Results 21 to 30 of about 184 (130)
Structural Insights into Sulfite Oxidase Deficiency [PDF]
Journal of Biological Chemistry, 2005 Sulfite oxidase deficiency is a lethal genetic disease that results from defects either in the genes encoding proteins involved in molybdenum cofactor biosynthesis or in the sulfite oxidase gene itself. Several point mutations in the sulfite oxidase gene have been identified from patients suffering from this disease worldwide.
Erkan, Karakas +6 more
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Molybdenum Cofactor Deficiency in Humans
Molecules, 2022 Molybdenum cofactor (Moco) deficiency (MoCD) is characterized by neonatal-onset myoclonic epileptic encephalopathy and dystonia with cerebral MRI changes similar to hypoxic–ischemic lesions.
Lena Johannes +2 more
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Sulfite oxidase activity in Thiobacillus novellus [PDF]
Journal of Bacteriology, 1983 Thiobacillus novellus shows a maximum induction of sulfite oxidase activity and a maximum growth rate as a result of supplementing the autotrophic growth medium with 4.0 microM ammonium molybdate. Cells grown in the presence of molybdate showed approximately 10-fold increases in the amount of enzyme-associated molybdenum and in the sulfite-to ...
W M, Southerland, F, Toghrol
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Sulfite oxidase activity of cytochrome c: Role of hydrogen peroxide
Biochemistry and Biophysics Reports, 2016 In humans, sulfite is generated endogenously by the metabolism of sulfur containing amino acids such as methionine and cysteine. Sulfite is also formed from exposure to sulfur dioxide, one of the major environmental pollutants.
Murugesan Velayutham +3 more
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Human Molecular Genetics, 2019 AbstractSulfite oxidase (SO) is encoded by the nuclear SUOX gene and catalyzes the final step in cysteine catabolism thereby oxidizing sulfite to sulfate. Oxidation of sulfite is dependent on two cofactors within SO, a heme and the molybdenum cofactor (Moco), the latter forming the catalytic site of sulfite oxidation.
Daniel, Bender +8 more
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Prenatal brain disruption in isolated sulfite oxidase deficiency
Orphanet Journal of Rare Diseases, 2017 Background Isolated sulfite oxidase deficiency (ISOD) is a very rare autosomal recessive inherited neurometabolic disease. The most striking postnatal neuroimaging finding is multicystic encephalomalacia, which occurs rapidly within days to weeks after ...
Hsiu-Fen Lee +4 more
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Frontiers in Microbiology, 2011 Sulfite dehydrogenases are enzymes that catalyze the oxidation of the toxic and mutagenic compound sulfite to sulfate, thereby protecting cells from adverse effects associated with sulfite exposure.
Louie eLow +3 more
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Fabrication of a Sulfite Biosensor by the Use of Conducting Polymer [PDF]
Iranian Journal of Chemistry & Chemical Engineering, 2008 In this research, an enzyme modified electrode has been produced during the electropolymerization of aniline through incorporation of sulfite oxidase into a conducting polymer.
Mohammad Hosseini +3 more
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Molybdenum‐Based Nanomaterials for Photothermal Cancer Therapy
Advanced NanoBiomed Research, 2022 Molybdenum (Mo) is a trace dietary element that is essential for human survival. Several molybdenum‐containing enzymes (e.g., aldehyde oxidase, xanthine oxidase and sulfite oxidase) are associated with key metabolic activities in the body.
Zhan Zhou +7 more
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Spectroscopic Studies of Mononuclear Molybdenum Enzyme Centers
Molecules, 2022 A concise review is provided of the contributions that various spectroscopic methods have made to our understanding of the physical and electronic structures of mononuclear molybdenum enzymes.
Martin L. Kirk, Russ Hille
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