Results 31 to 40 of about 5,084,169 (167)

Public health concerns regarding sporadic Creutzfeldt–Jakob disease in China: a case series

Journal of International Medical Research, 2019
In this study, we report three cases of sporadic Creutzfeldt–Jakob disease in China, two confirmed cases and one probable case. The aim of this study was to enrich the data regarding clinical and epidemiological features of this disease and to provide ...
Ru-Yi Zhou, Yinzhu Zhou, Heng Zhang, Qingqing Hu, Jinjie Zhu, Jin Zhao, Shuilian Chen, Ruchun Liu, Weihong Hu, Xixing Zhang, Xianfa Xuan, Yuxue Liao, Tianmu Chen   +12 more
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Synthetic prions generated in vitro are similar to a newly identified subpopulation of PrPSc from sporadic Creutzfeldt-Jakob disease [PDF]

, 2005
In recent studies, the amyloid form of recombinant prion protein (PrP) encompassing residues 89-230 (rPrP 89-230) produced in vitro induced transmissible prion disease in mice.
Bocharova, O V, Salnikov, V V, Gill, A C, Vadim V. Salnikov, Ilia V. Baskakov, Leonid Breydo, Breydo, L, Olga V. Bocharova, Andrew C. Gill, Baskakov, I V   +9 more
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Creutzfeldt-Jakob disease and homocysteine levels in plasma and cerebrospinal fluid [PDF]

, 2005
Background: There is evidence that homocysteine contributes to various neurodegenerative disorders. Objective: To assess the values of homocysteine in patients with Creutzfeldt-Jakob disease (CJD) in both cerebrospinal fluid (CSF) and plasma.
Bleich, S., Kropp, S., Wiltfang, J., Zerr, Inga, Zerr, I., Kretzschmar, Hans A., Kropp, Silke, Otto, Markus, Wiltfang, Jens, Bleich, Stefan   +9 more
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Young-onset sporadic Creutzfeldt–Jakob disease with atypical phenotypic features: a case report

Journal of Medical Case Reports, 2019
Background Sporadic Creutzfeldt–Jakob disease, with a mean survival of 6 months, is duly considered among the most fatal neurological disorders. Rapidly progressive dementia with multi-axial involvement of the nervous system is the known presentation ...
Durjoy Lahiri, Srimant Pattnaik, Ashwani Bhat, Souvik Dubey, Atanu Biswas, Biman Kanti Roy   +5 more
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Bioassay studies support the potential for iatrogenic transmission of variant Creutzfeldt Jakob Disease through dental procedures [PDF]

, 2012
<p>Background: Evidence is required to quantify the potential risks of transmission of variant Creutzfeldt Jakob (vCJD) through dental procedures. Studies, using animal models relevant to vCJD, were performed to address two questions.
Elizabeth Kirby (115076), Marsh, PD, Raven, N.D.H., Mark Cornwall, Andrew Smith (11197), Marsh Philip D., Vassey, M., Neil McLeod (115085), Cornwall Mark, Joanne Dickinson (115078), J. Mark Sutton (115091), Cornwall, M, Dickinson, J., Dickinson Joanne, Vassey Matthew, Mark Cornwall (115083), Raven, NDH, Matthew Vassey (115080), Mike Dennis, Walker, J.T., Kirby Elizabeth, Smith, A, McLeod, N., J Mark Sutton, Walker, JT, Dennis, M., Sutton, J.M., Matthew Vassey, Philip D. Marsh (115087), James T Walker, Marsh, P.D., Dennis, M, Joanne Dickinson, McLeod Neil, McLeod, N, Andrew Smith, Walker James T., Elizabeth Kirby, Raven Neil D. H., Smith, A., Vassey, M, Neil D. H. Raven (115095), James T. Walker (115089), Dickinson, J, Sutton, JM, Sutton J. Mark, Kirby, E, Kirby, E., Smith Andrew, Neil McLeod, Cornwall, M., Mike Dennis (115082), Philip D Marsh, Neil D H Raven, Dennis Mike   +54 more
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Applicability of long-term electroencephalography in pre-mortem diagnosis of Creutzfeldt–Jakob disease: A case report

SAGE Open Medical Case Reports, 2017
Creutzfeldt–Jakob disease accounts for more than 90% of all sporadic prion disease cases. The molecular MM2 genotype has been divided into cortical and thalamic subtypes based on structures involved and is characterized clinically by progressive dementia
Sanaz Attaripour Isfahani, Michelle Dougherty, Gediminas Peter Gliebus   +2 more
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Updated clinical diagnostic criteria for sporadic Creutzfeldt-Jakob disease [PDF]

, 2009
Several molecular subtypes of sporadic Creutzfeldt-Jakob disease have been identified and electroencephalogram and cerebrospinal fluid biomarkers have been reported to support clinical diagnosis but with variable utility according to subtype.
Summers, DM, Collins, S.J. (Steven), Brandel, J.P., Meissner, B, Meissner, B., Cras, P. (Patrick), Varges, D., Jansen, GH, Cras, Patrick, Pimentel, J, Brandel, J P, Smith, P., Taratuto, Ana Lia, van Duijn, Cornelia M., Begue, Christian, Summers, D. M., Summers, D.M., Jansen, G. H., Hewer, Ekkehard, Ladogana, Anna, Jansen, Gerard H, Will, Robert G., Schuur, M. (Maaike), Haik, S., Sanchez-Juan, P. (Pascual), Begue, C, Brandel, JP, Collins, S J, Heinemann, U., Haik, Stephane, Stokin, G B, Zerr, I., Schuur, M, Pimentel, Jose, Breithaupt, M., Taratuto, A, Sanchez-Juan, P, van Duijn, C., Stokin, GB, Breithaupt, Maren, Collins, SJ, Kallenberg, K., Sanchez-Juan, P., Collie, Donald A., Sanchez-Juan, Pascual, Hewer, E, Ladogana, A. (Anna), Schuur, M., Romero, C, Tikka-Kleemola, P. (Päivi), Cras, P., Schuur, Maaike, Romero, Carlos, Ladogana, A, Haik, S, Duijn, Cornelia, Stokin, G. B., Taratuto, A., Collie, D, Stokin, G.B., Brandel, J. P., Romero, C., Smith, P, Jansen, G H, Collie, D., Begue, C., Heinemann, U, Will, R G, Smith, Pete, Pocchiari, M., Collins, S. J., Pocchiari, Mauricio, Ladogana, A., Will, R. G., Will, RG, Meissner, Bettina, Summers, D M, Breithaupt, M, Jansen, G.H. (Gerard), Kallenberg, Kai, Hewer, E., Will, R.G., Cras, P, Zerr, I, Roberts, H., Jansen, Gerard H., Pocchiari, M, van Duijn, C, Pocchiari, M. (Maurizio), Varges, Daniel. A., Roberts, H, Brandel, Jean-Philippe, Kallenberg, K, Varges, D, Pimentel, J., et al.   +95 more
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Clinical Features of Rapidly Progressive Alzheimer's Disease [PDF]

, 2010
Objective: To characterize clinical features, CSF biomarkers and genetic polymorphisms of patients suffering from a rapidly progressing subtype of Alzheimer's dementia (rpAD).
Meissner, Bettina, Bettina Meissner, Zerr, Inga, Redyk, Katharina, Christian Schmidt, Nico von Ahsen, Kretzschmar, Hans A., Lennart Krack, Schmidt, Christian, Roeber, Sigrun, von Ahsen, Nico, Katharina Redyk, Sigrun Roeber, Hans Kretzschmar, Inga Zerr, Krack, Lennart, Kretzschmar, Hans, Schmidt, Christian D., Krack, Lennart A., Ahsen, Nico von   +19 more
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Movement Disorders in Prionopathies: A Systematic Review

Tremor and Other Hyperkinetic Movements, 2019
Background: Movement disorders are frequent features of prionopathies. However, their prevalence and onset remain poorly described. Methods: We performed a systematic review of case reports and case series of pathologically- and genetically confirmed ...
Federico Rodriguez-Porcel, Vinícius Boaratti Ciarlariello, Alok K. Dwivedi, Lilia Lovera, Gustavo Da Prat, Ricardo Lopez-Castellanos, Ritika Suri, Holly Laub, Ruth H. Walker, Orlando Barsottini, José Luiz Pedroso, Alberto J. Espay   +11 more
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The first reported case of Creutzfeldt‐Jakob disease from Nepal

Clinical Case Reports, 2020
Creutzfeldt‐Jakob disease (CJD) can also be diagnosed in a resource‐limited setting through good clinical analysis. The diagnosis of CJD should be considered in patients with rapidly evolving neurological signs associated with cognitive disturbances even
Himal Kharel, Pabitra Adhikari, Nishan B. Pokhrel, Zeni Kharel, Gaurav Nepal   +4 more
doaj   +1 more source