Long-Term Efficacy of Treatment with Intravenous Immunoglobulin in Scleromyxedema [PDF]
, 2020 Scleromyxedema or generalized lichen myxedematosus is a rare depositional disorder. Diagnostic criteria encompass a generalized papular and sclerodermoid eruption, monoclonal gammopathy (paraproteinemia), most often with G-lambda type immunoglobulin, a ...
Katarina Trčko, Špela Baglama
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Sklerodermie und fibrosierende Erkrankungen [PDF]
, 2018 Zusammenfassung: Bei der Sklerodermie und anderen fibrosierenden Erkrankungen wie den Fibromatosen, der Arthrofibrose und dem M.Ormond liegt eine Fibroblastenproliferation mit mehr oder weniger starker Begleitentzündung vor. Bei der Sklerodermie kommt es
Jakobs, M. +3 more
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NFκB activation and stimulation of chemokine production in normal human macrophages by the gadolinium-based magnetic resonance contrast agent Omniscan: possible role in the pathogenesis of nephrogenic systemic fibrosis. [PDF]
, 2010 OBJECTIVE: Nephrogenic systemic fibrosis (NSF) is a generalised fibrotic disorder occurring in certain individuals with renal insufficiency exposed to gadolinium-based contrast agents (GdBCA) for MRI.
Addya, Sankar +4 more
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Discrete Papular Lichen Myxedematosus and Scleromyxedema with Hypothyroidism: A Report of Two Cases [PDF]
, 2019 Scleromyxedema and lichen myxedematosus (LM) are rare disorders that fall along the spectrum of primary cutaneous mucinoses. Scleromyxedema is a systemic form that classically presents with generalized waxy papules, sclerodermoid eruption, and monoclonal
Adele Shenoy +3 more
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Adult Variant of Self-healing Cutaneous Mucinosis in a Patient with Epilepsy [PDF]
, 2016 A 52-year-old woman was admitted with a 3 weeks history of periorbital edema and lips swelling. She developed several subcutaneous firm erythematous papules and nodules on the face, scalp and two indurated plaques on the upper back and left forearm ...
Aliabdi, Maryam +5 more
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The Journal of Dermatology, Volume 51, Issue 12, Page 1665-1668, December 2024.Abstract Pemphigus vulgaris (PV) is a severe autoimmune bullous dermatosis that is characterized by autoantibodies against epidermal adhesion proteins causing painful mucosal and skin blistering. Standard treatments for PV include corticosteroids, steroid‐sparing immunosuppressants, or intravenous monoclonal anti–CD20‐antibody therapy.
Nadine Wiedenmayer +4 more
wiley +1 more source
Склеромикседема Арндта — Готтрона [PDF]
, 2012 The authors present a literature review and a case study of a rare form of dermatitis in a female patient aged 44 — Arndt — Gottron scleromyxedema associated with Ig-kappa monoclonal hyper-production. The authors also present the latest information about
CHIKIN V.V. +7 more
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Dermoscopy and Reflectance Confocal Microscopy for the Diagnosis of Scleromyxedema [PDF]
, 2019 info:eu-repo/semantics ...
Borges, AS +3 more
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Scleromyxedema with systemic involvement mimics rheumatic diseases [PDF]
, 1986 Scleromyxedema is an infiltrative skin disease produced by hyaluronic acid deposition in the dermis. A benign monoclonal gammopathy is usually present. We report 2 patients with scleromyxedema and systemic illnesses.
Chanda +14 more
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