Scleromyxedema: clinical diagnosis and autopsy findings [PDF]
Scleromyxedema is a rare chronic cutaneous mucinosis of unknown etiology. It is characterized by papular eruption and scleroderma with microscopic evidence of mucin deposition, fibroblast proliferation, and fibrosis.
Ana Carolina Bulhões Sala +5 more
doaj +4 more sources
Clinical Determinants of Urinary Podocyte Biomarkers and Their Feasibility in Paraprotein-Related Kidney Disease [PDF]
Background/Objectives: Kidney injury is a frequent complication of multiple myeloma (MM) and monoclonal gammopathies. Podocyte stress markers, such as urinary nephrin and podocin, have been studied in other renal diseases but their utility in paraprotein-
Oliver Helk +6 more
doaj +2 more sources
Xantoma plano difuso normolipêmico idiopático com hiperesplenismo Diffuse plane idiopathic normolipemic xanthoma with hiperesplenism [PDF]
O xantoma plano difuso normolipêmico é doença rara, do grupo das histiocitoses, caracterizada pelo aparecimento de placas amareladas ou amarelo-alaranjadas, distribuídas simetricamente na pele e geralmente acompanhadas por xantelasma.
Danielle Machado da Silva +4 more
doaj +2 more sources
Diffuse plane xanthomatosis associated with monoclonal gammopathy Xantomatose plana difusa associada a gamopatia monoclonal [PDF]
Diffuse plane normolipemic xanthomatosis (DPNX) is a rare, non-inherited disease that is often associated with systemic diseases, mainly malignant hematological (especially multiple myeloma) or lymph proliferative disorders.
Aristóteles Rosmaninho +4 more
doaj +2 more sources
O xantogranuloma necrobiótico é doença crônica granulomatosa e xantomatosa, caracterizada por pápulas e placas infiltradas, eritematosas e amareladas, preferencialmente localizadas na região periorbital.
Danielle Mazziero Macedo +5 more
doaj +3 more sources
Impact of single versus multiple infection on serum protein fractions in cats. [PDF]
Serum protein electrophoresis (SPE) is a widely used diagnostic tool for identifying acute and chronic inflammation, as well as immunodeficiencies. However, the impact of co-infections on SPE patterns in cats remains poorly understood.
Marteles D +11 more
europepmc +3 more sources
Systemic amyloidosis: an aggressive evolution in a patient with relapsing polychondritis and monoclonal gammopathy of undetermined significance (MGUS) undergoing peritoneal dialysis [PDF]
Herein, we report the case of primary amyloidosis with multi-organ involvement in a female patient in her 50s. The patient had a history of relapsing polychondritis, chronic kidney disease, and monoclonal gammopathy of undetermined significance (MGUS ...
Thiago Cavalcanti Matos +3 more
doaj +2 more sources
Caracterización del mieloma múltiple y de su componente monoclonal durante 14 años en Las Tunas [PDF]
El mieloma múltiple es una neoplasia de células plasmáticas que representa el 10% de las enfermedades hematológicas malignas. La mayoría de los pacientes presentan síntomas, signos y trastornos de laboratorio sugestivos de enfermedad activa, incluyendo ...
Olga Lina Pupo Rodríguez +3 more
doaj +2 more sources
Dysproteinemia-Associated Kidney Disease: A Single-Center Observational Study [PDF]
Introduction: Dysproteinemia is associated with kidney damage and treatment of underlying conditions is crucial to minimize kidney damage. The aim of this study was to describe and analyze the characteristics and outcome of the patients diagnosed with ...
João Bernardo +7 more
doaj +1 more source
Macroglobulinemia de Waldenström: primer caso con confirmación molecular en Honduras [PDF]
Antecedentes: La Macroglobulinemia de Waldens tröm (MW) es un desorden proliferativo en el cual está presente un Linfoma Linfoplasmocitoide (LLP) en la médula ósea y asociado a una gammapatía monoclonal IgM.
Flora Duarte +5 more
doaj +1 more source

