Results 291 to 300 of about 17,877 (340)

Cardiomyopathy in propionic acidaemia

European Journal of Pediatrics, 1993
Following the death of a patient with propionic acidaemia with a cardiomyopathy we reviewed 19 patients with the same disorder for evidence of cardiomyopathy. Six patients were found to meet the diagnostic criteria. Three patients died and in the other three the cardiac disease resolved completely.
A F, Massoud, J V, Leonard
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Methylmalonic and propionic aciduria

American Journal of Medical Genetics Part C: Seminars in Medical Genetics, 2006
AbstractMethylmalonic and propionic aciduria (PA) are the most frequent forms of branched‐chain organic acidurias. These autosomal recessive disorders result from deficient activity of methylmalonyl‐CoA mutase and propionyl‐CoA carboxylase, respectively.
Federica, Deodato, Sara, Boenzi, Filippo M, Santorelli, Carlo, Dionisi-Vici   +3 more
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The Neuropathology of Propionic Acidemia

Developmental Medicine & Child Neurology, 1983
SUMMARYThe neuropathology in two biochemically documented cases of propionic acidemia is presented. While spongiform changes in white matter were seen in the infant who died at 12 days, no such changes were evident in an older patient who died at age 23 months.
L, Steinman, R R, Clancy, H, Cann, H, Urich   +3 more
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The Reaction Rates of Propionic and Acetic Propionic Anhydrides

The Journal of Chemical Physics, 1936
The infrared absorption spectra of mixtures of water and acetic propionic and of propionic anhydrides have been measured in the region from 5μ to 6.4μ. The intensity of the bands was found to decrease with time. By using the relative intensity of the anhydride band the reaction rate was calculated for three concentrations.
E. S. Barr, E. K. Plyler
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Syntrophic Propionate Oxidation

1990
In vivo high-resolution NMR with the Gram-negative Syntrophobacter wolinii and a Gram-positive syntrophic propionate oxidizing organism, indicated the involvement of an oxaloacetate: propionyl-CoA transcarboxylase in propionate oxidation. This finding was confirmed by enzyme measurement in cell-free extracts.
Houwen, F.P., Plokker, J., Dijkema, C., Stams, A.J.M.   +3 more
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In vivo propionate oxidation as a prognostic indicator in disorders of propionate metabolism

European Journal of Pediatrics, 1990
Biochemical markers such as plasma and urinary metabolite concentrations and in vitro enzyme activity are of limited prognostic value in the most common disorders of propionate metabolism, methylmalonic acidaemia (MMA) and propionic acidaemia (PA). In vivo propionate oxidation was compared with conventional prognostic measures as predictors of clinical
G N, Thompson, J H, Walter, J L, Bresson, J P, Bonnefont, J M, Saudubray, J V, Leonard, D, Halliday   +6 more
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Dermatopharmacologic investigations of halobetasol propionate in comparison with clobetasol 17-propionate

Journal of the American Academy of Dermatology, 1991
Both halobetasol propionate and clobetasol 17-propionate exerted very marked antiinflammatory, antiproliferative, and vasoconstrictive effects during evaluation in a range of dermatopharmacologic models. Halobetasol propionate was distinctly more potent than clobetasol 17-propionate in the ultraviolet-induced dermatitis inhibition assay in guinea pigs ...
S, Yawalkar, I, Wiesenberg-Boettcher, J R, Gibson, S B, Siskin, W, Pignat   +4 more
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Pharmacology of fluticasone propionate

Respiratory Medicine, 1994
Fluticasone propionate is a new corticosteroid which has been used intranasally in the treatment of rhinitis and is now being introduced as a drug to be given by the inhaled route for the treatment of asthma (1). When reviewing the pharmacology of a new corticosteroid given by inhalation in asthma we need to review the fate of the drug from the moment ...
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Regioselectively substituted cellulose benzoate propionates for compensation film in optical displays

Carbohydrate Polymers, 2021
Charles R Buchanan, Bin Wang
exaly  

Synthesis of Propionic Anhydride and Propionic Acid

Industrial & Engineering Chemistry, 1957
R. E. Brooks, W. F. Gresham, J. V. E. Hardy, J. M. Lupton   +3 more
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