Macrophage Activation Syndrome Associated with Adult-Onset Still’s Disease Successfully Treated with Anakinra [PDF]
Macrophage activation syndrome (MAS) is a potentially fatal complication of Adult-Onset Still’s disease (Still’s disease). Whereas an increasing body of evidence supports interleukin-1 (IL-1) blockade as a promising treatment for Still’s disease, whether
Aswini Kumar, Hiroshi Kato
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ADULT-ONSET STILL’S DISEASE: ASPECTS OF THE HEMATOLOGY CLINIC
The analysis of literature data on modern approaches in the diagnosis and treatment of adult-onset Still’s disease has been performed. A clinical case of Still’s disease associated with lymphadenopathy syndrome was demonstrated.
M. M. Agakishiev +6 more
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Fever and erythema: exclude all and then… think of Still’s disease!
Adult-onset Still’s disease is a rare disease. Diagnosis of Still’s disease is often difficult to achieve. Herein, we describe our diagnostic approach in a case report regarding an adult patient who presented with fever, erythema, lymphadenopathy and ...
Marta Maset +5 more
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Pneumonitis in Adult Onset Still’s Disease: Uncommon or Under Diagnosed?
The adult onset Still’s Disease is an uncommon entity characterized by multiple clinical manifestations. Pneumonitis, less often considered, deserves particular emphasis given the need for differential diagnosis and because it can progress to severe ...
Silvia Fernandes +3 more
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Association between adult-onset still’s disease and COVID-19: A report of two cases and brief review
Adult-onset still’s disease is a rare multisystemic autoinflammatory disorder with an estimated annual incidence of 0.16–0.62 per 100,000 individuals worldwide. It is typically considered a diagnosis of exclusion.
Sarah Fet-He +2 more
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Adult Still’s disease and Tako-Tsubo syndrome [PDF]
Here we describe the case of a 68-year-old Italian female who was admitted in our hospital for the occurrence of arthralgia, abdominal pain and general discomfort.
Susanna Cozzio +4 more
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Efficacy of canakinumab in patients with Still’s disease across different lines of biologic therapy: real-life data from the International AIDA Network Registry for Still’s Disease [PDF]
IntroductionThe effectiveness of canakinumab may change according to the different times it is used after Still’s disease onset. This study aimed to investigate whether canakinumab (CAN) shows differences in short- and long-term therapeutic outcomes ...
Antonio Vitale +75 more
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Objectives Systemic autoinflammatory diseases (SAIDs) represent a set of conditions with exaggerated innate immune responses. IL-1β and IL-18 are key cytokines involved in the pathogenesis of some SAID.
+94 more
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Hepatic tuberculosis presenting with extreme hyperferritinemia masquerading as adult-onset Still’s disease: a case report [PDF]
Introduction Isolated hepatic tuberculosis is an uncommon manifestation of one of the most common infections worldwide, caused by Mycobacterium tuberculosis. Extremely high serum ferritin, which is regarded as a marker of adult onset Still’s disease, has
Manoj Edirisooriya +2 more
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Background Lymphadenopathy is not an uncommon presentation of adult onset Still’s disease: it is present in up to two thirds of patients with adult onset Still’s disease.
S. W. G. J. W. Chinthaka +5 more
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