Monoclonal Gammopathies of Clinical Significance—Scleromyxedema: A Case Report and Literature Review [PDF]
Clinical Case ReportsScleromyxedema is an uncommon, chronic connective tissue disorder with an obscure etiology. It is distinguished by fibromyxoid skin lesions and elevated serum monoclonal immunoglobulin levels.
Shanshan Liang +4 more
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Skin‐Colored Papules on the Face and Chest of a Female Patient [PDF]
Clinical Case ReportsScleromyxedema is an unpredictable but progressive disease and can be lethal due to systemic involvement if not diagnosed timely. Hence, we require a keen observational clinical eye to diagnose the condition from its differentials, along with further ...
Mehdi Ghahartars +3 more
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Scleromyxedema: clinical diagnosis and autopsy findings [PDF]
Anais Brasileiros de Dermatologia, 2016 Scleromyxedema is a rare chronic cutaneous mucinosis of unknown etiology. It is characterized by papular eruption and scleroderma with microscopic evidence of mucin deposition, fibroblast proliferation, and fibrosis.
Ana Carolina Bulhões Sala +5 more
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Case report: Scleromyxedema associated with a monoclonal gammapathy: Successful treatment with intravenous immunoglobulins [PDF]
Frontiers in Immunology, 2023 Scleromyxedema is a rare idiopathic fibromucinous disorder characterized by a generalized papular and sclerodermoid cutaneous eruption. Patients often have praraproteinemia and extracutaneous, even lethal, manifestations.
Shang-shang Wang +2 more
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Clinical Characteristics and Treatment Outcomes of Scleromyxedema: A 10-Year Retrospective Survey [PDF]
Case Reports in Dermatology, 2022 Scleromyxedema is a rare but important mucinosis disorder of the skin that is presented with dermatological manifestations such as waxy papules, diffuse induration, and nondermatologic involvements like neurological and renal disorders.
Abtin Ansari +6 more
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Discrete Papular Lichen Myxedematosus and Scleromyxedema with Hypothyroidism: A Report of Two Cases [PDF]
Case Reports in Dermatology, 2019 Scleromyxedema and lichen myxedematosus (LM) are rare disorders that fall along the spectrum of primary cutaneous mucinoses. Scleromyxedema is a systemic form that classically presents with generalized waxy papules, sclerodermoid eruption, and monoclonal
Adele Shenoy +3 more
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Lichen myxedematosus associated with monoclonal gammopathy of undetermined significance: A case report and literature review [PDF]
Frontiers in Medicine, 2023 Lichen myxedematosus (LM) is an idiopathic cutaneous mucinosis disorder, and monoclonal gammopathy of undetermined significance (MGUS) is a preneoplastic plasma cell disease with a monoclonal increase in globulin.
Hua Huang, Shen-Xian Qian
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Treatment of a Complex Case of Scleromyxedema Using a Novel Intravenous Immunoglobulin Preparation [PDF]
Case Reports in DermatologyIntroduction: We provide a case report on a patient with scleromyxedema treated with high-dose intravenous immunoglobulins (IVIgs) who reported less fatigue and fewer headaches after transitioning to Yimmugo, a novel IVIg preparation. Scleromyxedema is a
Anastasia Sophie Vollmer +3 more
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Early onset of scleromyxedema Arndt‐Gottron associated with a monoclonal gammapathy: Successful treatment with intravenous immunoglobulins [PDF]
Clinical Case Reports, 2022 Arndt‐Gottron (S‐AG) syndrome or scleromyxedema is a scarce disease characterized by a generalized papular and sclerodermoid eruption and systemic manifestations that can lead to significant morbid‐mortality.
Asma Kefi +3 more
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Acta Medica Iranica, 1996 Scleromyxedema is a rare, chronic, progressive, fibromucinous disorder of unknown etiology, characterized by lichenoid waxy papules and firm induration of skin of trunk, face, forearm and hands; fibroblast proliferation and mucin deposition in the upper ...
Z. Safaii Naraghi. +1 more
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