TAFRO Syndrome in a Kidney Transplant Recipient That Was Diagnosed on Autopsy: A Case Report
Frontiers in Medicine, 2021 A 57-year-old man who received a kidney transplant 4 years previously owing to unknown underlying disease presented with thrombocytopenia and fever. Hepatosplenomegaly and lymphadenopathy were observed, and development of prominent anasarca and worsening
Marie Nagai +10 more
doaj +1 more source
Long-term safety of siltuximab in patients with idiopathic multicentric Castleman disease: a prespecified, open-label, extension analysis of two trials. [PDF]
, 2020 BACKGROUND:Siltuximab is recommended by international consensus as a first-line treatment for idiopathic multicentric Castleman disease on the basis of durable efficacy and safety data.
Casper, Corey +6 more
core
Multicentric vs. Unresectable Unicentric Castleman Disease with Active Presentation: An Orphan Rare Disease in a Young Egyptian Female Patient. A Case Report [PDF]
, 2023 Background: Castleman disease (CD) is a rare disorder that affects lymph nodes and has a wide range of associated symptoms. The affected lymph nodes show characteristic histological picture.
Ahmed E. Eladl +10 more
core +1 more source
Idiopathic multicentric Castleman disease in an adolescent diagnosed following COVID‐19 infection
, 2023 Pediatric Blood &Cancer, Volume 70, Issue 6, June 2023.
Eman Mosleh +5 more
wiley +1 more source
Multicentric Castleman disease with TAFRO syndrome and Sjögren's [PDF]
Clinical Case Reports, 2019 AbstractWe describe a patient with Castleman's disease with TAFRO syndrome and concurrent Sjögren's syndrome and investigate whether the autoimmune process may have accelerated the onset of her Castleman's disease. Patient was treated with R‐CVP therapy with remission of symptoms although there is no current standard treatment.
Zi Ying Li +3 more
openaire +5 more sources
Immunological MedicineTAFRO syndrome is a systemic inflammatory disorder of unknown etiology, and its diagnosis requires the exclusion of autoimmune diseases. A 42-year-old Japanese woman presented with TAFRO syndrome-like manifestations, but had undiagnosed limited-cutaneous
Hiroyuki Kawahara +9 more
doaj +1 more source
A clinical, histological and transcriptomic characterization of a selected series of Castleman disease’s cases [PDF]
, 2023 Castleman disease (CD) is a rare lymphoproliferative disorder that includes various clinico-pathological subtypes. According to clinical course CD is divided in unicentric CD (UCD) and multicentric CD (MCD).
FRATICELLI, SARA
core
Rare disease research requires (and benefits from) global collaboration: three examples from the Castleman Disease Collaborative Network [PDF]
, 2016 Castleman disease (CD) describes a heterogeneous group of rare and poorly understood lymphoproliferative disorders that can involve flu-like symptoms, multiple organ system dysfunction, and even death.
Ahagon, Deise +11 more
core +2 more sources
TAFRO syndrome: A severe manifestation of Sjogren's syndrome? A systematic review
Autoimmunity Reviews, 2022 Sjögren's syndrome (SjS) is a systemic autoimmune disease characterized by lymphocytic infiltration of the salivary and lacrimal glands associated with sicca syndrome. TAFRO syndrome is a systemic inflammatory disease of unknown cause, characterized by Thrombocytopenia, Anasarca, Fever, Reticulin fibrosis, Renal dysfunction and Organomegaly, first ...
Grange, Lucile +6 more
openaire +4 more sources
Case Reports in Hematology, 2016 TAFRO syndrome is a rare constellation of symptoms: thrombocytopenia, anasarca, reticulin fibrosis of the bone marrow, renal dysfunction, and organomegaly.
Malorie Simons +3 more
doaj +1 more source