Results 81 to 90 of about 493,260 (275)

Whole‐Body Pattern of Muscle Degeneration and Progression in Sarcoglycanopathies

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective To characterize whole‐body intramuscular fat distribution pattern in patients with sarcoglycanopathies and explore correlations with disease severity, duration and age at onset. Methods Retrospective, cross‐sectional, multicentric study enrolling patients with variants in one of the four sarcoglycan genes who underwent whole‐body ...
Laura Costa‐Comellas, Mauro Monforte, Angel Sanchez‐Montañez, Penélope Romero‐Duque, Elena Pegoraro, Jordi Díaz‐Manera, Dmitry Vlodavets, Lorenzo Maggi, Marco Moscatelli, Adele D‘Amico, Montse Olivé, Jorge Alonso‐Pérez, Giacomo Comi, José Miguel Escudero‐Fernández, Gabriela S. Urcuyo, Anna Pichiecchio, Angela Berardinelli, Kristl G. Claeys, Claudio Bruno, Chiara Panicucci, Sara Bortolani, Eleonora Torchia, Enzo Ricci, Soledad Monges, Jorge A. Bevilacqua, Jorge Diaz‐Jara, Maggie C. Walter, Simone Thiele, Nicoline Løkken, John Vissing, Susana Quijano‐Roy, Robert Y. Carlier, Nicol C. Voermans, Chiara Marini‐Bettolo, Michela Guglieri, Volker Straub, Lea Leonardis, Francina Munell, David Gómez‐Andrés, Giorgio Tasca   +39 more
wiley   +1 more source

Coexistence and competition of multiple charge-density-wave orders in rare-earth tri-telluride RTe3

, 2014
The occurrences of collective quantum states, such as superconductivity (SC) and charge- or spin-densitywaves (CDWs or SDWs), are among the most fascinating phenomena in solids. To date much effort has been made to explore the interplay between different
Cheng, B., Dong, T., Hu, B. F., Wang, N. L., Yuan, R. H.   +4 more
core   +1 more source

Clinical Spectrum and Outcomes of SOX1 Antibody‐Associated Paraneoplastic Neurological Syndromes: A Chinese Cohort Study

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Background SOX1 antibody‐positive paraneoplastic neurological syndromes (PNS) exhibit significant population‐specific clinical heterogeneity. While Western cohorts predominantly manifest Lambert‐Eaton myasthenic syndrome (65%–80%), comprehensive clinical characterization and treatment response data in Asian populations remain critically ...
Jin‐Long Ye, Zu‐Ying Kuang, Bo Li, Meng‐Qiu Pan, Li‐Hua Zhou, Yang‐Yang Dai, Si‐Fen Xie, Xian‐Guang Lin, Ye‐Peng Hu, Li‐Hong Jiang, Zhan‐Hang Wang, Wei‐Jing Zhang   +11 more
wiley   +1 more source

Introduction to a Resources Special Issue on Criticality of the Rare Earth Elements: Current and Future Sources and Recycling

, 2018
The rare earth elements (REE) are vital to modern technologies and society and are amongst the most important of the critical elements. This special issue of Resources examines a number of facets of these critical elements, current and future sources of ...
Jowitt, Simon M.
core   +2 more sources

Rare earth elements distribution in marine sediments of Malaysia coasts [PDF]

, 2009
In the east coast Peninsular Malaysia region, sediments are transported by several rivers from the east Malaysia into the South China Sea estuary. In the vicinity of the five river estuaries core sediments were collected in order to investigate rare ...
Abdi, Mohammad Reza, Saion, Elias, Saraee, Khadijeh Rezaee Ebrahim, Wood, Abdul Khalik   +3 more
core   +1 more source

Remote Assessment of Ataxia Severity in SCA3 Across Multiple Centers and Time Points

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective Spinocerebellar ataxia type 3 (SCA3) is a genetically defined ataxia. The Scale for Assessment and Rating of Ataxia (SARA) is a clinician‐reported outcome that measures ataxia severity at a single time point. In its standard application, SARA fails to capture short‐term fluctuations, limiting its sensitivity in trials.
Marcus Grobe‐Einsler, Vivian Maas, Arian Taheri Amin, Jennifer Faber, Tamara Schaprian, Katharina Hill, Matthis Synofzik, Lisa H. Graf, Heike Jacobi, Manuela Lima, Ana F. Ferreira, Bart P. van de Warrenburg, Ilse H. J. Willemse, Dagmar Timmann, Andreas Thieme, Paola Giunti, Hector Garcia‐Moreno, Magda M. Santana, Jeannette Hübener‐Schmid, Elin H. Davies, Thomas Klockgether   +20 more
wiley   +1 more source

Nuclear Forensic Analysis of Rare Earth Elements in Uranium Ore Concentrates

Yankuang ceshi
The distribution pattern of rare earth elements (REEs) in uranium ore concentrates (UOC) is an important fingerprint information for geological source tracing in nuclear forensics.
Lan WANG, Quanli CHU, Liangsheng GE, Jianchen JI, Ming HUANG, Zhaohui WU   +5 more
doaj   +1 more source

Diffusion Spectrum Imaging Maps Early Axonal Loss and a Unique Progressive Signal in Neuronal Intranuclear Inclusion Disease

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective To delineate specific in vivo white matter pathology in neuronal intranuclear inclusion disease (NIID) using diffusion spectrum imaging (DSI) and define its clinical relevance. Methods DSI was performed on 42 NIID patients and 38 matched controls.
Kaiyan Jiang, Yixiu Pei, Xiaobao Hu, Ying Xiong, Fang Wang, Yanyan Yu, Min Zhu, Dandan Tan, Meihong Zhou, Daojun Hong, Fuqing Zhou   +10 more
wiley   +1 more source

Method of forming low cost, formable High T(subc) superconducting wire [PDF]

A ceramic superconductivity part, such as a wire, is produced through the partial oxidation of a specially formulated copper alloy in a core. The alloys contains low level of quantities of rare earth and alkaline earth dopant elements.
Smialek, James L.
core   +1 more source

Rare earth elements in Andaman Island surface water : geochemical tracers for the monsoon [PDF]

, 2012
The Asian summer monsoon affects the lives of billions of people. With the aim of identifying geochemical tracers for the monsoon related freshwater input from the major rivers draining into the Bay of Bengal and Andaman Sea we have taken surface ...
Frank, Martin, Hathorne, Ed, Mohan, P. M.   +2 more
core