Results 61 to 70 of about 7,288 (241)

Assessment of the efficacy of an antimicrobial peptide in the context of cystic fibrosis airways

Current Research in Microbial Sciences
Antimicrobial peptides (AMPs) offer a promising alternative to control airway infections with multi-resistant bacteria, such as methicillin-resistant Staphylococcus aureus (MRSA), which commonly infects patients with cystic fibrosis (CF).
Albane Jouault, Inès Jeguirim, Inès Ben Hadj Kaddour, Lhousseine Touqui   +3 more
doaj   +1 more source

Prática fisioterapêutica no tratamento da fibrose cística

ABCS Health Sciences, 2014
A fibrose cística (FC), denominada também de mucoviscidose, é uma doença genética do tipo autossômica recessiva que acomete principalmente crianças e indivíduos de raça branca.
Carolina Lazzarim de Conto, Cintia Teixeira Vieira, Kelen Nunes Fernandes, Laís Machado Jorge, Gabriela da Silva Cândido, Rafael Inácio Barbosa, Rafael Cypriano Dutra   +6 more
doaj   +1 more source

A Importância das Associações de Fibrose Cística na Vida dos Pacientes e Familiares

Clinical and Biomedical Research, 2011
Na organização da sociedade moderna as associações filantrópicas tornaram-se importantes no cenário mundial.No Brasil após a fundação da ABRAM várias associações regionais se estruturaram para defender os pacientes com Fibrose Cística.No RGS, duas ...
Cleci Furian Müller, Elizabete Backes
doaj  

Proteomic profiling of sweat in patients with cystic fibrosis provides new insights into epidermal homoeostasis

Skin Health and Disease, 2023
Background A high proportion of patients with Cystic Fibrosis (CF) also present the rare skin disease aquagenic palmoplantar keratoderma. A possible link between this condition and absence of a functional CF Transmembrane conductance Regulator protein in
Matthieu Cornet, Thao Nguyen‐Khoa, Mairead Kelly‐Aubert, Vincent Jung, Frédérique Chedevergne, Muriel Le Bourgeois, Laura Aoust, Kévin Roger, Chiara Ida Guerrera, Isabelle Sermet‐Gaudelus   +9 more
doaj   +1 more source

Le Vardénafil rétablit le déséquilibre pro/anti-inflammatoire des macrophages dans la mucoviscidose [PDF]

, 2013
Introduction L’inflammation pulmonaire est l’une des caractéristiques clefs de la pathologie pulmonaire de la mucoviscidose. Nous avons préalablement démontré que, même en absence de toute stimulation, les macrophages alvéolaires et péritonéaux sont plus
Noël, Sabrina, 14ème colloque des jeunes chercheurs de la Mucoviscidose, Dhooghe, Barbara, Castanho Vaz, Pedro, Leal, Teresinha   +4 more
core  

One year of ETI reduces lung bacterial colonisation in adults with cystic fibrosis

Scientific Reports
The triple combination elexacaftor-tezacaftor-ivacaftor (ETI) has provided unprecedented clinical benefits for people with cystic fibrosis (pwCF) and drastically transformed the outcome of this disease.
Lucile Mianowski, Anne Doléans-Jordheim, Laurent Barraud, Muriel Rabilloud, Mael Richard, Raphaele Nove Josserand, Isabelle Durieu, Quitterie Reynaud   +7 more
doaj   +1 more source

Phenotype‐Genotype Correlations in ABCA3 Patients—The RespiRare Cohort

Pediatric Pulmonology, Volume 60, Issue 10, October 2025.
ABSTRACT Background ATP‐binding cassette transporter A3 (ABCA3) deficiency is one of the most severe causes of childhood interstitial lung diseases (chILD). This study aims to report the RespiRare ABCA3 cohort and to establish phenotype‐genotype correlations. Methods Phenotypic and genotypic data of patients under 18 years were retrospectively included
Manon Fleury, Céline Delestrain, Alice Hadchouel, Julie Mazenq, Myriam Benhamida, Anne‐Sophie Bernard, Raphaël Borie, Jacques Brouard, Harriet Corvol, Pierrick Cros, Christophe Delacourt, Tifenn Desroziers, Jean‐Christophe Dubus, Carole Egron, Ralph Epaud, Michael Fayon, Aude Forgeron, Lisa Giovannini‐Chami, Christophe Marguet, Alexandra Masson‐Rouchaud, Hortense Petat, Marie‐Catherine Renoux, Léa Roditis, Caroline Thumerelle, Clémentine Vigier, Aurore Coulomb L'Herminé, Hubert Ducou le Pointe, Pascale Fanen, Camille Fletcher, Chiara Sileo, Laureline Berteloot, Camille Louvrier, Alix de Becdelièvre, Marie Legendre, Nadia Nathan   +34 more
wiley   +1 more source

Mucoviscidose : dans la ligne des miR [PDF]

, 2018
La mucoviscidose est la plus fréquente des maladies génétiques dans les populations d’origine caucasienne, caractérisée par des mutations du gène codant le canal chlorure CFTR.
Olivier Tabary, Sonneville, Florence, Bardin, Pauline, Tabary, Olivier, Florence Sonneville, Pauline Bardin   +5 more
core   +1 more source

Expression and Roles of Antimicrobial Peptides in Innate Defense of Airway Mucosa: Potential Implication in Cystic Fibrosis

Frontiers in Immunology, 2020
The treatment of respiratory infections is associated with the dissemination of antibiotic resistance in the community and clinical settings. Development of new antibiotics is notoriously costly and slow; therefore, alternative strategies are needed ...
Regina Geitani, Carole Ayoub Moubareck, Carole Ayoub Moubareck, Zhengzhong Xu, Zhengzhong Xu, Zhengzhong Xu, Dolla Karam Sarkis, Lhousseine Touqui, Lhousseine Touqui   +8 more
doaj   +1 more source

Muqueuse naso-sinusienne et mucoviscidose

Bulletin de l'Académie Nationale de Médecine, 2019
Resume L’epithelium nasal assure le role de filtre des voies aeriennes inferieures grâce au drainage mucociliaire dont l’efficacite depend des transports ioniques trans-epitheliaux qui regulent l’hydratation du liquide de surface recouvrant les cellules ...
V. Prulière-Escabasse
semanticscholar   +1 more source