Results 1 to 10 of about 1,366 (168)

Scleromyxedema: clinical diagnosis and autopsy findings [PDF]

open access: yesAnais Brasileiros de Dermatologia, 2016
Scleromyxedema is a rare chronic cutaneous mucinosis of unknown etiology. It is characterized by papular eruption and scleroderma with microscopic evidence of mucin deposition, fibroblast proliferation, and fibrosis.
Ana Carolina Bulhões Sala   +5 more
doaj   +4 more sources

Xantoma plano difuso normolipêmico idiopático com hiperesplenismo Diffuse plane idiopathic normolipemic xanthoma with hiperesplenism [PDF]

open access: yesAnais Brasileiros de Dermatologia, 2010
O xantoma plano difuso normolipêmico é doença rara, do grupo das histiocitoses, caracterizada pelo aparecimento de placas amareladas ou amarelo-alaranjadas, distribuídas simetricamente na pele e geralmente acompanhadas por xantelasma.
Danielle Machado da Silva   +4 more
doaj   +2 more sources

Xantogranuloma necrobiótico solitário sem paraproteinemia Necrobiotic xanthogranuloma without paraproteinemia

open access: yesAnais Brasileiros de Dermatologia, 2008
O xantogranuloma necrobiótico é doença crônica granulomatosa e xantomatosa, caracterizada por pápulas e placas infiltradas, eritematosas e amareladas, preferencialmente localizadas na região periorbital.
Danielle Mazziero Macedo   +5 more
doaj   +3 more sources

Systemic amyloidosis: an aggressive evolution in a patient with relapsing polychondritis and monoclonal gammopathy of undetermined significance (MGUS) undergoing peritoneal dialysis [PDF]

open access: yesAutopsy and Case Reports
Herein, we report the case of primary amyloidosis with multi-organ involvement in a female patient in her 50s. The patient had a history of relapsing polychondritis, chronic kidney disease, and monoclonal gammopathy of undetermined significance (MGUS ...
Thiago Cavalcanti Matos   +3 more
doaj   +2 more sources

Caracterización del mieloma múltiple y de su componente monoclonal durante 14 años en Las Tunas [PDF]

open access: yesRevista Electrónica Dr. Zoilo E. Marinello Vidaurreta, 2015
El mieloma múltiple es una neoplasia de células plasmáticas que representa el 10% de las enfermedades hematológicas malignas. La mayoría de los pacientes presentan síntomas, signos y trastornos de laboratorio sugestivos de enfermedad activa, incluyendo ...
Olga Lina Pupo Rodríguez   +3 more
doaj   +2 more sources

Dysproteinemia-Associated Kidney Disease: A Single-Center Observational Study [PDF]

open access: yesRevista Portuguesa de Nefrologia e Hipertensão, 2022
Introduction: Dysproteinemia is associated with kidney damage and treatment of underlying conditions is crucial to minimize kidney damage. The aim of this study was to describe and analyze the characteristics and outcome of the patients diagnosed with ...
João Bernardo   +7 more
doaj   +1 more source

Macroglobulinemia de Waldenström: primer caso con confirmación molecular en Honduras [PDF]

open access: yesRevista Médica Hondureña, 2021
Antecedentes: La Macroglobulinemia de Waldens tröm (MW) es un desorden proliferativo en el cual está presente un Linfoma Linfoplasmocitoide (LLP) en la médula ósea y asociado a una gammapatía monoclonal IgM.
Flora Duarte   +5 more
doaj   +1 more source

Data on the clinical, analytical, and laboratory factors associated with negative anion gaps at an academic medical center

open access: yesData in Brief, 2022
The anion gap is a calculated parameter derived from the difference between the major plasma cations and anions in serum/plasma or whole blood, with a widely used simple equation utilizing concentrations of sodium, chloride, and bicarbonate.
Joseph M. Laakman   +2 more
doaj   +1 more source

Ileo-ileal Intussusception and Bowel Obstruction Caused by Plasmablastic Lymphoma of Small Bowel- A Rare Entity in Rare Location [PDF]

open access: yesJournal of Clinical and Diagnostic Research, 2016
Intussusception of small bowel is considered a rare cause of bowel obstruction in adults accounting for only about 1% of bowel obstruction in adults. Intussusception in adults is uncommon with 95% cases of intussusceptions occurring in children.
Aditya Atul Kulkarni, Sanjiv S. Thakur
doaj   +1 more source

Identification of Monoclonal Immunoglobulins by Immunofixation Electrophoresis - Some Questions

open access: yesActa Medica, 1999
In the series of 2413 paraproteins analyzed by immunoelectrophoresis during 30 years, doubled paraproteinemias were found 42 times, i.e. a frequence of 1.7%.
Miloš Tichý
doaj   +1 more source

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