Results 71 to 80 of about 613,875 (232)

Obliterative cholangiopathy in acquired cystic biliary atresia type III after cyst perforation: a case report

BMC Pediatrics, 2018
Background In biliary atresia, the disease process of obliterative cholangiopathy may begin in the perinatal period; however, no chronological evidence exists on how the cholangiopathy progresses to biliary obliteration.
Tsugumichi Koshinaga, Kensuke Ohashi, Kakou Ono, Hide Kaneda, Takeshi Furuya   +4 more
doaj   +1 more source

Extrahepatic biliary atresia and normal‐range serum gamma‐glutamyltranspeptidase activity: A case report

JPGN Reports, Volume 5, Issue 4, Page 533-537, November 2024.
Abstract An infant with biliary atresia had normal‐range (‘low’) serum gamma‐glutamyltranspeptidase (GGT) activity, exceptional because GGT generally is elevated in biliary atresia. Mechanisms underlying low‐GGT cholestasis in biliary atresia are not defined, but the phenomenon is associated with worse clinical outcome.
Benno Kohlmaier, Heidelis Tichy, Jasmin Blatterer, Holger Till, Axel Schlagenhauf, A. S. Knisely   +5 more
wiley   +1 more source

Postoperative Imaging Findings of Biliary Atresia

대한영상의학회지, 2022
The Kasai portoenterostomy is the first-line treatment for the restoration of the flow of bile to the small intestine in patients with biliary atresia.
Jisun Hwang, Hee Mang Yoon, Pyeong Hwa Kim, Jung-Man Namgoong, Seak Hee Oh, Ah Young Jung, Jin Seong Lee, Young Ah Cho   +7 more
doaj   +1 more source

Awareness, referral and age at Kasai surgery for biliary atresia in Europe: A survey of the Quality‐of‐Care Task Force of ESPGHAN

Journal of Pediatric Gastroenterology and Nutrition, Volume 78, Issue 6, Page 1374-1382, June 2024.
Abstract Objectives To identify infants with biliary atresia (BA), European Society of Paediatric Gastroenteroloy and Nutrition (ESPGHAN)/North American Society of Pediatric Gastroenteroloy and Nutrition (NASPGHAN) guidelines recommend measurement of conjugated/direct bilirubin in infants with prolonged jaundice and using a stool colour card (SCC). The
Florence Lacaille, Emanuele Nicastro, Piotr Czubkowski, Cristina Campos Gonçalves, Thu Giang Le Thi, Sibylle Koletzko, the ESPGHAN Quality‐of‐Care Task Force   +6 more
wiley   +1 more source

P53 Mutation at Codon 249 is Uncommon in Neonatal Kotb Disease Biliary Atresia [PDF]

Pediatric Sciences Journal
Background: Hepatocellular carcinoma (HCC) is known to result from aflatoxin B1 that induces p53 mutation at codon 249. Aflatoxins are also known to cause The Kotb disease Biliary atresia (BA) variant which is characterized by congenital aflatoxicosis B1
Magd A. Kotb, Ayda K. Kelany, Sherif Shehata, Gamal El Tagy, Sherif Kaddah, Nahla I. Sabry, Ahmed A. Elhaddad, Radwa Shamma   +7 more
doaj   +1 more source

Nutritional status of children with biliary atresia and the role of portoenterostomy to improve nutrition

Journal of Indian Association of Pediatric Surgeons, 2020
Background: Nutritional depletion and growth stunting are present in patients with biliary atresia; “normal” nutrient and vitamin supplementation fail to correct these deficiencies.
Shailesh Solanki, Veereshwar Bhatnagar, Sandeep Agarwala, Rakesh Lodha, Nandita Gupta, Manoj Kumar Singh   +5 more
doaj   +1 more source

Diagnostic and Prognostic Significance of Various Histopathological Features in Extrahepatic Biliary Atresia [PDF]

Journal of Clinical and Diagnostic Research, 2016
Introduction: Extrahepatic biliary atresia is a progressive disorder characterised by fibroinflammatory obliteration or stenosis of the extrahepatic biliary tree leading to obstruction of bile flow and cholestatic jaundice.
Shenbagam Jeevakarunyam Muthukanagarajan, Indumathi Karnan, Padmanaban Srinivasan, Pappathi Sadagopan, Saraswathy Manickam   +4 more
doaj   +1 more source

Distinct effects of racial and socioeconomic disparities on biliary atresia diagnosis and outcome

Journal of Pediatric Gastroenterology and Nutrition, Volume 78, Issue 5, Page 1038-1046, May 2024.
Abstract Objectives To identify and distinguish between racial and socioeconomic disparities in age at hepatology care, diagnosis, access to surgical therapy, and liver transplant‐free survival in patients with biliary atresia (BA). Methods Single‐center retrospective cohort study of 69 BA patients from 2010 to 2021.
Julie Bonn, Kristen Gamm, Teresa Ambrosino, Sarah H. Orkin, Amy Taylor, Anna L. Peters   +5 more
wiley   +1 more source

Correlation between Histological Changes of Liver and Early Surgical Outcome of Kasai Portoenterostomy in Biliary Atresia

SAS Journal of Surgery
Background: Biliary atresia (BA) is a progressive fibrosing obstructive cholangiopathy involving both resulting in the intrahepatic and extrahepatic bile ducts. Hepatic portoenterostomy was first described by Kasai and Suzuki in 1959 to re-establish bile
Md. Mustafizur Rahman, A. Hossain, Md. Rezaul Islam, Md. Ahsan Habib, Bishnu Pada Dey, Mahabub Hossain, Md. Rezaul Karim Mojumder, Shapla Sultana, F. Jannat   +8 more
semanticscholar   +1 more source

Correlation of pre- and post-operative liver function, duct diameter at porta hepatis, and portal fibrosis with surgical outcomes in biliary atresia

Journal of Indian Association of Pediatric Surgeons, 2015
Background and Aims: Extrahepatic biliary atresia is one of the most challenging conditions in pediatric surgery. The definition of prognostic factors is controversial. Surgical outcomes after bilioenteric drainage procedures are variable.
Rajib Ray Baruah, Veereshwar Bhatnagar, Sandeep Agarwala, Siddhartha Datta Gupta   +3 more
doaj   +1 more source