Results 71 to 80 of about 5,184 (174)
Resumen: Introducción y objetivos: El síndrome de Peutz-Jeghers (SPJ) es una enfermedad hereditaria, autosómica dominante caracterizada por la presencia de pólipos hamartomatosos en el tubo digestivo de predominio en el intestino delgado y que se ...
G. Blanco-Velasco +6 more
doaj +1 more source
The WHO Classification of Genetic Tumour Syndromes: Considerations for histopathology
Histopathology, Volume 88, Issue 7, Page 1291-1294, June 2026.
Ian A Cree +18 more
wiley +1 more source
El síndrome Peutz - Jeghers es una enfermedad con pólipos del colon con un patrón autosómico dominante, su tipo histológico es hamartomatoso y aunque es muy rara la transformación maligna, se ha postulado una secuencia hamartoma - carcinoma.
María Helena Gaitán Buitrago +7 more
doaj
peutz-jeghers syndrome as a cause of intussusception
Introduction: Peutz-Jeghers syndrome, also known as periorificial lentigines is adisease of autosomal dominant transmission. It is characterized by the associationof gastrointestinal polyposis and mucocutaneous pigmentation, which is evidentfrom the ...
Durango- Guevara Kary +4 more
doaj
Peutzo ir Jegherso sindromo klinika, diagnostika, gydymas ir klinikinis atvejis
Orinta Marija Kviatkovskaja, Vytautas Lipnickas, Kęstutis Strupas Vilniaus universiteto ligoninės Santariškių klinikos Pilvo chirurgijos centras, Santariškių g.
Orinta Marija Kviatkovskaja +2 more
doaj
Se presenta el raro caso de una mujer de 20 años con un tumor del estroma gonadal específico del ovario, variedad tumor de los cordones sexuales, con túbulos anulares no asociado a síndrome de Peutz-Jeghers.
David Mayerson B +4 more
doaj
The Peutz-Jeghers Syndrome [PDF]
openaire +2 more sources
A CASE OF PEUTZ-JEGHER SYNDROME [PDF]
S, Mehrotra +2 more
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Ovarian Sex Cord Stromal Tumor With Annular Tubules: A Rare Diagnosis in Young Women
Ovarian sex cord‐stromal tumor with annular tubules (SCTAT) is a rare neoplasm with distinct clinicopathological features in its sporadic and syndromic forms, the latter commonly associated with Peutz‐Jeghers syndrome.
Prescillia Marques +3 more
doaj +1 more source
Peutz-Jeghers syndrome is an autonomic dominant disease characterized by hamartomatous polyps and mucocutaneous hyperpigmentation. We present 16 cases; females were more affected. The most common presenting complaints were of gastrointestinal tract. All polyps found were hamartomatous with general distribution through gastrointestinal tract. Endoscopic
Roberto, Cervantes Bustamante +6 more
openaire +1 more source

