Results 61 to 70 of about 1,713 (227)

Obliterative cholangiopathy in acquired cystic biliary atresia type III after cyst perforation: a case report

BMC Pediatrics, 2018
Background In biliary atresia, the disease process of obliterative cholangiopathy may begin in the perinatal period; however, no chronological evidence exists on how the cholangiopathy progresses to biliary obliteration.
Tsugumichi Koshinaga, Kensuke Ohashi, Kakou Ono, Hide Kaneda, Takeshi Furuya   +4 more
doaj   +1 more source

Surgical technique of orthotopic liver transplantation [PDF]

, 1988
Athough significant strides have been made in the surgical technique of orthotopic liver transplantation, numerous problems and nuisances are still encountered. Further surgical refinements will certainly evolve.
Bowman, J, Kahn, D, Makowka, L, Mieles, L, Sher, L, Starzl, TE, Stieber, AC, Wallis Marsh, J   +7 more
core   +1 more source

Improved Results with Hepatic Portoenterostomy

Annals of Surgery, 1982
As reported in 1974, the initial experience at the Oklahoma Children's Memorial Hospital with the Kasai procedure for biliary atresia was unsatisfactory. A subsequent series of 20 patients, in which 50% of the patients are alive and improved and 25% jaundice-free, is described.
E I, Smith, J A, Carson, W P, Tunell, D C, Hitch, T J, Pysher   +4 more
openaire   +3 more sources

Extrahepatic biliary atresia and normal‐range serum gamma‐glutamyltranspeptidase activity: A case report

JPGN Reports, Volume 5, Issue 4, Page 533-537, November 2024.
Abstract An infant with biliary atresia had normal‐range (‘low’) serum gamma‐glutamyltranspeptidase (GGT) activity, exceptional because GGT generally is elevated in biliary atresia. Mechanisms underlying low‐GGT cholestasis in biliary atresia are not defined, but the phenomenon is associated with worse clinical outcome.
Benno Kohlmaier, Heidelis Tichy, Jasmin Blatterer, Holger Till, Axel Schlagenhauf, A. S. Knisely   +5 more
wiley   +1 more source

Postoperative Imaging Findings of Biliary Atresia

대한영상의학회지, 2022
The Kasai portoenterostomy is the first-line treatment for the restoration of the flow of bile to the small intestine in patients with biliary atresia.
Jisun Hwang, Hee Mang Yoon, Pyeong Hwa Kim, Jung-Man Namgoong, Seak Hee Oh, Ah Young Jung, Jin Seong Lee, Young Ah Cho   +7 more
doaj   +1 more source

A genome-wide association study identifies a susceptibility locus for biliary atresia on 2p16.1 within the gene EFEMP1 [PDF]

, 2018
Biliary atresia (BA) is a rare pediatric cholangiopathy characterized by fibrosclerosing obliteration of the extrahepatic bile ducts, leading to cholestasis, fibrosis, cirrhosis, and eventual liver failure.
Bailey-Wilson, Joan E, Chen, Ying, Devoto, Marcella, Gilbert, Melissa A, Grochowski, Christopher M, Hakonarson, Hakon, Llewellyn, Jessica, Loomes, Kathleen M, Mceldrew, Deborah, Russo, Pierre, Spinner, Nancy B, Waisbourd-Zinman, Orith, Wells, Rebecca G   +12 more
core   +2 more sources

Patient complexity and genotype-phenotype correlations in biliary atresia: a cross-sectional analysis [PDF]

, 2017
published_or_final_versio
Chan, EKW, Cheng, G, Cherny, SS, Chung, HY, Garcia-Barcelo, MM, Sham, PC, So, MT, Tam, PKH   +7 more
core   +2 more sources

Awareness, referral and age at Kasai surgery for biliary atresia in Europe: A survey of the Quality‐of‐Care Task Force of ESPGHAN

Journal of Pediatric Gastroenterology and Nutrition, Volume 78, Issue 6, Page 1374-1382, June 2024.
Abstract Objectives To identify infants with biliary atresia (BA), European Society of Paediatric Gastroenteroloy and Nutrition (ESPGHAN)/North American Society of Pediatric Gastroenteroloy and Nutrition (NASPGHAN) guidelines recommend measurement of conjugated/direct bilirubin in infants with prolonged jaundice and using a stool colour card (SCC). The
Florence Lacaille, Emanuele Nicastro, Piotr Czubkowski, Cristina Campos Gonçalves, Thu Giang Le Thi, Sibylle Koletzko, the ESPGHAN Quality‐of‐Care Task Force   +6 more
wiley   +1 more source

A histopathological study of liver and biliary remnants with clinical outcome in cases of extrahepatic biliary atresia

Indian Journal of Pathology and Microbiology, 2010
Context: The indicators of poor prognosis in cases of extrahepatic biliary atresia (EHBA) continue to remain controversial. Aims: To correlate the histopathological findings of wedge biopsy from liver and tissue obtained from the shaving at the porta ...
Roy Paromita, Chatterjee Uttara, Ganguli M, Banerjee Sugato, Chatterjee S, Basu A   +5 more
doaj  

P53 Mutation at Codon 249 is Uncommon in Neonatal Kotb Disease Biliary Atresia [PDF]

Pediatric Sciences Journal
Background: Hepatocellular carcinoma (HCC) is known to result from aflatoxin B1 that induces p53 mutation at codon 249. Aflatoxins are also known to cause The Kotb disease Biliary atresia (BA) variant which is characterized by congenital aflatoxicosis B1
Magd A. Kotb, Ayda K. Kelany, Sherif Shehata, Gamal El Tagy, Sherif Kaddah, Nahla I. Sabry, Ahmed A. Elhaddad, Radwa Shamma   +7 more
doaj   +1 more source