Results 51 to 60 of about 1,053 (167)
Immunohistochemical investigations and introduction of new therapeutic strategies in scleromyxoedema: Case report [PDF]
BACKGROUND: Scleromyxoedema is a rare chronic skin disease of obscure origin, which may often be associated with severe internal co-morbidity. Even though different casuistic treatment modalities have been described, to date, curing still seems to be ...
Altmeyer, Peter +5 more
core +3 more sources
Scleromyxedema is a rare cutaneous mucinosis, usually presenting with generalized papular eruption and sclerodermoid induration, monoclonal gammopathy and systemic manifestations.
M. Dolenc-Voljč +3 more
doaj +1 more source
ABSTRACT Background Scleromyxedema (SMX) is a cutaneous mucinosis characterised by an abnormal accumulation of mucin in the skin and limited treatment options. Assessment of therapy response during treatment is challenging. Objectives Patients with SMX receiving high‐dose intravenous IVIg therapy were included to assess validity of the double modified ...
Julia K. Winkler, Alexander H. Enk
wiley +1 more source
Scleromyxedema, a therapeutic dilemma
Scleromyxedema is characterized by indurated erythematous papules disseminated on the face, chest and limbs. About twenty cases treated with thalidomide, stem cells, melphalan and immunoglobulin with varying results have been described.
Julio Cesar Salas-Alanis +3 more
doaj +1 more source
Scleromyxedema without paraproteinemia
AbstractBackgroundScleromyxedema is a rare generalized form of lichen myxedematosus, a chronic cutaneous mucinosis of unknown etiology usually associated with a monoclonal gammopathy and underlying systemic disorders. It is characterized by the presence of lichenoid papules and diffuse indurations of the skin.
Abarzúa, Alvaro A. +3 more
openaire +3 more sources
Systemic sclerosis without antinuclear antibodies or Raynaud's phenomenon: a multicentre study in the prospective EULAR Scleroderma Trials and Research (EUSTAR) database [PDF]
Objective. To assess patients with SSc who present without circulating ANAs or RP. Methods. Five thousand three hundred and ninety patients who fulfilled the ACR criteria for SSc and were enrolled in the EULAR Scleroderma Trials and Research (EUSTAR ...
Carreira, Patricia E. +9 more
core
Sklerosierende Erkrankungen der Haut
Zusammenfassung Sklerosierende Hautkrankheiten sind eine Gruppe unterschiedlicher dermatologischer Erkrankungen, die durch fibrotische Veränderungen gekennzeichnet sind und die Lebensqualität der Patienten stark einschränken können. Diese Erkrankungen treten häufig mit kutanen Manifestationen auf und können in bestimmten Fällen auch extrakutanes Gewebe
Yasamin Kalantari +4 more
wiley +1 more source
Successful Treatment of Scleromyxedema with IVIG: A Case Report
Scleromyxedema (SM), a rare progressive cutaneous mucinosis with a systemic involvement, presents with progressive dermal mucin depositions, causing skin thickening.
Fatemeh Niksolat +5 more
doaj
Long-Term Efficacy of Treatment with Intravenous Immunoglobulin in Scleromyxedema [PDF]
Scleromyxedema or generalized lichen myxedematosus is a rare depositional disorder. Diagnostic criteria encompass a generalized papular and sclerodermoid eruption, monoclonal gammopathy (paraproteinemia), most often with G-lambda type immunoglobulin, a ...
Katarina Trčko, Špela Baglama
core +1 more source
Systemic Sclerosis Mimics [PDF]
Many clinical conditions are presenting with sclerosis of the skin and with tissue fibrosis. These conditions may be confused with systemic sclerosis (SSc, scleroderma).
Kodet, Ondřej, Oreská, Sabína
core +2 more sources

