Results 51 to 60 of about 5,453 (193)
Effects of Pilates mat exercises on muscle strength and on pulmonary function in patients with cystic fibrosis [PDF]
, 2014 Objective: To analyze the effects of Pilates mat exercises in patients with cystic fibrosis (CF). Methods: This was a clinical trial involving 19 CF patients recruited from either the CF Outpatient Clinic of the State University at Campinas Hospital de ...
Almeida, Marina Buarque +5 more
core +4 more sources
A intersubjetividade no contexto da família de pessoas com fibrose cística
Revista Brasileira de Enfermagem, 2012 Trata-se de uma investigação qualitativa, com aproximação fenomenológica, que objetivou desvelar os processos intersubjetivos no contexto da família de pessoas com Fibrose Cística (FC).
Geisa Santos Luz +5 more
doaj +1 more source
Skin Health and Disease, 2023 Background A high proportion of patients with Cystic Fibrosis (CF) also present the rare skin disease aquagenic palmoplantar keratoderma. A possible link between this condition and absence of a functional CF Transmembrane conductance Regulator protein in
Matthieu Cornet +9 more
doaj +1 more source
Implementation of Model-Based Dose Adjustment of Tobramycin in Adult Patients with Cystic Fibrosis
Pharmaceutics, 2022 Therapeutic drug monitoring (TDM) of tobramycin is widely performed in patients with cystic fibrosis (CF), but little is known about the value of model-informed precision dosing (MIPD) in this setting.
Jérémy Reverchon +12 more
doaj +1 more source
De l'animal expérimental au modèle en recherche biomédicale. [PDF]
, 2008 Cet article est destiné à la Revue PhilosophiqueSince the beginning of experimentation in biology, animals have been used to study processes that cannot be approached on human beings.
Gachelin, Gabriel
core +3 more sources
Phenotype‐Genotype Correlations in ABCA3 Patients—The RespiRare Cohort
Pediatric Pulmonology, Volume 60, Issue 10, October 2025.ABSTRACT Background ATP‐binding cassette transporter A3 (ABCA3) deficiency is one of the most severe causes of childhood interstitial lung diseases (chILD). This study aims to report the RespiRare ABCA3 cohort and to establish phenotype‐genotype correlations. Methods Phenotypic and genotypic data of patients under 18 years were retrospectively included
Manon Fleury +34 more
wiley +1 more source
Prática fisioterapêutica no tratamento da fibrose cística
ABCS Health Sciences, 2014 A fibrose cística (FC), denominada também de mucoviscidose, é uma doença genética do tipo autossômica recessiva que acomete principalmente crianças e indivíduos de raça branca.
Carolina Lazzarim de Conto +6 more
doaj +1 more source
Linguistic validation of cystic fibrosis quality of life questionnaires [PDF]
, 2006 OBJECTIVE: The purpose of this study was to validate the Portuguese translations of four cystic fibrosis quality of life questionnaires (CFQ). The first three were developed for patients with cystic fibrosis aged from 6 to 11 years, from 12 to 13 years ...
Cunha, Maristela T. +4 more
core +2 more sources
New insights into interactions between the nucleotide-binding domain of CFTR and keratin 8 [PDF]
, 2016 The intermediate filament protein keratin 8 (K8) interacts with the nucleotide-binding domain 1 (NBD1) of the cystic fibrosis transmembrane regulator (CFTR) with phenylalanine 508 deletion (ΔF508), and this interaction hampers the biogenesis of ...
Bonna, Arkadiusz +11 more
core +2 more sources