Scleromyxedema: clinical diagnosis and autopsy findings [PDF]
Scleromyxedema is a rare chronic cutaneous mucinosis of unknown etiology. It is characterized by papular eruption and scleroderma with microscopic evidence of mucin deposition, fibroblast proliferation, and fibrosis.
Ana Carolina Bulhões Sala +5 more
doaj +4 more sources
Xantoma plano difuso normolipêmico idiopático com hiperesplenismo Diffuse plane idiopathic normolipemic xanthoma with hiperesplenism [PDF]
O xantoma plano difuso normolipêmico é doença rara, do grupo das histiocitoses, caracterizada pelo aparecimento de placas amareladas ou amarelo-alaranjadas, distribuídas simetricamente na pele e geralmente acompanhadas por xantelasma.
Danielle Machado da Silva +4 more
doaj +2 more sources
O xantogranuloma necrobiótico é doença crônica granulomatosa e xantomatosa, caracterizada por pápulas e placas infiltradas, eritematosas e amareladas, preferencialmente localizadas na região periorbital.
Danielle Mazziero Macedo +5 more
doaj +3 more sources
Systemic amyloidosis: an aggressive evolution in a patient with relapsing polychondritis and monoclonal gammopathy of undetermined significance (MGUS) undergoing peritoneal dialysis [PDF]
Herein, we report the case of primary amyloidosis with multi-organ involvement in a female patient in her 50s. The patient had a history of relapsing polychondritis, chronic kidney disease, and monoclonal gammopathy of undetermined significance (MGUS ...
Thiago Cavalcanti Matos +3 more
doaj +2 more sources
Caracterización del mieloma múltiple y de su componente monoclonal durante 14 años en Las Tunas [PDF]
El mieloma múltiple es una neoplasia de células plasmáticas que representa el 10% de las enfermedades hematológicas malignas. La mayoría de los pacientes presentan síntomas, signos y trastornos de laboratorio sugestivos de enfermedad activa, incluyendo ...
Olga Lina Pupo Rodríguez +3 more
doaj +2 more sources
Dysproteinemia-Associated Kidney Disease: A Single-Center Observational Study [PDF]
Introduction: Dysproteinemia is associated with kidney damage and treatment of underlying conditions is crucial to minimize kidney damage. The aim of this study was to describe and analyze the characteristics and outcome of the patients diagnosed with ...
João Bernardo +7 more
doaj +1 more source
Macroglobulinemia de Waldenström: primer caso con confirmación molecular en Honduras [PDF]
Antecedentes: La Macroglobulinemia de Waldens tröm (MW) es un desorden proliferativo en el cual está presente un Linfoma Linfoplasmocitoide (LLP) en la médula ósea y asociado a una gammapatía monoclonal IgM.
Flora Duarte +5 more
doaj +1 more source
The anion gap is a calculated parameter derived from the difference between the major plasma cations and anions in serum/plasma or whole blood, with a widely used simple equation utilizing concentrations of sodium, chloride, and bicarbonate.
Joseph M. Laakman +2 more
doaj +1 more source
Ileo-ileal Intussusception and Bowel Obstruction Caused by Plasmablastic Lymphoma of Small Bowel- A Rare Entity in Rare Location [PDF]
Intussusception of small bowel is considered a rare cause of bowel obstruction in adults accounting for only about 1% of bowel obstruction in adults. Intussusception in adults is uncommon with 95% cases of intussusceptions occurring in children.
Aditya Atul Kulkarni, Sanjiv S. Thakur
doaj +1 more source
Identification of Monoclonal Immunoglobulins by Immunofixation Electrophoresis - Some Questions
In the series of 2413 paraproteins analyzed by immunoelectrophoresis during 30 years, doubled paraproteinemias were found 42 times, i.e. a frequence of 1.7%.
Miloš Tichý
doaj +1 more source

