Results 21 to 30 of about 1,053 (167)

An unusual case of granulomatous scleromyxedema [PDF]

JAAD Case Reports, 2022
Lauren Michelle, BA, Sara Sabeti, BS, Katerina Yale, MD, Brittany Urso, MD, Bonnie Lee, MD, Janellen Smith, MD   +5 more
doaj   +2 more sources

Clonal disorders of clinical significance. A concept with important therapeutic implications. [PDF]

J Eur Acad Dermatol Venereol
Journal of the European Academy of Dermatology and Venereology, Volume 39, Issue 5, Page 891-892, May 2025.
Lipsker D.
europepmc   +2 more sources

Successful treatment of scleromyxedema with dupilumab: A case report [PDF]

JAAD Case Reports
Abdulelah Alghamdi, MBBS, Abdulrahman Alfawzan, MBBS, Khalid Aburas, MBBS, Nedhal Ayoub, MD, Mohammad Almohideb, MD   +4 more
doaj   +2 more sources

Plasma cell-directed therapies induce profound clinical and durable responses in patients with severe or relapsed/refractory scleromyxedema. [PDF]

J Eur Acad Dermatol Venereol
In severe forms of monoclonal gammapathy associated with scleromyxoedema with dermatoneuro syndrome and/or cardiac involvement, deep and durable responses allowing IVIG withdrawal could be achieved using anti‐plasma cell therapy, including Imids, anti‐CD38 or proteasome inhibitors. Abstract Background Scleromyxedema (SM) is a rare skin disorder related
Theves F, Lahuna C, Mahévas T, Harel S, Royer B, Lemiale V, Brignier A, Parquet N, Jachiet M, Bouaziz JD, Elessa D, Arnulf B, Talbot A.   +12 more
europepmc   +2 more sources

Localized eruption of glabella and eyebrows [PDF]

JAAD Case Reports
Celestina Okoye, MD, Kai Brady, BS, Jennifer Shastry, MD   +2 more
doaj   +2 more sources

Unilateral Extremity Swelling, a Rare Manifestation of Scleredema Adultorum of Buschke in a Child: Case Report. [PDF]

Clin Case Rep
ABSTRACT Scleredema adultorum of Bushcke is a rare connective tissue disorder that is characterized by skin thickening that commonly starts from the neck and spreads to the face, shoulders, upper back, abdomen, and in some cases, thighs. The symptoms are generally seen after an infection associated with streptococcus.
Hajiani Ghotbabadi S, Derakhshan D, Rubab Amir R, Tabibi P.   +3 more
europepmc   +2 more sources

Look Outside the Brain: Incidentally Detected Cutis Verticis Gyrata. [PDF]

Clin Case Rep
ABSTRACT Cutis verticis gyrata (CVG) is a rare dermatological condition characterized by thickened and folded scalp skin, often discovered incidentally during neuroimaging for unrelated issues. Clinicians should remain vigilant and consider a multidisciplinary approach to recognize and manage potential comorbidities, emphasizing the importance of a ...
Devkota S, Bhatta OP.
europepmc   +2 more sources

Scleromyxedema

Current Opinion in Rheumatology, 2014
To synthesize the current known data on pathogenesis and treatment of scleromyxedema. This review will also highlight the clinical presentation, systemic features and outcomes and distinguishing features between scleromyxedema and scleroderma, as a common mimic.Most recent publications have focused on describing treatment responses with novel therapies,
Ryan R, Bogner, David A, Wetter, David, Dingli   +2 more
openaire   +5 more sources

Severe cutaneous scleromyxedema treated by lenalidomide

JEADV Clinical Practice, 2023
Scleromyxedema is a rare clinical variant of primary cutaneous mucinosis. It is defined by a generalized papular and sclerodermoid eruption associated with monoclonal gammopathy. No specific definitive treatment is known and those tried have inconsistent
Théo Brochet, Ali Dadban, Quentin Beauvillain, Clemence Boucher, Fanny Dessirier, Christophe Attencourt, Catherine Lok, Pierre Morel, Aurélie Halle, Guillaume Chaby   +9 more
doaj   +1 more source

Eosinophilic fasciitis (Shulman's disease): review and comparative evaluation of seven patients. [PDF]

, 2019
OBJECTIVES: Eosinophilic fasciitis (EF) was described in 1974 by Shulman as a rare fibrosing connective tissue disease of unknown etiology. An undetermined trigger is thought to lead to the degranulation of eosinophils that interact with fibroblasts and
Cimbron, M, Farinha, F, Mendonça, T, Urzal, J   +3 more
core   +1 more source