamicin in patients with cystic fibrosis: a pilot study

BMC Medicine, 2018
The original article [1] contains errors in Table 1 affecting some of the presented oligonucleotide sequences and readthrough values in Table 1.
I. Sermet-Gaudelus, M. Renouil, A. Fajac, L. Bidou, B. Parbaille, S. Pierrot, N. Davy, E. Bismuth, P. Reinert, G. Lenoir, J. F. Lesure, J. P. Rousset, A. Edelman   +12 more
doaj   +1 more source

In Vitro Activity of 22 Antibiotics against Achromobacter Isolates from People with Cystic Fibrosis. Are There New Therapeutic Options?

Microorganisms, 2021
Bacteria belonging to the genus Achromobacter are increasingly isolated from respiratory samples of people with cystic fibrosis (PWCF). The management of this multidrug-resistant genus is challenging and characterised by a lack of international ...
Clémence Beauruelle, Claudie Lamoureux, Arsid Mashi, Sophie Ramel, Jean Le Bihan, Thomas Ropars, Anne Dirou, Anandadev Banerjee, Didier Tandé, Hervé Le Bars, Geneviève Héry-Arnaud   +10 more
doaj   +1 more source

Dix ans de dépistage néonatal de la mucoviscidose en Suisse. [PDF]

, 2023
Im Jahr 2011 wurde das Neugeborenen-Screening für zystische Fibrose in der Schweiz eingeführt. Nach zehn Jahren ist es Zeit für einen Blick zurück auf das, was erreicht wurde, und für einen Ausblick auf weitere Optimierungen des Programms in der Zukunft ...
Rueegg, Corina S., Berger, Daria, Kuehni, Claudia E., Baumgartner, Matthias, Pedersen, Eva S. L., Sluka, Susanna, Sanz, Javier, Barben, Jürg   +7 more
core   +1 more source

AVALIAÇÃO POSTURAL COMPUTADORIZADA EM PACIENTES PORTADORES DA FIBROSE CÍSTICA EM UM CENTRO DE REFERÊNCIA EM SALVADOR-BA

Revista Pesquisa em Fisioterapia, 2015
Introdução: A Fibrose Cística (FC) é uma anormalidade genética de caráter sistêmico gerando ao sistema respiratório uma hipersecretividade e obstrução brônquica crônica.
Francisco Oliveira, Cristiane Dias, Anna Lúcia Dinniz, Selena Márcia Dubois Mendes, Abrahão Fontes Baptista, Kátia Nunes Sá   +5 more
doaj   +1 more source