Results 241 to 250 of about 1,195,100 (331)

Long‐term outcome after allogeneic stem cell transplantation for GATA2 deficiency: An analysis of 67 adults and children from France and Belgium

British Journal of Haematology, Volume 208, Issue 1, Page 250-258, January 2026.
The overall survival of patients receiving an allogeneic haematopoietic stem cell transplant (HSCT) for GATA2 deficiency was significantly better if they were transplanted recently, with a bone marrow or cord blood graft and if the transplant was performed before the onset of excess blast. Excess blast before HSCT was the only factor associated with an
Flore Sicre de Fontbrune, Florian Chevillon, Mony Fahd, Kristell Desseaux, Xavier Poiré, Edouard Forcade, Arthur Sterin, Bénédicte Neven, Virginie Gandemer, Sylvain Thepot, Alice Garnier, Bruno Lioure, Ambroise Marcais, Stephanie Nguyen‐Quoc, Suzanne Tavitian, Laure Vincent, Jean Donadieu, Matthieu Resche Riggon, Sylvie Chevret, Marlene Pasquet, Regis Peffault de Latour   +20 more
wiley   +1 more source

Alpha-1 Antitrypsin Gene Variants in Patients without Severe Deficiency Diagnosed with Pulmonary Emphysema on Chest CT. [PDF]

Int J Chron Obstruct Pulmon Dis
Laviña E, Lumbreras S, Bravo L, Soriano JB, Izquierdo JL, Rodríguez JM.   +5 more
europepmc   +1 more source

Frailty as a Key Determinant of Cardiovascular Risk and Mortality in Preserved Ratio Impaired Spirometry: A Nationally Representative Study

The Clinical Respiratory Journal, Volume 20, Issue 1, January 2026.
In adults with preserved ratio impaired spirometry (PRISm), frailty was common and strongly associated with increased cardiovascular events and all‐cause mortality. Frailty significantly improved risk stratification beyond traditional clinical factors. A frailty‐based nomogram demonstrated good discrimination and calibration, highlighting frailty as a ...
Yue Ren, Yixing Wu, Weiping Hu, Li Liu, Hui Cai, Jing Zhang   +5 more
wiley   +1 more source

Filamin A gene mutation in an infant with progressive pulmonary emphysema, periventricular nodular heterotopia and congenital heart disease. [PDF]

BMJ Case Rep
Khera S, Jauhari S, Pattanayak S, Choubey M.   +3 more
europepmc   +1 more source

OBSERVATIONS ON THE PATHOLOGIC PHYSIOLOGY OF CHRONIC PULMONARY EMPHYSEMA

, 1920
R. Scott
semanticscholar   +1 more source

Paratracheal air cysts on thoracic multidetector CT: incidence, morphological characteristics and relevance to pulmonary emphysema.

British Journal of Radiology, 2013
H. Bae, E. Kang, H. Yong, Yul-Seong Kim, O. Woo, Y. Oh, K. Doo   +6 more
semanticscholar   +1 more source

SMARCA4‐Deficient Undifferentiated Thoracic Tumor: Clinical Features and Prognosis of a Case Series and Literature Review

The Clinical Respiratory Journal, Volume 20, Issue 1, January 2026.
Our manuscript presents detailed presentations of case series of thoracic SMARCA4‐UT, and we report a unique case of diaphragmatic metastases and, interestingly, the occurrence of brain metastasis in one patient, which is a rare phenomenon in SMARCA4‐UT.
Fangzhen Shan, Shuntao Liang, Youwen Zhang, Wei Wu, Guangxia Yang, Mei Yan, Xuemei Zhang, Yumao Miao, Linlin Liu, Jingjing Cai, Zhitao Shi, Bangdong Liu, Nannan Zhang   +12 more
wiley   +1 more source

Clinical Study on Masquelet Membrane Induction Technique Combined With Free Skin Grafting for the Treatment of Chronic Refractory Wounds With Bone/Tendon Exposure in Aged Patients

International Wound Journal, Volume 23, Issue 1, January 2026.
ABSTRACT The treatment of chronic wounds in the Aged is often difficult. Masquelet technique is used for the treatment of infected large segmental bone defects as it provides an adequate blood supply for bone and soft tissue reconstruction. In this study, a two‐stage wound management strategy was used, consisting of covering the initial wound with bone
Jianyuan Gao, Shenkai Su, Feiya Zhou, Yingying Zhang, Guangheng Xiang, Zupo Yu   +5 more
wiley   +1 more source

Pulmonary Microvascular Blood Flow in Mild Chronic Obstructive Pulmonary Disease and Emphysema. The MESA COPD Study.

American Journal of Respiratory and Critical Care Medicine, 2015
K. Hueper, J. Vogel-Claussen, Megha A. Parikh, J. Austin, D. Bluemke, J. Carr, Jiwoong Choi, T. Goldstein, A. Gomes, E. Hoffman, S. Kawut, J. Lima, E. Michos, W. Post, M. Po, M. Prince, Kiang Liu, Daniel Rabinowitz, J. Skrok, Ben M. Smith, K. Watson, Youbing Yin, Alan M. Zambeli-Ljepovic, R. Barr   +23 more
semanticscholar   +1 more source

Kaempferol Mitigates CSE‐Induced Lung Injury and Epithelial Cell Ferroptosis via Modulating Nrf2/NCOA4/GPx4 Axis

Journal of Cellular and Molecular Medicine, Volume 30, Issue 1, January 2026.
ABSTRACT Ferroptosis, an iron‐dependent regulated necrosis driven by redox imbalance, plays a critical role in the pathogenesis of chronic obstructive pulmonary disease (COPD). Kaempferol (KF), a bioactive flavonoid from Polygonati Rhizoma, exhibits anti‐ferroptotic properties in lipid peroxidation disorders, yet its molecular mechanism against ...
Fengri Jin, Yanfei Xing, Songyu Li, Zhennan Yi, Aibin Wu, Xin Li   +5 more
wiley   +1 more source