Results 21 to 30 of about 11,158 (184)

European S2k guidelines on management of autoimmune blistering diseases in children and adolescents [PDF]

Journal of the European Academy of Dermatology and Venereology, Volume 40, Issue 7, Page 1137-1161, July 2026.
Autoimmune blistering disorders (AIBDs) in children are rare, challenging to diagnose and treat and often require immunosuppressants. Until now, no paediatric care guidelines existed. The EADV Task Force for AIBDs has developed the consensus‐based recommendations, enabling physicians to adopt a uniform, tailored treatment strategy to improve outcomes ...
A. Nanda, B. Tedbirt, C. Bodemer, M. C. Bolling, M. El Hachem, M. Nikolić, E. Benton, M. Caproni, D. De, D. Didona, K. Drenovska, M. Goebeler, M. Hertl, B. Horváth, M. Kasperkiewicz, D. Kiritsi, M. Larralde, A. V. Marzano, J. Meijer, D. F. Murrell, J. Powell, E. Sprecher, N. S. Chandran, M. M. Tomayko, S. Uzun, N. van Beek, H. Ott, A. Patsatsi, A. Torrelo, A. Welfringer‐Morin, E. Schmidt, P. Joly   +31 more
wiley   +2 more sources

A Case of Pemphigus Herpetiformis in a 12-Year-Old Male [PDF]

ISRN Pediatr, 2011
Pemphigus herpetiformis (PH) is one of the less common forms of pemphigus. PH in children is unreported. We describe a case of a child who developed PH. Observation.
I. Ait Sab, N. Akhdari, M. Hakkou, S. Amal, O. Hocar   +4 more
core   +2 more sources

Development of a Desmocollin-3 Active Mouse Model Recapitulating Human Atypical Pemphigus [PDF]

Frontiers in Immunology, 2019
Pemphigus vulgaris (PV) is a life-threatening mucocutaneous autoimmune blistering disease. It is often associated with autoantibodies to the desmosomal adhesion proteins Desmoglein 3 (DSG3) and Desmoglein 1 (DSG1).
Roberta Lotti, Claudio Giacinto Atene, Alessandra Marconi, Giulia Di Rocco, L. Reggiani Bonetti, Tommaso Zanocco Marani, Carlo Pincelli   +6 more
doaj   +2 more sources

A Single-Center Profile of Pemphigus in China: Significant Diagnostic Delay and Evolving Treatment Patterns [PDF]

Clinical, Cosmetic and Investigational Dermatology
Hanlin Zhang,* Dianmo Li,* Yuqiao Zhang,* Xinyi Lu, Keyun Tang, Ya-Gang Zuo, Hongzhong Jin Department of Dermatology, State Key Laboratory of Complex Severe and Rare Diseases, Peking Union Medical College Hospital, Chinese Academy
Zhang H, Li D, Zhang Y, Lu X, Tang K, Zuo YG, Jin H   +6 more
doaj   +2 more sources

Pemphigus herpetiformis: A case report of response to dupilumab after failure of multiple conventional therapies [PDF]

JAAD Case Reports
Fabiola Pabón-González, MD, Iancarlos Jiménez-Sacarello, MD, José Cuesta-Camuñas, MD, Oscar Nevarez-Pomales, MD, Luis G. García-Guzmán, MD, Melanie Medina-Figueroa, MBA, MD   +5 more
doaj   +2 more sources

A Case of Pemphigus Herpetiformis Strongly Associated with Gastric Cancer [PDF]

Acta Dermato-Venereologica
Masakazu Kakurai, Hana Takeshita, Hiroshi Koga, Norito Ishii, Yoshihiro Moriyama   +4 more
doaj   +2 more sources

Epidemiology of Pemphigus

JID Innovations, 2021
Pemphigus is an epidemiologically heterogeneous group of autoimmune bullous diseases comprising pemphigus vulgaris (PV), pemphigus foliaceus, paraneoplastic pemphigus, IgA pemphigus, and pemphigus herpetiformis.
Khalaf Kridin, Enno Schmidt
doaj   +1 more source

An atypical case of pemphigus herpetiformis with erythroderma [PDF]

JAAD Case Reports
Charlotte Jeong, Peichi P. Chou, Elaine Dong, Amy Shen, Shanice McKenzie, Fiona Lane, Chandra Smart, Yuna Kang, Michael Kasperkiewicz, April W. Armstrong   +9 more
openaire   +3 more sources

A relapse of pemphigus vulgaris in pemphigus herpetiformis or a phenotypic “switch” [PDF]

Our Dermatology Online, 2022
Sir, Pemphigus herpetiformis (PH) was originally described by Jablonska et al. in 1975. Clinically, PH presents itself as a herpetiform dermatitis with immunopathological characteristics of pemphigus [1,2]. We report an exceptional case of typical pemphigus vulgaris (PV) relapsing after 36 years in PH.
Siham Belmourida, Meriame Meziane, Nadia Ismaïli, Laïla Benzekri, Badreddine Hassam, Karima Senouci   +5 more
openaire   +1 more source

Pemphigus Foliaceus [PDF]

, 2022
Pemphigus foliaceus (PF) is a group of autoimmune skin blistering disease comprising four subtypes: Cazenave, endemic, erythematosus and herpetiformis. The common characteristic is the frequent presence of pathogenic anti-desmoglein 1 antibodies leading ...
Laura de Sena N. Maehara, Barbara Horváth, Maehara, Laura de Sena N., Horváth, Barbara, Marcel F. Jonkman, Jonkman, Marcel F., Horváth, Barbara; id_orcid   +6 more
core   +1 more source