Results 61 to 70 of about 5,537 (170)

Stiff Person Syndrome and Myasthenia Gra

, 2002
Association of stiff person syndrome, an immune related disorder of anterior horn cells and myasthenia gravis an endplate disorder with similar pathogenesis, is rare.
P. K. Saravanan, J. Paul, Zaheer Ahmed Sayeed   +2 more
core  

Successful anesthetic management of patient with stiff person syndrome

, 2018
We herein describe the successful anesthetic management of a patient with stiff person syndrome undergoing right total hip replacement under spinal anesthesia. We also describe the problems associated with general anesthesia.
Siddiqui, Sarfraz, Sohaib, Muhammad
core  

Subcutaneous immunoglobulin for maintenance therapy in stiff-person syndrome: One-year follow-up in two patients

, 2020
Stiff person syndrome is a rare condition characterised by prolonged stiffness with superimposed muscle spasms. Immunotherapy relies mainly on intravenous immunoglobulin, steroids and plasma exchange. Azathioprine or rituximab are other possible options.
Liguori R., Bartolomei L., Rinaldi R., Minicuci G. M., Donadio V., D'Angelo R., Fileccia E.   +6 more
core   +1 more source

Stiff-Person Syndrome [PDF]

, 2019
Stiff person syndrome spectrum disorder (SPSSD) consists of a rare set of diseases characterized by severe muscle stiffness and rigidity with decline in function. Although poorly understood, an underlying autoimmune disorder interfering with the CNS inhibitory mechanism is likely the culprit.
openaire   +2 more sources

PET evidence of central GABAergic changes in stiff-person syndrome

, 2007
We measured expression of central nervous system GABA-A receptors with 11C-flumazenil (11C-FMZ) and PET in two subjects with stiff person syndrome (SPS).
V. Garibotto, Corbo, Massimo, D. Perani, A. Panzacchi, M. Corbo, R. M. Moresco, Ortelli, Paola, F. Folli, PERANI, DANIELA FELICITA L., Garibotto, Valentina, Fazio, Ferruccio, P. Ortelli, Panzacchi, Andrea, F. Fazio, Moresco Rosa Maria,, Folli, Franco   +15 more
core   +1 more source

Efficacy of Surgical Treatment for Thymoma-Related Stiff Person Syndrome

Annals of Thoracic Surgery Short Reports
Stiff person syndrome (SPS) is a neurologic disorder, some cases of which are associated with malignant disease. Here, we report a case of thymoma-associated SPS that was successfully treated with surgical resection.
Ryusuke Sumiya, MD, PhD, Takamitsu Banno, MD, Hiroyasu Ueno, MD, PhD, Shunki Hirayama, MD, PhD, Kenji Suzuki, MD, PhD   +4 more
doaj   +1 more source

Lower Extremity Predominant Stiff-Person Syndrome and Limbic Encephalitis With Amphiphysin Antibodies in Breast Cancer

, 2012
A 54-year-old woman presented with several weeks of psychiatric symptoms, partial-onset seizures, and painful spasms of the lower extremities. On examination, she exhibited severe stiffness and intermittent extensor spasms of the lower extremities ...
Sivakumar, Kumaraswamy, Knievel, Kerry, Krishna, Vivek R., Ladha, Shafeeq S.   +3 more
core   +1 more source

Disease-specific monoclonal antibodies targeting glutamate decarboxylase impair GABAergic neurotransmission and affect motor learning and behavioral functions

Frontiers in Behavioral Neuroscience, 2015
Autoantibodies to the smaller isoform of glutamate decarboxylase can be found in patients with type 1 diabetes and a number of neurological disorders, including stiff-person syndrome, cerebellar ataxia and limbic encephalitis.
Mario U Manto, Jerome eHonorat, Christiane Susanne Hampe, Rafael eGuerra-Narbona, Juan Carlos eLópez Ramos, José M Delgado-García, Fumihito eSaitow, Hidenori eSuzuki, Yuchio eYanagawa, Hidehiro eMizusawa, Hiroshi eMitoma   +10 more
doaj   +1 more source

Stiff person syndrome: avoiding misdiagnosis

, 2007
Stiff person syndrome (SPS) is a rare neurological disorder characterised by muscular rigidity and superimposed spasms of the trunk and limbs that may be precipitated by voluntary movements and unexpected tactile, auditory or emotional stimulation.
Andreadou, E., Vassilopoulos, D., Sfagos, C., Kattoulas, E.   +3 more
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Analysis on clinical and electrophysiological characteristics of 11 patients with stiff-person syndrome

Chinese Journal of Contemporary Neurology and Neurosurgery, 2019
Objective To summarize the clinical features and electrophysiological characteristics of stiff-person syndrome (SPS). Methods and Results Clinical data of 11 SPS patients [8 were classic and 3 were stiff-person plus syndrome (SPPS)], who were diagnosed ...
Xin-jing ZHONG, Cheng ZHANG, Jie ZHONG, Xue-ling CHEN   +3 more
doaj