Results 81 to 90 of about 82,322 (154)

Eculizumab in the management of paroxysmal nocturnal hemoglobinuria: patient selection and special considerations

, 2016
Fatimah Al-Ani,1 Ian Chin-Yee,1 Alejandro Lazo-Langner1,2 1Department of Medicine, Division of Hematology, 2Department of Epidemiology and Biostatistics, Western University, London, ON, Canada Abstract: Paroxysmal nocturnal hemoglobinuria (PNH) is a ...
Chin-Yee I, Lazo-Langner A, Al-Ani F
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Recurrent Ischemic Stroke in Paroxysmal Nocturnal Hemoglobinuria: Paroxysmal Nocturnal Hemoglobinuria or Missed Patent Foramen Ovale? [PDF]

, 2009
Paroxysmal nocturnal hemoglobinuria (PNH) is a rare, acquired bone-marrow disorder characterized by hemolytic anemia, hemoglobinuria, and cytopenia. Most patients die from venous thrombotic events.
Yacoub, Hussam A., MD, Tiu, Ramon, MD, Maciejewski, Jaroslaw, MD, PhD, Sila, Cathy A, MD   +3 more
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Global Epidemiology of Paroxysmal Nocturnal Hemoglobinuria: A Systematic Literature Review

Journal of Epidemiology and Global Health
Background Paroxysmal nocturnal hemoglobinuria (PNH) is a rare acquired hematological disorder characterized by chronic intravascular hemolysis and an increased risk of thrombosis. A systematic synthesis of disease epidemiology is essential to understand
Olessia Zorina, Omid Beiki, Matthew Holt, Jocelyn Buisker, Philippe Ferber, Jilles M. Fermont, Richard J. Kelly   +6 more
doaj   +1 more source

Necrotizing Fasciitis in Paroxysmal Nocturnal Hemoglobinuria

Case Reports in Hematology, 2015
Paroxysmal nocturnal hemoglobinuria (PNH) is a rare, progressive, and life-threatening hematopoietic stem cell disorder characterized by complement-mediated intravascular hemolysis and a prothrombotic state.
Pusem Patir, Yakup Isik, Yigit Turk, Mehmet Can Ugur, Cengiz Ceylan, Gulnur Gorgun, Nihal Mete Gokmen, Guray Saydam, Fahri Sahin   +8 more
doaj   +1 more source

Paroxysmal Nocturnal Hemoglobinuria Superimposed with Preeclampsia

Taiwanese Journal of Obstetrics & Gynecology, 2006
Objective: Paroxysmal nocturnal hemoglobinuria (PNH) is a rare hematologic disorder characterized by complement-mediated intravascular hemolysis. As maternal complication of PNH is already severe, it becomes much more complex when preeclampsia is ...
Mann-Ling Chen, Chen-Hsiang Yu, Fong-Ming Chang, Pao-Lin Kuo   +3 more
doaj   +1 more source

Paroxysmal nocturnal hemoglobinuria and thrombosis

Акушерство, гинекология и репродукция
Paroxysmal nocturnal hemoglobinuria (PNH) is a rare acquired clonal hematopoiesis disorder caused by a somatic mutation in the PIGA (phosphatidylinositol glycan, class A) gene, resulting in deficiency of glycosylphosphatidylinositol (GPI)anchored ...
A. R. Khisamieva, A. R. Oskolkova, V. O. Bitsadze, J. Kh. Khizroeva, N. A. Makatsariya, M. V. Tretyakova, N. R. Gashimova, K. N. Grigoreva, D. V. Blinov, J.-Ch. Gris, I. Elalamy, G. Gerotziafas, A. D. Makatsariya   +12 more
doaj   +1 more source

Paroxysmal Nocturnal Hemoglobinuria and Acute Kidney Injury: A Case Report

, 2013
Paroxysmal nocturnal hemoglobinuria (PNH) is a rare cause of hemolytic anemia. The major outlines of clinical presentation comprises findings of hemolysis, venous thrombosis and findings of bone marrow failure.
Rumeyza Kazancioglu, Ozturk, Savaş, Halil Donmez, KAZANCIOĞLU, Rümeyza, Gursu, Meltem, Kilicarslan, Isin, Isın Kilicarslan, Abdullah Sumnu, Meltem Gursu, Sumnu, Abdullah, Cebeci, Egemen, Savas Ozturk, Egemen Cebeci, Donmez, Halil   +13 more
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Expert Consensus of Multidisciplinary Diagnosis and Treatment for Paroxysmal Nocturnal Hemoglobinuria(2024)

Xiehe Yixue Zazhi
Paroxysmal nocturnal hemoglobinuria (PNH) is an acquired clonal hematopoietic stem cell disease caused by abnormal expression of glycosylphosphatidylinositol (GPI) on the cell membrane due to mutations in the phosphatidylinositol glycan class A(PIGA ...
CHEN Miao, YANG Chen, LIU Ziwei, CAO Wei, ZHANG Bo, LIU Xin, LI Jingnan, LIU Wei, PAN Jie, WANG Jian, ZHENG Yuehong, CHEN Yuexin, LI Fangda, DU Shunda, NING Cong, CHEN Limeng, YUE Cai, NI Jun, PENG Min, GUO Xiaoxiao, WANG Tao, LI Hongjun, LI Rongrong, WU Tong, HAN Bing, ZHANG Shuyang, Multidiscipline Collaboration Group on Rare Disease at Peking Union Medical College Hospital   +26 more
doaj   +1 more source

A raman tweezer study with single red blood cells for the diagnosis of paroxysmal nocturnal hemoglobinuria

, 2022
© 2021 The Author (s).The surface structure of individual erythrocytes changes in the state of paroxysmal nocturnal hemoglobinuria.
Soysal, Kaan Batu, Yenerel, Mustafa, Başar, Günay, Ozbalak, Mustafa Murat, Unlu, Burcin, Mastanzade, Metban, Parlatan, Seyma, Parlatan, Ugur   +7 more
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Off-Pump Coronary Revascularization Using Bilateral Internal Thoracic Arteries in A Patient with Paroxysmal Nocturnal Hemoglobinuria: A Case Report

, 2019
Paroxysmal nocturnal hemoglobinuria (PNH) is an ultra-orphan disease. We report the first case in the literature of Off-Pump Coronary Revascularization Using Bilateral Internal Thoracic Arteries in a patient with paroxysmal nocturnal hemoglobinuria. A 36-
Juan Mariano Vrancic (5628258), Daniel Navia (4732464), Manuel Roque Cervetti (5628244), Julián Benavides (7316717)   +3 more
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