Clinical and laboratory variability in a cohort of patients diagnosed with type 1 VWD in the United States [PDF]
Von Willebrand disease (VWD) is the most common inherited bleeding disorder, and type 1 VWD is the most common VWD variant. Despite its frequency, diagnosis of type 1 VWD remains the subject of much debate.
Abshire, T.C. +24 more
core +1 more source
Abstract Background We tested the hypothesis that the addition of biomarkers of multimorbidity and biological aging would improve the predictive accuracy of point‐of‐care viscoelastometry or laboratory tests of coagulation for clinically important bleeding following cardiac surgery.
Weiqi Liao +8 more
wiley +1 more source
Influences of ABO blood group, age and gender on plasma coagulation factor VIII, fibrinogen, von Willebrand factor and ADAMTS13 levels in a Chinese population [PDF]
Background ABO blood group is a hereditary factor of plasma levels of coagulation factor VIII (FVIII) and von Willebrand factor (VWF). Age and gender have been shown to influence FVIII, VWF, fibrinogen (Fbg), and ADAMTS13 (A disintegrin and ...
Zongkui Wang +11 more
doaj +2 more sources
Increased plasma von Willebrand factor antigen levels but normal von Willebrand factor cleaving protease (ADAMTS13) activity in preeclampsia. [PDF]
The activity of ADAMTS13, the von Willebrand factor (VWF) cleaving protease is low in several conditions, including HELLP (haemolysis, elevated liver enzymes, and low platelet count) syndrome.
Bõze, Tamás +9 more
core +1 more source
Essential Thrombocythemia's Role in the Complex Landscape of Vasculitis: A Case Report
ABSTRACT Peripheral gangrenes have been sporadically documented as the initial presentation of essential thrombocythemia (ET), as exemplified in the preceding case reports. Nevertheless, the prevalence of vasculitis‐induced skin problems as the primary indication of ET has not been extensively examined.
Mohammad Reza Jafari Nakhjavani +8 more
wiley +1 more source
Platelet function was studied in a child with myelodysplastic syndrome (MDS: refractory anemia with an excess of blasts) and a child with acute myeloblastic leukemia (AML-M6) associated with trilineage myelodysplasia (TMDS).
G Hiçsönmez +5 more
doaj
Lymphoma‐associated acquired von Willebrand syndrome responsive to splenectomy: A case report
A previously healthy 33‐year‐old female presented with a large hematoma over her right knee after kneeling. She was found to have pancytopenia and massive splenomegaly.
Fatima Khadadah +5 more
doaj +1 more source
MYH9-related disease: Five novel mutations expanding the spectrum of causative mutations and confirming genotype/phenotype correlations [PDF]
MYH9-related disease (MYH9-RD) is a rare autosomal dominant syndromic disorder caused by mutations in MYH9, the gene encoding for the heavy chain of non-muscle myosin IIA (myosin-9).
Balduini, Carlo L. +12 more
core +1 more source
Complications at Diagnosis of Pediatric Chronic Myeloid Leukemia in Chronic Phase
ABSTRACT Chronic myeloid leukemia (CML) is uncommon during the first two decades of life, resulting in limited experience of pediatricians in handling this leukemia. This is even more true when it comes to managing rare complications at the time of diagnosis.
Nirmalya Roy Moulik +4 more
wiley +1 more source
Ristocetin-induced platelet aggregation, von Willebrand factor and coagulation factor VIII of 170 children with essential arterial hypertension and 40 healthy children were investigated.
M. V. Gomellya
doaj

