Heterotaxy pattern associated with sinus node dysfunction in an adult: A case report
Key Clinical Message A 26‐year‐old male patient admitted to the hospital ward with experience of repetitive syncopes for a year. The patient was diagnosed with sick sinus syndrome.
Naman Shah +8 more
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Polysplenia Syndrome With Persistent Left Superior Vena Cava: Case Report and Review of the Literature [PDF]
Polysplenia syndrome is an uncommon condition associating several splenic nodules (sometimes polylobed spleen and cases of normal spleen have been described) with a number of malformations that appear between the fourth and sixth week of embryonic ...
El Houss Salma MD +5 more
doaj +2 more sources
Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adult [PDF]
Polysplenia syndrome associates multiple spleens to other malformations, most frequently cardiac, vascular, visceral, and biliary malformations. Polysplenia has been described mainly in childhood owing to critical anatomic malformations related to ...
Hajar El Mortaji +3 more
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Polysplenia syndrome with semi-annular pancreas, midgut malrotation and interrupted inferior vena cava: A rare adult case report [PDF]
Polysplenia syndrome is a rare congenital anomaly within the heterotaxy spectrum. It is typically diagnosed in childhood due to associated cardiac malformations, whereas detection in adults without cardiovascular involvement is uncommon.
Saber Abdellah Bassel, MD +6 more
doaj +2 more sources
Polysplenia syndrome associated with multisystem malformation: A rare case report [PDF]
Polysplenia syndrome is a rare congenital disease with multiple systemic developmental abnormalities. Their occurrence and development are closely related to embryonic development. The prognosis of the disease depends on its anatomical structure, and the
Wangyi Yang +3 more
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A Rare Case of Polysplenia Syndrome Associated with Severe Cardiac Malformations and Congenital Alveolar Dysplasia in a One-Month-Old Infant: A Complete Macroscopic and Histopathologic Study [PDF]
Polysplenia syndrome represents a type of left atrial isomerism characterized by multiple small spleens, often associated with cardiac malformations and with situs ambiguus of the abdominal organs.
Cosmin Ioan Mohor +13 more
doaj +2 more sources
Polysplenia Syndrome and the Development of Heart Failure due to Associated Congenital Heart Defect [PDF]
Key message: Patients with polysplenia syndrome can develop pulmonary hypertension and heart failure due to underlying congenital heart disease, underscoring the need for early recognition and intervention to prevent further progression of the condition.
Valerie Van Ballaer +2 more
doaj +2 more sources
BILIARY ATRESIA IS ASSOCIATED WITH POLYSPLENIA AND SITUS INVERSUS ON ULTRASOUND, A CASE REPORT STUDY. [PDF]
Biliary atresia is a destructive, idiopathic, and inflammatory cholangiopathy that affects intra and extra-hepatic bile ducts leading to fibrosis and obliteration of the biliary tract and development of liver cirrhosis.
Evalyne Tukwasibwe +3 more
doaj +3 more sources
From multiple spleens to absence: Insights from two cases of heterotaxy syndromes [PDF]
Heterotaxy syndrome is a rare congenital disorder characterized by abnormal arrangement of the thoracic and abdominal organs and is classified into polysplenia (left isomerism) and asplenia (right isomerism) syndromes.
Suman Paudel, MD +4 more
doaj +2 more sources
Intra-Abdominal Abnormalities Associated with Polysplenia Syndrome [PDF]
What to look for in case of polysplenia and/or unusual disposition of several intra-abdominal organs.
Hadrien Renier
doaj +2 more sources

